[Periodic disease and periarteritis nodosa in the same patient: coincidence?].
Familial Mediterranean fever (FMF) chiefly affects patients of Arabic, Jewish, Armenian or Turkish origin and takes the form of recurrent episodes of peritonitis, arthritis or pleurisy. Periarteritis nodosa (PAN) is a vasculitis affecting elderly people and manifested by a general deterioration, unexplained fever and peripheral neuropathy or muscular weakness. We describe a patient presenting both diseases. Ours is the seventh reported case associating these two affections. This association was suspected by SACHS and co-workers who discovered an increased frequency of PAN in patients with FMF compared to the expected rate for the whole population (7). These observations warrant a search for PAN in young patients affected by FMF and showing signs of vasculitis.
Clinique médicale thérapeutique, Hôpital cantonal universitaire, Genève.
M
M
Pechère
C
C
Helfer
F L
FL
Laurencet
D000328:Adult; D001379:Azathioprine / Q000008:administration & dosage; D003078:Colchicine / Q000008:administration & dosage; D003520:Cyclophosphamide / Q000008:administration & dosage; D004359:Drug Therapy, Combination; D010505:Familial Mediterranean Fever / Q000150:complications* / Q000188:drug therapy; D006801:Humans; D008297:Male; D010488:Polyarteritis Nodosa / Q000150:complications* / Q000188:drug therapy; D011241:Prednisone / Q000008:administration & dosage
D003520:Cyclophosphamide; D001379:Azathioprine; D003078:Colchicine; D011241:Prednisone
Maladie périodique et périartérite noueuse chez un même malade: coïncidence?