The impact of a syndromal diagnosis on surgery for congenital minor ear anomalies.
Between 1964 and 1986, 104 ears of 86 patients with a minor congenital ear anomaly underwent an exploratory tympanotomy at the Institute of Otorhinolaryngology of the University Hospital Nijmegen. A classification of these anomalies is proposed based on the surgical findings and results. The 4 groups in this classification are: isolated stapes ankylosis, stapes ankylosis associated with an anomaly of the malleus and incus, an isolated anomaly of the malleus and incus with a mobile stapes footplate and finally, aplasia of the oval and/or round window. In a total of 29 ears (22 patients) out of these 104 ears, the anomaly formed part of a syndrome. The various syndromes and the anomalies encountered are discussed. The impact of a syndromal diagnosis on the outcome of reconstructive ear surgery is discussed per syndrome.
Institute of Otorhinolaryngology, University Hospital of Nijmegen, The Netherlands.
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Cremers
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Teunissen
D000015:Abnormalities, Multiple / Q000473:pathology; D002648:Child; D004423:Ear / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D012189:Retrospective Studies