[Femoral osteosarcoma revealing onset of unifocal Paget's disease. Favourable course with 7-year follow-up].
Sarcomatous degeneration is the most serious complication of Paget's disease, and few cases survive beyond 5 years. The authors report a new case, which occurred in a 62-year-old woman, in which calcifying periarthritis of the hip revealed the presence of a sarcoma developed in a context of a single bone case of Paget's disease affecting the upper extremity of the femur. Diagnosis was histological. The prognostic factors of Paget-related sarcomas are reviewed. The most important are the early timing of diagnosis and a site permitting radical surgical exeresis.
Morlock
G
G
Service de Rhumatologie, Hôpital A. Gayraud, Carcassonne.
Cadène
C
C
Feru
M
M
Durand
J
J
D005260:Female; D005266:Femoral Neoplasms / Q000209:etiology* / Q000473:pathology / Q000503:physiopathology; D005500:Follow-Up Studies; D006801:Humans; D008875:Middle Aged; D010001:Osteitis Deformans / Q000150:complications*; D012516:Osteosarcoma / Q000209:etiology* / Q000473:pathology / Q000503:physiopathology
Ostéosarcome du fémur révélateur d'une maladie de Paget unifocale débutante. Evolution favorable avec un recul de 7 ans.