Idiopathic dilatation of the aorta with dissection in a family without Marfan syndrome.
Dissection of the aorta is very rare in children, but classically occurs in the presence of Marfan syndrome or other connective tissue disorder. We present a case of spontaneous dissection in a 12-year-old boy whose half brother has an idiopathic dilated aorta and whose mother has also required surgery for dissection of a dilated aorta. No features of connective tissue disorder were present in any family member.
Teien
D
D
Department of Cardiology, Izaak Walton Killam Hospital for Children, Dalhousie University, Halifax, Canada.
Finley
J P
JP
Murphy
D A
DA
Lacson
A
A
Longhi
J
J
Gillis
D A
DA
D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging* / Q000235:genetics; D001011:Aorta / Q000002:abnormalities*; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging* / Q000235:genetics; D001027:Aortography; D002648:Child; D004452:Echocardiography; D005260:Female; D006801:Humans; D008297:Male; D010375:Pedigree