Steroid-responsive chorea in moyamoya disease.
We report the case of a 13-year-old boy with disabling chorea due to moyamoya disease. His chorea seemed to improve with steroid therapy. We conclude that steroid therapy may ameliorate moyamoya-associated chorea, and perioperative steroids can confound neurosurgical outcome. We are unable to assess the effect of cerebrovascular bypass procedures on the outcome of chorea in this patient.
Pavlakis
S G
SG
Department of Pediatrics, North Shore University Hospital, New York City, New York.
Schneider
S
S
Black
K
K
Gould
R J
RJ
D000293:Adolescent; D002533:Cerebral Angiography; D002548:Cerebral Revascularization; D002819:Chorea / Q000000981:diagnostic imaging / Q000188:drug therapy* / Q000601:surgery; D003131:Combined Modality Therapy; D003907:Dexamethasone / Q000008:administration & dosage*; D004305:Dose-Response Relationship, Drug; D006801:Humans; D008297:Male; D009072:Moyamoya Disease / Q000000981:diagnostic imaging / Q000188:drug therapy* / Q000601:surgery; D011183:Postoperative Complications / Q000000981:diagnostic imaging / Q000188:drug therapy; D011241:Prednisone / Q000008:administration & dosage*
D003907:Dexamethasone; D011241:Prednisone