Epidemiology of lissencephaly type I.
In a cooperative study in The Netherlands 22 patients with lissencephaly type I were collected. In the period 1980-1988, the prevalence of lissencephaly type I in the Netherlands was 11.7 per million births (12.2 for females and 11.0 for males). The 5-year survival rate of patients with a complete or nearly complete agyria (grade 1 or 2) in this study was 54% compared to 91% in patients with a mixture of agyria with pachygyria or complete pachygyria (grade 3 or 4).
de Rijk-van Andel
J F
JF
Department of Neurology, Westeinde Hospital, The Hague, The Netherlands.
Arts
W F
WF
Hofman
A
A
Staal
A
A
Niermeijer
M F
MF
D000015:Abnormalities, Multiple / Q000453:epidemiology* / Q000235:genetics / Q000401:mortality; D000293:Adolescent; D002540:Cerebral Cortex / Q000002:abnormalities*; D002648:Child; D002675:Child, Preschool; D003430:Cross-Sectional Studies; D005260:Female; D006801:Humans; D015994:Incidence; D007223:Infant; D015993:Life Tables; D008297:Male; D009426:Netherlands / Q000453:epidemiology; D012307:Risk Factors; D015996:Survival Rate