title: Tracheobronchomegaly--the Mounier-Kuhn syndrome: report of two cases and review of the literature.
abstract: Tracheobronchomegaly (TBM) is a rare disorder of uncertain aetiology, characterized by marked dilatation of the trachea and main bronchi, bronchiectasis and recurrent lower respiratory tract infections. Two patients with TBM are presented. In one case, a marked decrease of elastic and smooth muscle tissue was present in the bronchial biopsy specimens, obtained by rigid bronchoscopy. The airways of the second patient were visualized using computed tomography. The dimensions of the airways of our patients are compared with the normal values supplied in the literature.
authors.affiliation: Dept. of Respiratory Diseases, University Hospital, Ghent, Belgium.
authors.forename: J
authors.initials: J
authors.lastname: Van Schoor
authors.forename: G
authors.initials: G
authors.lastname: Joos
authors.forename: R
authors.initials: R
authors.lastname: Pauwels
mesh_terms: D001706:Biopsy; D001980:Bronchi / Q000473:pathology; D001995:Bronchography; D006801:Humans; D008297:Male; D008875:Middle Aged; D014057:Tomography, X-Ray Computed; D014137:Tracheobronchomegaly / Q000000981:diagnostic imaging / Q000473:pathology