Pycnodysostosis. Report of a case and review of the Japanese literature, with emphasis on oral and maxillofacial findings.
We report a case of pycnodysostosis and review 54 cases of this syndrome in the Japanese literature, with special emphasis on oral and maxillofacial findings. Common findings were as follows: hypoplasia of maxilla and mandible, hypopneumatization of the maxillary sinuses, loss of mandibular angle, a grooved palate, and malpositioned teeth.
First Department of Oral Surgery, School of Dentistry, Higashi-Nippon-Gakuen University, Tobetsu-cho, Japan.
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Muto
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Michiya
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Taira
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Murase
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Kanazawa
D004392:Dwarfism; D004413:Dysostoses; D005260:Female; D006801:Humans; D007564:Japan; D007569:Jaw Abnormalities; D008875:Middle Aged; D009056:Mouth Abnormalities; D013577:Syndrome; D014071:Tooth Abnormalities