Gorlin's syndrome with associated odontogenic cysts.
Multiple maxillary and mandibular cysts are principle features of basal cell nevus syndrome (Gorlin-Goltz). We present cases from an affected family in which magnetic resonance imaging (MRI) was helpful in evaluation of the cystic lesions. A middle ear anomaly was identified which may represent an additional abnormality associated with the syndrome.
Lovin
J D
JD
Department of Radiology, Womack Army Hospital, Fort Bragg, North Carolina.
Talarico
C L
CL
Wegert
S L
SL
Gaynor
L F
LF
Sutley
S S
SS
D000293:Adolescent; D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000150:complications / Q000175:diagnosis* / Q000235:genetics; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008336:Mandibular Diseases / Q000175:diagnosis* / Q000209:etiology / Q000235:genetics; D008439:Maxillary Diseases / Q000175:diagnosis* / Q000209:etiology / Q000235:genetics; D008875:Middle Aged; D009807:Odontogenic Cysts / Q000175:diagnosis* / Q000209:etiology / Q000235:genetics; D014057:Tomography, X-Ray Computed