title: Repair of complete atrioventricular canal. 15 year's experience.
abstract: Corrective surgery for complete atrioventricular canal was performed over a 15-year period on 72 patients, 49 of whom had Down's syndrome: 46 were without major associated cardiac anomalies and 15 had previously undergone pulmonary artery banding. The pressures in the right and left ventricles equilibrated in 77% of the patients. The early mortality rate was 18% and the late mortality 7%. At follow-up 4% of the patients had severe mitral incompetence and 6% had severe tricuspid incompetence. The mean reduction of pulmonary artery pressure was 40 mmHg. The mean peak systolic pressure ratio between pulmonary artery and aorta was 0.73 before repair and had fallen to 0.38 at follow-up catheterization, when 88% of the patients were asymptomatic. Early repair in the first year of life is nowadays preferred in order to avoid progressive pulmonary vascular disease. Although the alternative of first-stage pulmonary artery banding gave lower (13%) mortality at the corrective operation, it cannot be recommended if atrioventricular valvular incompetence is significant.
authors.affiliation: Pediatric Department, St Göran's Children's Hospital, Stockholm, Sweden.
authors.forename: C
authors.initials: C
authors.lastname: Frid
authors.forename: C
authors.initials: C
authors.lastname: Thorén
authors.forename: K
authors.initials: K
authors.lastname: Böök
authors.forename: V O
authors.initials: VO
authors.lastname: Björk
mesh_terms: D006328:Cardiac Catheterization; D002675:Child, Preschool; D003250:Constriction; D004314:Down Syndrome / Q000150:complications; D004694:Endocardial Cushion Defects / Q000150:complications / Q000401:mortality / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D006976:Hypertension, Pulmonary / Q000517:prevention & control; D007223:Infant; D008297:Male; D011651:Pulmonary Artery; D011669:Pulmonary Wedge Pressure / Q000502:physiology; D013997:Time Factors