title: [A case of total intestinal aganglionosis. 2 years of survival].
abstract: A two-year-old male is presented. Small bowel aganglionosis was proved to extend to 3 cm below ligament of Treitz. Gastrostomy and ileostomy was done. He received his caloric intake by cyclic home parenteral nutrition trough implantable venous system. At eighteen months of age, intestinal transplantation was refused and reoperation was done. The child underwent Ziegler's miotomymiectomy on 60 cm of aganglionic jejunum. Now at twenty seven months of age he receives cyclic parenteral nutrition, and enteral feedings are being increased slowly. The weight/height was at 91 per 100 standard, intestinal motility appears much better on contrast study and he is developmentally a normal child.
authors.affiliation: Departamento de Cirugía Pediátrica, Hospital Infantil La Paz, Madrid.
authors.forename: J C
authors.initials: JC
authors.lastname: López Gútiérrez
authors.forename: J C
authors.initials: JC
authors.lastname: de Agustín
authors.forename: J
authors.initials: J
authors.lastname: Murcia
authors.forename: C
authors.initials: C
authors.lastname: Carrero
authors.forename: R
authors.initials: R
authors.lastname: Muguerza
authors.forename: C
authors.initials: C
authors.lastname: Soto
authors.forename: J G
authors.initials: JG
authors.lastname: Utrilla
authors.forename: L
authors.initials: L
authors.lastname: Lassaletta
mesh_terms: D001706:Biopsy; D002675:Child, Preschool; D003131:Combined Modality Therapy; D006627:Hirschsprung Disease / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D006801:Humans; D007421:Intestine, Small / Q000473:pathology / Q000601:surgery; D008297:Male; D008722:Methods; D010288:Parenteral Nutrition; D011859:Radiography
vernacular_title: Un caso de aganglionismo intestinal total. Dos años de supervivencia.