Entodermal inclusion cyst of the tricuspid valve.
This is a report on an epithelial inclusion cyst covering the septal leaflet of the tricuspid valve. The tumor was an accidental finding in a 5 1/2 years-old boy with congenital heart disease including double-chambered right ventricle, ventricular and atrial septal defects and subvalvular aortic stenosis. Histological examination showed a two-layered ciliated epithelium, typically present in the respiratory system. Embryologic tissue heterotopia arising from sequestered entodermal elements from the primitive foregut during cardiac organogenesis is a possible explanation for the locality and histology of the tumor. To our knowledge, a similar case has never been presented before.
Machens
G
G
Department of Cardiac Surgery, University of Heidelberg, Germany.
Vahl
C F
CF
Hofmann
R
R
Wolf
D
D
Hagl
S
S
D002675:Child, Preschool; D003560:Cysts / Q000150:complications / Q000473:pathology / Q000601:surgery*; D004848:Epithelium; D006330:Heart Defects, Congenital / Q000150:complications / Q000601:surgery; D006349:Heart Valve Diseases / Q000150:complications / Q000473:pathology / Q000601:surgery; D006801:Humans; D008297:Male; D014261:Tricuspid Valve