Nevoid basal cell carcinoma syndrome. A case report.
Nevoid basal cell carcinoma syndrome is an autosomal dominant disorder and is characterized by a great variety of signs and symptoms. The most important are a characteristic facies, the occurrence of basal cell carcinomas and odontogenic keratocysts. In view of the neoplastic skin change, constant review of the patients is indicated. Any jaw film revealing two or more dentigerous or follicular cysts should alert the clinician to the possibility of this underlying syndrome.
Piattelli
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Dental School, University of Chieti, Italy.
D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000175:diagnosis* / Q000235:genetics; D003803:Dentigerous Cyst / Q000150:complications / Q000601:surgery; D005149:Facial Expression; D005260:Female; D005497:Follicular Cyst / Q000150:complications / Q000601:surgery; D005799:Genes, Dominant; D006801:Humans; D011862:Radiography, Panoramic