The Peutz-Jeghers syndrome. Case reports.
Two additional cases of Peutz-Jeghers syndrome are described. One of them, a 19 year-old female, is a sporadic case, whereas in the other case, also a 19 year-old female, there are two members of the family with the Peutz-Jeghers syndrome. A review of some salient features of this entity is made. These include clinical presentation, histopathological features, malignant potential and treatment.
Dorfman
S
S
Department of Surgery, Hospital General del Sur, Maracaibo, Venezuela.
Talbot
I C
IC
Cardozo
J
J
Tjon
M
M
Camacho
S
S
D000328:Adult; D005260:Female; D006801:Humans; D010580:Peutz-Jeghers Syndrome / Q000175:diagnosis / Q000235:genetics