[Massive hemothorax: an exceptional complication of Rendu-Osler-Weber disease].
Hereditary familial telangiectasis is a vascular dysplasia characterized by a triple syndrome: hereditary character, telangiectasias and hemorrhages. Its association with systemic and/or pulmonary arterio-venous fistulae is frequent and can condition several complications: cerebral abscess, digestive hemorrhages, epistaxis, hemoptysis, hypoxemia, polyglobulia, and rarely the appearance of hemothorax. We describe a patient who was admitted in hospital with a hypovolemic shock secondary to a massive hemothorax; during emergency surgery, which was necessary to perform, a pulmonary A-V fistula was observed in the middle lobe. The studies afterwards performed demonstrated that it was a Rendu-Osler-Weber disease with duodenal, hepatic, and cerebral involvement.
Blasco Navalpotro
M A
MA
Departamento de Cuidados Intensivos, Hospital Doce de Octubre, Madrid.
Alted López
E
E
Cantalapiedra Santiago
J A
JA
Cisneros Alonso
C
C
Montero Castillo
A
A
Guillén Ramírez
F
F
D000328:Adult; D006491:Hemothorax / Q000150:complications / Q000209:etiology*; D006801:Humans; D008297:Male; D012769:Shock / Q000209:etiology; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*
Hemotórax masivo: complicación excepcional de la enfermedad de Rendu-Osler-Weber.