[Pulmonary metastasis of a dermatofibrosarcoma].
Progressive and recurrent dermatofibrosarcoma, described by Darier and Ferrand in 1924, is a fibrous skin tumour with essentially local malignancy. The authors report a case with pulmonary metastasis, a rare event as only 13 cases of visceral metastases have been reported in the literature. The clinical course of this case was favourable (follow-up of 5 years), in contrast with the usually pejorative nature of metastatic disease (death after several months to one year following the discovery of the first metastasis).
Grosdidier
G
G
Service de Chirurgie Générale "E" à orientation thoracique, Hôpital Central, Nancy.
Sibille
P
P
Borrelly
J
J
Thomas
C
C
D005354:Fibrosarcoma / Q000473:pathology / Q000556:secondary* / Q000601:surgery; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary* / Q000601:surgery; D008297:Male; D008875:Middle Aged; D009364:Neoplasm Recurrence, Local; D011013:Pneumonectomy; D012878:Skin Neoplasms / Q000473:pathology*
Métastase pulmonaire d'un dermatofibrosarcome.