[Neuroarthropathy, kyphoscoliosis and progressive tetraparesis in cervical syringomyelia].
The clinical picture of syringomyelia with special emphasis of its effects of the locomotor system is described on the basis of an individual case history. A 64 year old female patient experienced recurring subluxations of the right shoulder due to a neuroarthropathy. A marked throraco-lumbar kyphoscoliosis was present since childhood. The neurological picture was dominated by symmetrical muscular atrophy of both hands and an incomplete spastic paraparesis. Myelography of high cervical region shows an enlarged epidural space and atrophy of the myelon. MRI reveals a syrinx within the atrophied cervical spinal cord. Most likely the spinal cord has been enlarged and compressed from within by the syrinx which subsequently collapsed leaving the atrophied cervical spinal cord.
Neurologische Abteilung, Rheuma- und Rehabilitationszentrum, Valens.
J
J
Blanco
J
J
Kesselring
D001177:Arthropathy, Neurogenic / Q000175:diagnosis*; D001284:Atrophy; D005260:Female; D006801:Humans; D007738:Kyphosis / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D009133:Muscular Atrophy / Q000175:diagnosis; D009192:Myelography; D011782:Quadriplegia / Q000175:diagnosis*; D012600:Scoliosis / Q000175:diagnosis*; D012783:Shoulder Dislocation / Q000175:diagnosis; D013116:Spinal Cord / Q000473:pathology; D013595:Syringomyelia / Q000175:diagnosis*
Neuroarthropathie, Kyphoskoliose und progrediente Tetraparese bei cervikaler Syringomyelie.