Histiocytic cytophagic panniculitis: report of a case in a 12-year-old girl.
We report a 12-year-old girl with nodular skin lesions, fever, pancytopenia, coagulation defects and a fatal outcome within 4 months. Histopathology revealed proliferation of histiocytes with haemophagocytosis in skin, perivisceral fat and haemopoietic organs. The symptoms were most consistent with cytophagic histiocytic panniculitis.
Garcia-Consuegra
J
J
Department of Paediatrics, La Paz Hospital, Madrid, Spain.
Barrio
M I
MI
Fonseca
E
E
Rodriguez
J I
JI
Contreras
F
F
D001778:Blood Coagulation Disorders / Q000150:complications; D002648:Child; D005260:Female; D015614:Histiocytosis / Q000150:complications* / Q000473:pathology; D006801:Humans; D010198:Pancytopenia / Q000150:complications*; D015434:Panniculitis / Q000150:complications* / Q000473:pathology; D010587:Phagocytosis