[Benign systemic mastocytosis: report of 2 cases].
The case histories of two patients with benign systemic mastocytosis with skin involvement are presented. The first patient had urticaria pigmentosa diagnosed at the age of 2 months, and developed systemic disease within two years. The second presented urticaria pigmentosa at the age of 22 years while benign systemic mastocytosis was diagnosed 30 years later. The clinical findings in both cases were: skin involvement, hepatosplenomegaly and abdominal pain. The second patient had myelofibrosis. There was a favorable response to H1 and H2 histamine antagonist and ketotifen.
Velloso
E D
ED
Disciplina de Hematologia e Hemoterapia, Hospital das Clínicas da Faculdade de Medicina, Universidade de São Paulo.
Beitler
B
B
Chamone
D A
DA
D000293:Adolescent; D001853:Bone Marrow / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D008415:Mastocytosis / Q000188:drug therapy / Q000473:pathology*; D008875:Middle Aged; D011379:Prognosis; D014582:Urticaria Pigmentosa / Q000188:drug therapy / Q000473:pathology
Mastocitose sistêmica benigna: relato de dois casos.