[Type I neurofibromatosis (von Recklinghausen's disease) associated with abdominal neurofibrosarcoma and pheochromocytoma. Apropos of a case].
Neoplasia and endocrine disorders are common complications of neurofibromatosis 1 (NF1--von Recklinghausen disease). We report here a case of NF1 in a 31-year-old woman presenting simultaneously with an abdominal neurofibrosarcoma and a pheochromocytoma. The prevalence of secondary neoplasia and endocrine tumors in NF1 is also discussed.
De Grez
T
T
Service de Médecine Interne Générale, Cliniques Universitaires Saint-Luc, Bruxelles.
Lambert
M
M
Delaere
B
B
Gigot
J F
JF
Haot
J
J
D000008:Abdominal Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D000310:Adrenal Gland Neoplasms / Q000150:complications*; D000328:Adult; D005260:Female; D006801:Humans; D009378:Neoplasms, Multiple Primary; D009455:Neurofibroma / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000150:complications*; D010673:Pheochromocytoma / Q000150:complications*; D014057:Tomography, X-Ray Computed
Neurofibromatose de type I (maladie de von Recklinghausen) associée àun neurofibrosarcome abdominal et un phéochromocytome. A propos d'un cas.