Behçet's syndrome with childhood onset.
Behçet's syndrome is a multisystemic disease of vasculitic nature. Main symptoms consist of oral and genital ulceration, uveitis and skin lesions, mainly erythema nodosum. Other features may evolve: arthritis, thrombophlebitis, gastrointestinal, cardiovascular and neurologic lesions. The disease usually manifests in early adulthood, childhood onset is rare. There exists a male preponderance and a genetic disposition. The course of Behçet's syndrome in 5 patients with childhood onset is described.
Häfner
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R
Rheuma-Kinderklinik Garmisch-Partenkirchen, Germany.
Truckenbrodt
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H
D000328:Adult; D001528:Behcet Syndrome / Q000175:diagnosis* / Q000235:genetics; D002648:Child; D006801:Humans; D008297:Male