[Surgical repair of Scimitar syndrome with azygos connection by extracardiac conduit between right pulmonary vein and left atrium].
We present a surgical case of 41-year-old woman with Scimitar syndrome. Preoperative catheterization showed azygos connection and L-R shunt ratio of 45% without intracardiac malformations. To our knowledge, this combination has not been previously reported. At operation the right single pulmonary vein was found and drained into the inferior vena cava below the diaphragm. Because of counter clockwise rotation of the heart the distance of the scimitar vein and the left atrium was too long for direct anastomosis, a polytetrafluoroethylene tube (10 mm in diameter) was utilized for an extracardiac conduit using cardiopulmonary bypass. Postoperative course was uneventful. We conclude that this technique is effective for this syndrome with a large amount of L-R shunt and a sufficient patency is expected.
Noji
S
S
Department of Cardiovascular Surgery, Osaka National Hospital, Japan.
Kitamura
N
N
Yamaguchi
A
A
Otaki
M
M
Miki
T
T
Tamura
H
H
D000328:Adult; D001401:Azygos Vein / Q000002:abnormalities*; D005260:Female; D006325:Heart Atria / Q000601:surgery; D006801:Humans; D008722:Methods; D011667:Pulmonary Veins / Q000601:surgery; D012587:Scimitar Syndrome / Q000601:surgery*