Pulmonary blastoma: a rare childhood malignancy.
Pulmonary blastoma is a rare primary malignancy of the lung, with few cases reported in children. The tumor consists of mesenchymal and epithelial components resembling the fetal lung. Seven children (aged 18 months to 5 years) with pulmonary blastoma were studied. The pulmonary radiographic patterns seen were a large, space-occupying solid mass with opacification of the hemithorax and preexisting cystic disease with a small solid tumor component. Computed tomographic images showed a low-attenuation mass with whorls of high-attenuation solid tissue. Four of the seven patients died within 2 years despite surgery and therapy; of the three surviving patients, one has recurrent disease.
Senac
M O
MO
Department of Radiology, Childrens Hospital Los Angeles, CA 90027.
Wood
B P
BP
Isaacs
H
H
Weller
M
M
D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008175:Lung Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D008297:Male; D009373:Neoplasms, Germ Cell and Embryonal / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D011859:Radiography