title: [Massive hemothorax: an exceptional complication of Rendu-Osler-Weber disease].
abstract: Hereditary familial telangiectasis is a vascular dysplasia characterized by a triple syndrome: hereditary character, telangiectasias and hemorrhages. Its association with systemic and/or pulmonary arterio-venous fistulae is frequent and can condition several complications: cerebral abscess, digestive hemorrhages, epistaxis, hemoptysis, hypoxemia, polyglobulia, and rarely the appearance of hemothorax. We describe a patient who was admitted in hospital with a hypovolemic shock secondary to a massive hemothorax; during emergency surgery, which was necessary to perform, a pulmonary A-V fistula was observed in the middle lobe. The studies afterwards performed demonstrated that it was a Rendu-Osler-Weber disease with duodenal, hepatic, and cerebral involvement.
authors.affiliation: Departamento de Cuidados Intensivos, Hospital Doce de Octubre, Madrid.
authors.forename: M A
authors.initials: MA
authors.lastname: Blasco Navalpotro
authors.forename: E
authors.initials: E
authors.lastname: Alted López
authors.forename: J A
authors.initials: JA
authors.lastname: Cantalapiedra Santiago
authors.forename: C
authors.initials: C
authors.lastname: Cisneros Alonso
authors.forename: A
authors.initials: A
authors.lastname: Montero Castillo
authors.forename: F
authors.initials: F
authors.lastname: Guillén Ramírez
mesh_terms: D000328:Adult; D006491:Hemothorax / Q000150:complications / Q000209:etiology*; D006801:Humans; D008297:Male; D012769:Shock / Q000209:etiology; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*
vernacular_title: Hemotórax masivo: complicación excepcional de la enfermedad de Rendu-Osler-Weber.