[Idiopathic retroperitoneal fibrosis. An atypical case of multisystem presentation].
Idiopathic retroperitoneal fibrosis (IRF) is a disease difficult to diagnose. It is considered by different authors of autoimmune origin given its similarity to other connective tissue diseases. We present the case of a female patient diagnosed by a postmortem study, of IRF with multiorgan involvement (lymph nodes, serose tissue, liver, spleen, adrenal glands, thyroid and kidneys) and atypical presentation, not finding other similar cases in the national literature.
Castiella Herrero
J
J
Servicio de Medicina Interna, Hospital Clínico Universitario, Zaragoza.
Cía Gómez
P
P
Gallel Vicente
P
P
Martínez Navarro
E
E
Martínez Rodés
P
P
Ramón y Cajal
S
S
D000368:Aged; D001344:Autopsy; D005260:Female; D006801:Humans; D009102:Multiple Organ Failure / Q000209:etiology*; D012185:Retroperitoneal Fibrosis / Q000175:diagnosis*
Fibrosis retroperitoneal idiopática. Un caso atípico de presentación multisistémica.