[Malignant germ cell tumor in XY gonadal dysgenesis (Swyer syndrome)].
Case of a 20-year-old patient with severe abdominal pain, right adnexal mass, positive beta-HCG titre and free fluid in the abdominal cavity, as diagnosed by ultrasound. Laparotomy resulted in a ruptured ovarian tumour (chorionic carcinoma). Despite chemotherapy, the tumour developed fulminant metastases with a follow-up of 3 months.


METHODS
Gonadal dysgenesis, XY female type (Swyer-Syndrome).
Universitätsfrauenklinik Würzburg.
H
H
Spingler
P J
PJ
Albert
M
M
Schmid
J
J
Müller
D000328:Adult; D014408:Biomarkers, Tumor / Q000097:blood; D002822:Choriocarcinoma / Q000473:pathology* / Q000601:surgery; D006063:Chorionic Gonadotropin / Q000097:blood; D018997:Chorionic Gonadotropin, beta Subunit, Human; D005260:Female; D006059:Gonadal Dysgenesis / Q000473:pathology*; D006061:Gonadal Dysgenesis, 46,XY / Q000473:pathology*; D006801:Humans; D009362:Neoplasm Metastasis; D010051:Ovarian Neoplasms / Q000473:pathology* / Q000601:surgery; D010052:Ovariectomy; D010053:Ovary / Q000473:pathology; D010446:Peptide Fragments / Q000097:blood; D012422:Rupture, Spontaneous
D014408:Biomarkers, Tumor; D006063:Chorionic Gonadotropin; D018997:Chorionic Gonadotropin, beta Subunit, Human; D010446:Peptide Fragments
Maligner Keimzelltumor bei XY-Gonadendysgenesie (Swyer-Syndrom).