[Heart amyloidosis with enormous cardiomegaly ("the king of hearts")].
A case is presented of a 74 years old man with systemic hypertension, congestive heart failure and history of heart infarction in the past. The physical findings revealed: blood pressure - 130/80 mmHg, arrhythmia and symptoms of congestion in systemic and pulmonary circulation. Ecg tracing showed multifocal atrial rhythm about 90 bpm., very low QRS voltage and lack of R waves in precordial V1-V4. On autopsy an enormous enlargement of the whole heart (1005 g) was found. Microscopical investigation revealed abundant amyloid deposits in the muscle of atria, ventricles and sinus node, disseminated atheromatous changes in the coronary system with no critical narrowing (more than 75% of lumen area). No sings of healed infarct were find. This is the first published case of so called "the king of hearts" due to amyloidosis.
Lesiak
M
M
I Kliniki Kardiologii Instytutu Kardiologii Akademii Medycznej im. K. Marcinkowskiego w Poznaniu.
Pyda
M
M
Grajek
S
S
D000368:Aged; D000686:Amyloidosis / Q000150:complications / Q000473:pathology*; D006332:Cardiomegaly / Q000209:etiology*; D009202:Cardiomyopathies / Q000150:complications / Q000473:pathology*; D006801:Humans; D008297:Male
Amyloidoza serca z niezwykłym jego przerostem ("the king of hearts").