A familial form of incomplete septal cirrhosis.
The clinical features and hepatic histology of a disorder resembling idiopathic portal hypertension and nodular regenerative hyperplasia but most consistent with incomplete septal cirrhosis, occurring in four family members, are described. This represents the first description of the familial occurrence of this entity. Features common to incomplete septal cirrhosis and the noncirrhotic nodular conditions of the liver that may present with complications of portal hypertension are discussed.
Barnett
J L
JL
Department of Internal Medicine, University of Michigan School of Medicine, Ann Arbor.
Appelman
H D
HD
Moseley
R H
RH
D000328:Adult; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000209:etiology / Q000235:genetics; D008103:Liver Cirrhosis / Q000150:complications / Q000235:genetics* / Q000473:pathology*; D008297:Male