title: Prion diseases in man.
abstract: Human spongiform encephalopathies (HSE) are uncommon neurodegenerative diseases of unknown etiology. Whilst numerous observations provide arguments for an infectious disorder mediated by an unconventional agent of the so-called prion-type, the recent discovery of predisposing allelic variants suggests that HSE might be considered as genetically linked diseases.
authors.affiliation: Hematology-Oncology Department, Centre Hospitalier de Luxembourg.
authors.forename: F
authors.initials: F
authors.lastname: Jacob
authors.forename: F
authors.initials: F
authors.lastname: Ries
authors.forename: M
authors.initials: M
authors.lastname: Dicato
mesh_terms: D000818:Animals; D002417:Cattle; D016643:Encephalopathy, Bovine Spongiform / Q000235:genetics / Q000382:microbiology / Q000635:transmission*; D006801:Humans; D009410:Nerve Degeneration; D009422:Nervous System Diseases / Q000235:genetics / Q000382:microbiology; D011328:Prions
chemical_list: D011328:Prions