Polysplenia syndrome: a case with congenital heart block, infarction of a splenic mass, and a short pancreas.
A case of polysplenia with congenital heart block, infarction of a splenic mass, and a short pancreas was reported. The infant died of severe heart failure at the age of 28 days. Deformity of the SA node was suspected to be the cause of congenital heart block but could not be demonstrated because of some limitations of autopsy procedure. Redundant splenic pedicle might cause infarction of a splenic mass after birth. The author suggests that, in addition to the semi-annular pancreas, the pancreatic anomalies of this syndrome should include the short pancreas.
Sriplung
H
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Department of Pathology, Faculty of Medicine, Prince of Songkla University, Thailand.
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000235:genetics / Q000473:pathology*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000235:genetics / Q000473:pathology*; D006801:Humans; D007231:Infant, Newborn; D007238:Infarction / Q000209:etiology*; D008168:Lung / Q000002:abnormalities*; D008297:Male; D010179:Pancreas / Q000002:abnormalities*; D013154:Spleen / Q000002:abnormalities*