Prion diseases in man.
Human spongiform encephalopathies (HSE) are uncommon neurodegenerative diseases of unknown etiology. Whilst numerous observations provide arguments for an infectious disorder mediated by an unconventional agent of the so-called prion-type, the recent discovery of predisposing allelic variants suggests that HSE might be considered as genetically linked diseases.
Jacob
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F
Hematology-Oncology Department, Centre Hospitalier de Luxembourg.
Ries
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F
Dicato
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M
D000818:Animals; D002417:Cattle; D016643:Encephalopathy, Bovine Spongiform / Q000235:genetics / Q000382:microbiology / Q000635:transmission*; D006801:Humans; D009410:Nerve Degeneration; D009422:Nervous System Diseases / Q000235:genetics / Q000382:microbiology; D011328:Prions
D011328:Prions