A case of erythropoietic protoporphyria with severe liver dysfunction suggesting a close relationship between erythrocyte protoporphyrin levels and those of gamma-GTP.
A case of erythropoietic protoporphyria (EPP) with severe acute abdominal pain and jaundice was reported. Erythrocyte protoporphyrin (PP) levels were constantly high, and liver histology showed a slight fibrosis with inflammatory infiltration. During the investigation period of 18 months, erythrocyte PP levels closely paralleled those of serum gamma-GTP.
Watanabe
M
M
Department of Dermatology, Nagasaki University School of Medicine, Japan.
Ohgami
T
T
Nonaka
S
S
Yoshida
H
H
Tanaka
M
M
D000208:Acute Disease; D000328:Adult; D001706:Biopsy; D004912:Erythrocytes / Q000737:chemistry*; D004920:Erythropoiesis; D005355:Fibrosis; D006160:Guanosine Triphosphate / Q000097:blood*; D006801:Humans; D008107:Liver Diseases / Q000097:blood*; D008297:Male; D011164:Porphyrias / Q000097:blood*; D011166:Porphyrins / Q000097:blood*
D011166:Porphyrins; D006160:Guanosine Triphosphate