Identification of pristanoyl-CoA oxidase and phytanic acid decarboxylation in peroxisomes and mitochondria from human liver: implications for Zellweger syndrome.
Wanders
R J
RJ
Department of Paediatrics, University Hospital Amsterdam, The Netherlands.
van Roermund
C W
CW
Jakobs
C
C
ten Brink
H J
HJ
D002499:Centrifugation, Density Gradient; D003653:Decarboxylation; D006801:Humans; D008830:Microbodies / Q000201:enzymology / Q000378:metabolism*; D008930:Mitochondria, Liver / Q000201:enzymology / Q000378:metabolism*; D010088:Oxidoreductases / Q000032:analysis*; D010831:Phytanic Acid / Q000378:metabolism*; D015211:Zellweger Syndrome / Q000201:enzymology / Q000378:metabolism*
D010831:Phytanic Acid; D010088:Oxidoreductases; C066272:pristanoyl-CoA oxidase