[Initial primary sarcoma of the pulmonary valve and trunk of the pulmonary artery].
Primary sarcomas arising from the trunk or branches of the pulmonary artery are exceedingly rare and usually diagnosed at autopsy. The authors report the case of a 31 year old man referred for investigation of recurrent syncope. Echocardiography, right ventriculography and the thoracic computed tomography led to early diagnosis of a pulmonary artery tumour and surgical resection. Histology revealed a primary sarcoma. The early postoperative course was uncomplicated but one month after surgery a local recurrence was diagnosed at routine echocardiographic examination. The syncopal symptoms recurred seven months after surgery and echocardiography showed tumour recurrence on the interventricular septum and in the pulmonary artery. A second palliative operation was attempted but was unsuccessful because of the size of the tumour.
Grollier
G
G
Service de soins intensifs de cardiologie, CHU Côte de Nacre, Caen.
Montécot
L
L
Galateau
F
F
Hédoire
F
F
Scanu
P
P
Lassaigne
D
D
Valette
B
B
Maïza
D
D
Potier
J C
JC
D000328:Adult; D004452:Echocardiography; D005500:Follow-Up Studies; D006338:Heart Neoplasms / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local / Q000000981:diagnostic imaging*; D011651:Pulmonary Artery; D011664:Pulmonary Valve; D012509:Sarcoma / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000601:surgery
Sarcome intimal primitif de la valve et du tronc de l'artère pulmonaire. Suivi échocardiographique.