Congenital agammaglobulinemia presenting with ecthyma gangrenosum.
Two males with presumed X-linked agammaglobulinemia (X-LA) presented with ecthyma gangrenosum. This is an unusual presentation of this syndrome. Possible causes are discussed.
Nussinovitch
M
M
Department of Pediatrics, Hasharon Hospital, Petach Tikvah, Isreal.
Frydman
M
M
Cohen
H A
HA
Varsano
I
I
D000361:Agammaglobulinemia / Q000150:complications / Q000151:congenital* / Q000175:diagnosis; D002423:Cause of Death; D002675:Child, Preschool; D004473:Ecthyma / Q000150:complications* / Q000175:diagnosis / Q000382:microbiology; D006801:Humans; D007223:Infant; D008297:Male; D011552:Pseudomonas Infections / Q000150:complications* / Q000175:diagnosis / Q000382:microbiology