[Perioperative treatment of a patient with myotonic muscular dystrophy (Curschmann-Steinert disease)].
The perioperative period is hazardous for patients with neuromuscular disorder. In case of dystrophia myotonica the anaesthesist must avoid all stimuli that may cause a myotonic crisis. If neuromuscular blockade is required, the moderately long-acting vecuronium bromide seems to be the drug of first choice. Blockade and recovery should be monitored. Postoperative pulmonary complications can be minimised by using regional anaesthetic techniques including epidural anaesthesia with local anaesthetics and/or opioids.
Thölke
M H
MH
Institut für Anästhesie, Klinikum Wuppertal-Barmen.
Tolksdorf
W
W
Mitrenga
I
I
D000768:Anesthesia, General / Q000379:methods*; D005743:Gastrectomy; D006801:Humans; D008297:Male; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000150:complications / Q000235:genetics*; D009466:Neuromuscular Blocking Agents / Q000008:administration & dosage; D011183:Postoperative Complications / Q000517:prevention & control; D013577:Syndrome
D009466:Neuromuscular Blocking Agents
Perioperative Behandlung eines Patienten mit myotoner Muskeldystrophie (M. Curschmann-Steinert).