Aplasia of the right aortic cusp in a neonate: a life-threatening but curable anomaly.
A case of absent right aortic cusp causing serious aortic incompetence in a neonate is reported. A "bicuspidalization" repair broke down within 24 hours, but reoperation with annular enlargement and insertion of a 19-mm prosthetic valve resulted in complete recovery. This rare but life-threatening anomaly of the aortic valve can be recognized with Doppler echocardiography. Valve replacement in conjunction with aortic annular enlargement should be performed as primary repair.
Henze
A C
AC
Department of Cardiothoracic Surgery, University Hospital, Uppsala, Sweden.
Malm
T K
TK
Sunnegårdh
J T
JT
Hallberg
M B
MB
D001021:Aortic Valve / Q000002:abnormalities*; D001022:Aortic Valve Insufficiency / Q000209:etiology / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012086:Reoperation