Metabolism of branched chain fatty acids in peroxisomal disorders.
Department of Chemical Pathology, Adelaide Children's Hospital, South Australia.
H
H
Singh
S
S
Usher
D
D
Johnson
A
A
Poulos
D000326:Adrenoleukodystrophy / Q000378:metabolism; D002478:Cells, Cultured; D002806:Chondrodysplasia Punctata / Q000378:metabolism; D005227:Fatty Acids / Q000378:metabolism*; D005347:Fibroblasts / Q000648:ultrastructure; D006538:Heptanoic Acids / Q000378:metabolism; D006801:Humans; D008661:Metabolism, Inborn Errors / Q000378:metabolism*; D008830:Microbodies / Q000378:metabolism*; D010084:Oxidation-Reduction; D012035:Refsum Disease / Q000378:metabolism; D013229:Stearic Acids / Q000378:metabolism; D015211:Zellweger Syndrome / Q000378:metabolism
D005227:Fatty Acids; D006538:Heptanoic Acids; D013229:Stearic Acids; C066164:4,8,12,16-tetramethylheptanoic acid; C031183:stearic acid; C002844:pristanic acid