[Bilateral claw deformity of the fingers due to fasciitis with eosinophilia (Shulman's syndrome). Apropos of a case].
Shulman's syndrome or fasciitis with eosinophilia is a disease of unknown origin with unclear relations with scleroderma, characterised by thickening of the fascia superficialis associated with blood eosinophilia. This diagnosis should be considered in a patient presenting with a lesion of the anterior surface of the forearms, which have an "armoured" appearance, associated with claw deformity of the wrist, hand and fingers. The diagnosis is based on cutaneo-muscular biopsy and treatment consists of corticosteroids. The clinical course is generally favourable, although recovery is sometimes incomplete. There is generally no visceral or systemic involvement apart from rare cytopenic forms which must be identified.
Clinique du Ter, Ploemeur.
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Katz
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Berhault
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000328:Adult; D001706:Biopsy; D004802:Eosinophilia / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D005208:Fasciitis / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D005385:Fingers; D006227:Hand Deformities, Acquired / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology; D006801:Humans; D008297:Male; D009132:Muscles / Q000473:pathology; D012867:Skin / Q000473:pathology
D000305:Adrenal Cortex Hormones
Attitude en crochet bilatérale des doigts par fasciite avec éosinophilie (syndrome de Shulman). A propos d'un cas.