Hereditary gingival fibromatosis in a family with the Zimmermann-Laband syndrome.
Hereditary gingival fibromatosis is frequently an isolated condition of little consequence apart from a cosmetic problem and occasional associations with hypertrichosis and/or epilepsy. There are, however, several uncommon or rare eponymous syndromes described in which gingival fibromatosis can be a feature: these include the Zimmermann-Laband, Murray-Puretic-Drescher, Rutherfurd, Cowden and Cross syndromes. This paper describes two siblings with features of the rare Zimmermann-Laband syndrome and discusses the major aspects of this and other eponymous syndromes that may be associated with hereditary gingival fibromatosis.
Bakaeen
G
G
Faculty of Dentistry, University of Jordan, Amman.
Scully
C
C
D000293:Adolescent; D002648:Child; D004431:Ear, External / Q000002:abnormalities*; D005260:Female; D005351:Fibromatosis, Gingival / Q000235:genetics*; D005385:Fingers / Q000002:abnormalities*; D006801:Humans; D007592:Joint Diseases / Q000473:pathology; D008297:Male; D009264:Nails, Malformed; D009666:Nose / Q000002:abnormalities*; D013577:Syndrome; D014034:Toes / Q000002:abnormalities