title: Idiopathic dilatation of the aorta with dissection in a family without Marfan syndrome.
abstract: Dissection of the aorta is very rare in children, but classically occurs in the presence of Marfan syndrome or other connective tissue disorder. We present a case of spontaneous dissection in a 12-year-old boy whose half brother has an idiopathic dilated aorta and whose mother has also required surgery for dissection of a dilated aorta. No features of connective tissue disorder were present in any family member.
authors.affiliation: Department of Cardiology, Izaak Walton Killam Hospital for Children, Dalhousie University, Halifax, Canada.
authors.forename: D
authors.initials: D
authors.lastname: Teien
authors.forename: J P
authors.initials: JP
authors.lastname: Finley
authors.forename: D A
authors.initials: DA
authors.lastname: Murphy
authors.forename: A
authors.initials: A
authors.lastname: Lacson
authors.forename: J
authors.initials: J
authors.lastname: Longhi
authors.forename: D A
authors.initials: DA
authors.lastname: Gillis
mesh_terms: D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging* / Q000235:genetics; D001011:Aorta / Q000002:abnormalities*; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging* / Q000235:genetics; D001027:Aortography; D002648:Child; D004452:Echocardiography; D005260:Female; D006801:Humans; D008297:Male; D010375:Pedigree