Hypoplastic left heart syndrome with rhabdomyoma of the left ventricle.
A case of primary cardiac tumor with hypoplastic left heart syndrome (HLH) is presented. Sonographic examination at 32 weeks' gestation revealed a large tumor in the left ventricle of the fetal heart. The newborn died of congestive heart failure at 11 days of age. Autopsy demonstrated a large tumor in the left ventricle obliterating most of the left ventricular cavity, aortic atresia, and hypoplastic ascending aorta. Microscopically, the cardiac tumor showed "spider-cells" characteristics of rhabdomyoma.
Watanabe
T
T
Department of Pediatrics, National Nagoya Hospital, Japan.
Hojo
Y
Y
Kozaki
T
T
Nagashima
M
M
Ando
M
M
D005260:Female; D005317:Fetal Growth Retardation / Q000150:complications* / Q000000981:diagnostic imaging; D005318:Fetal Heart / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006338:Heart Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000196:embryology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D012207:Rhabdomyoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000196:embryology; D014463:Ultrasonography