Histiocytic cytophagic panniculitis: report of a case in a 12-year-old girl.
We report a 12-year-old girl with nodular skin lesions, fever, pancytopenia, coagulation defects and a fatal outcome within 4 months. Histopathology revealed proliferation of histiocytes with haemophagocytosis in skin, perivisceral fat and haemopoietic organs. The symptoms were most consistent with cytophagic histiocytic panniculitis.
Department of Paediatrics, La Paz Hospital, Madrid, Spain.
J
J
Garcia-Consuegra
M I
MI
Barrio
E
E
Fonseca
J I
JI
Rodriguez
F
F
Contreras
D001778:Blood Coagulation Disorders / Q000150:complications; D002648:Child; D005260:Female; D015614:Histiocytosis / Q000150:complications* / Q000473:pathology; D006801:Humans; D010198:Pancytopenia / Q000150:complications*; D015434:Panniculitis / Q000150:complications* / Q000473:pathology; D010587:Phagocytosis