Childhood eosinophilic fasciitis presenting as inflammatory polyarthritis and associated with selective IgA deficiency.
A 13 year old school boy presented with seronegative inflammatory polyarthritis after a flu-like illness. Four months later clinical features of eosinophilic fasciitis became apparent. After histological diagnosis treatment was started with prednisone 40 mg daily, with a good response. Routine investigations showed persistent selective IgA deficiency.
Queen Elizabeth Hospital for Rheumatic Disease and Rehabilitation, Rotoura, New Zealand.
D W
DW
Ching
J P
JP
Petrie
D000293:Adolescent; D001168:Arthritis / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology; D003238:Connective Tissue / Q000473:pathology; D004406:Dysgammaglobulinemia / Q000150:complications* / Q000188:drug therapy / Q000473:pathology; D004802:Eosinophilia / Q000150:complications* / Q000188:drug therapy / Q000473:pathology; D005208:Fasciitis / Q000150:complications* / Q000188:drug therapy / Q000473:pathology; D006801:Humans; D007070:Immunoglobulin A / Q000378:metabolism*; D008297:Male; D009132:Muscles / Q000473:pathology; D011239:Prednisolone / Q000627:therapeutic use
D007070:Immunoglobulin A; D011239:Prednisolone