title: Bilateral pure gonadoblastoma in a 46 XY individual--a case report.
abstract: We report here a rare case of bilateral pure gonadoblastoma which accounts for only 0.2% of all ovarian tumours seen at Universiti Kebangsaan Malaysia from 1980 to 1987. This tumour occurred in an 18 year old Chinese "female" who presented with primary amenorrhoea. Examination showed a phenotypic female with poorly developed external gentalia. Exploratory laparotomy revealed a hypoplastic uterus, rudimentary fallopian tubes and streak gonads. Histological examination of the gonads showed a mixed tumour comprising large germ cells and smaller sex cord derivatives arranged in characteristic nests or islands containing hyaline material.
authors.affiliation: Jabatan Obst. & Gynae., Fakulti Perubatan, Universiti Kebangsaan Malaysia, Jalan Raja Muda Abdul Aziz, Kuala Lumpur.
authors.forename: M A
authors.initials: MA
authors.lastname: Siti Aishah
authors.forename: R
authors.initials: R
authors.lastname: Chandran
authors.forename: H
authors.initials: H
authors.lastname: Tahir
mesh_terms: D000293:Adolescent; D004407:Dysgerminoma / Q000235:genetics / Q000473:pathology* / Q000601:surgery; D005260:Female; D006801:Humans; D007621:Karyotyping; D010051:Ovarian Neoplasms / Q000235:genetics / Q000473:pathology* / Q000601:surgery