title: [Prune belly syndrome. Necropsy study of 2 cases].
abstract: The authors report two cases of Prune Belly syndrome (female and male newborn) with urethral obstruction and other associated malformations: imperforate anus, vaginal septae and bicornuate uterus in the female case; unilateral anorchia and hyaline membrane disease in the male. These findings support the mechanical pathogenic theory. In the cytogenetic studies no chromosomal abnormalities were detected. Both karyotypes were normal.
authors.affiliation: Servicio de Anatomía Patológica, Hospital Clínico Universitario, Valencia, España.
authors.forename: A
authors.initials: A
authors.lastname: Cremades Mira
authors.forename: C
authors.initials: C
authors.lastname: Sánchez Fernández de Sevilla
authors.forename: J
authors.initials: J
authors.lastname: Fons Font
mesh_terms: D005260:Female; D006801:Humans; D015994:Incidence; D007231:Infant, Newborn; D008297:Male; D011535:Prune Belly Syndrome / Q000196:embryology / Q000453:epidemiology / Q000235:genetics / Q000473:pathology*
vernacular_title: Síndrome de Prune Belly. Estudio necrópsico de dos casos.