Effect of polyethylene glycol-modified adenosine deaminase (PEG-ADA) therapy in two ADA-deficient children: measurement of erythrocyte deoxyadenosine triphosphate as a useful tool.
Bory
C
C
Laboratoire de Biochimie, Hôpital Debrousse, Lyon, France.
Boulieu
R
R
Souillet
G
G
Chantin
C
C
Guibaud
P
P
Hershfield
M S
MS
D000243:Adenosine Deaminase / Q000172:deficiency* / Q000627:therapeutic use*; D000255:Adenosine Triphosphate / Q000097:blood*; D015415:Biomarkers / Q000097:blood; D002648:Child; D002675:Child, Preschool; D004912:Erythrocytes / Q000187:drug effects / Q000378:metabolism*; D005260:Female; D006801:Humans; D007223:Infant; D008214:Lymphocytes / Q000187:drug effects / Q000276:immunology; D008297:Male; D016511:Severe Combined Immunodeficiency / Q000097:blood / Q000188:drug therapy* / Q000276:immunology
D015415:Biomarkers; D000255:Adenosine Triphosphate; D000243:Adenosine Deaminase; C051409:pegademase bovine