Tracheobronchiomegaly. The Mounier-Kuhn syndrome in a patient with the Kenny-Caffey syndrome.
A 36-year-old woman with features of both the Mounier-Kuhn syndrome and the Kenny-Caffey syndrome is described. To our knowledge, this is the first reported case of these syndromes occurring together. Three-dimensional computed tomographic reconstruction of the upper airway revealed marked dilatation of the trachea and main-stem bronchi and several large diverticulae of the trachea.
Sane
A C
AC
Department of Pulmonary Medicine, Duke University Medical Center, Durham, NC.
Effmann
E L
EL
Brown
S D
SD
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000328:Adult; D001842:Bone and Bones / Q000002:abnormalities / Q000000981:diagnostic imaging; D001995:Bronchography; D004392:Dwarfism / Q000000981:diagnostic imaging*; D005260:Female; D006801:Humans; D013577:Syndrome; D014057:Tomography, X-Ray Computed; D014132:Trachea / Q000000981:diagnostic imaging; D014137:Tracheobronchomegaly / Q000000981:diagnostic imaging*