title: Bilateral acoustic neurofibromatosis (neurofibromatosis 2): a disorder distinct from von Recklinghausen's neurofibromatosis (neurofibromatosis 1).
abstract: A case report of bilateral acoustic neurofibromatosis (NF-2) is presented with temporal bone histopathology. The distinct clinical and genetic features of NF-2 are reviewed in the context of recent data that show it to be a disorder distinct from classic von Recklinghausen's disease (NF-1).
authors.affiliation: Department of Otology, Harvard Medical School, Boston.
authors.forename: P B
authors.initials: PB
authors.lastname: Flexon
authors.forename: J B
authors.initials: JB
authors.lastname: Nadol
authors.forename: H F
authors.initials: HF
authors.lastname: Schuknecht
authors.forename: W W
authors.initials: WW
authors.lastname: Montgomery
authors.forename: R L
authors.initials: RL
authors.lastname: Martuza
mesh_terms: D000328:Adult; D007758:Ear, Inner / Q000473:pathology; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000235:genetics; D016518:Neurofibromatosis 2 / Q000175:diagnosis / Q000235:genetics / Q000473:pathology; D013701:Temporal Bone / Q000473:pathology