title: Branched-chain amino acid-free parenteral nutrition in the treatment of acute metabolic decompensation in patients with maple syrup urine disease.
authors.affiliation: Division of Biochemical Development and Molecular Diseases, Children's Hospital of Philadelphia, PA 19104.
authors.forename: G T
authors.initials: GT
authors.lastname: Berry
authors.forename: R
authors.initials: R
authors.lastname: Heidenreich
authors.forename: P
authors.initials: P
authors.lastname: Kaplan
authors.forename: F
authors.initials: F
authors.lastname: Levine
authors.forename: A
authors.initials: A
authors.lastname: Mazur
authors.forename: M J
authors.initials: MJ
authors.lastname: Palmieri
authors.forename: M
authors.initials: M
authors.lastname: Yudkoff
authors.forename: S
authors.initials: S
authors.lastname: Segal
mesh_terms: D000138:Acidosis / Q000628:therapy; D000597:Amino Acids, Branched-Chain / Q000097:blood; D002648:Child; D002675:Child, Preschool; D003681:Dehydration / Q000628:therapy; D004750:Enteral Nutrition; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D008375:Maple Syrup Urine Disease / Q000628:therapy*; D010288:Parenteral Nutrition / Q000379:methods*
chemical_list: D000597:Amino Acids, Branched-Chain