title: [Primary segmental sclerosing cholangitis associated with Sjögren's syndrome].
abstract: We report the case of a patient with primary sclerosing cholangitis associated with Sjögren's syndrome and Raynaud's phenomenon, an uncommon association. The presence of periportal lymph nodes with features similar to those described in autoimmune diseases suggests an immune pathogenesis of the disease. The localized and segmentary involvement of the common duct is also an uncommon finding. The pathogenetic and therapeutic aspects are discussed.
authors.affiliation: Sección de Anatomía Patológica, Hospital Universitario de Valme, Sevilla.
authors.forename: P
authors.initials: P
authors.lastname: Guerrero
authors.forename: M
authors.initials: M
authors.lastname: Martín
authors.forename: J M
authors.initials: JM
authors.lastname: Conde
authors.forename: M
authors.initials: M
authors.lastname: Castro
authors.forename: M C
authors.initials: MC
authors.lastname: Rodríguez
authors.forename: L
authors.initials: L
authors.lastname: Castilla
authors.forename: P
authors.initials: P
authors.lastname: Guillén
mesh_terms: D000368:Aged; D015209:Cholangitis, Sclerosing / Q000150:complications* / Q000276:immunology; D005260:Female; D006801:Humans; D011928:Raynaud Disease / Q000150:complications; D012859:Sjogren's Syndrome / Q000150:complications* / Q000276:immunology
vernacular_title: Colangitis esclerosante primaria segmentaria asociada a síndrome de Sjögren.