[Morphologic lung changes in a female patient with Zivert-Kartagener's syndrome].
Histologic and ultrastructural pulmonary changes in a female with a classical Zivert-Kartagener's syndrome are described. Congenital anomalies of the columnar epithelium brushes as well as defects acquired in the process of inflammation (decreased number and various length of bruches with their orientation disturbances, additional doublets and the lack of basal bodies) were revealed at transmission and scanning microscopy level. Follicular bronchiectasis, chronic pneumonia, dystelectasies, emphysema result from the mucociliary clearance disturbance and are of an acquired nature.
Voronina
L M
LM
Kop'eva
T N
TN
Barmina
G V
GV
Zhavoronkov
N A
NA
D000328:Adult; D005260:Female; D006801:Humans; D007619:Kartagener Syndrome / Q000473:pathology*; D008168:Lung / Q000473:pathology*
Morfologicheskie izmeneniia v legkikh u bol'noĭ s sindromom Ziverta-Kartagenera.