title: Inflammatory pseudotumor of the choroid plexus in Sjögren's disease.
abstract: We report an unusual case of inflammatory pseudotumor of the choroid plexus of the right lateral ventricle, manifesting as an intraventricular mass and causing unilateral hydrocephalus in a 48-year-old man who suffered from Sjögren's disease and subacute cutaneous lupus erythematosus. The lesion obliterated the normal choroidal architecture by a mixed chronic inflammatory process that was associated with reactive connective tissue changes. Immunohistochemical studies showed no light-chain restriction in the cells, and residual islands of transthyretin-positive epithelial cells were identified, implicating the choroid plexus origin of the mass.
authors.affiliation: Department of Pathology (Neuropathology), Stanford University Medical Center, California.
authors.forename: Y
authors.initials: Y
authors.lastname: Chang
authors.forename: D S
authors.initials: DS
authors.lastname: Horoupian
authors.forename: B
authors.initials: B
authors.lastname: Lane
authors.forename: R D
authors.initials: RD
authors.lastname: Fross
authors.forename: L T
authors.initials: LT
authors.lastname: Smyth
authors.forename: R J
authors.initials: RJ
authors.lastname: Seiling
mesh_terms: D002551:Cerebral Ventricle Neoplasms / Q000209:etiology*; D002831:Choroid Plexus; D005350:Fibroma / Q000209:etiology* / Q000473:pathology; D006801:Humans; D006849:Hydrocephalus / Q000209:etiology; D008178:Lupus Erythematosus, Cutaneous / Q000150:complications; D008297:Male; D008875:Middle Aged; D012859:Sjogren's Syndrome / Q000150:complications*