[Cerebrovascular episodes in chronic liver diseases and terminal nephrotic syndrome. A case of amyloidosis associated with paraproteinemia IgA-lambda].
The authors describe a case of amyloidosis associated with an electrophoretic picture, characterized by a monoclonal band with an M component in the alpha 2 and beta regions, in presence of para IgA-lambda. The case casually discovered in the course of a cerebral vascular manifestation and confirmed by bioptic exams, had negative results after four years due to an extremely progressive course involving intestine, liver and kidney, as a consequence of the extension of amyloidosis deposits.
Tenna
M
M
Centro Anziani, USL RM 7, Roma.
Giorgetti
G M
GM
Tenna
S
S
Carratelli
L E
LE
Balistreri
P
P
D000686:Amyloidosis / Q000097:blood / Q000150:complications*; D002561:Cerebrovascular Disorders / Q000097:blood / Q000209:etiology*; D005260:Female; D006801:Humans; D007070:Immunoglobulin A / Q000097:blood*; D007146:Immunoglobulin lambda-Chains / Q000097:blood*; D008107:Liver Diseases / Q000097:blood / Q000150:complications*; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000097:blood / Q000150:complications*; D010265:Paraproteinemias / Q000097:blood / Q000209:etiology*
D007070:Immunoglobulin A; D007146:Immunoglobulin lambda-Chains
Da un episodio vascolare cerebrale all'epatopatia cronica e sindrome nefrosica terminale. Storia di una amiloidosi associata a paraproteinemia IgA-lambda.