title: Malignant peripheral nerve sheath tumor (malignant schwannoma) of urinary bladder in von Recklinghausen neurofibromatosis.
abstract: Von Recklinghausen neurofibromatosis occurs in 1 in 3,000 live births; however, urologic manifestations are rare. There have been over 40 reported cases of neurofibroma of the bladder. Malignant degeneration of subcutaneous neurofibroma occurs in about 5 to 10 percent of patients. We believe we present the second reported case of a malignant peripheral nerve sheath tumor involving the bladder in a patient with this disorder.
authors.affiliation: Department of Urology, Wayne State University, Detroit, Michigan.
authors.forename: P E
authors.initials: PE
authors.lastname: Rober
authors.forename: J B
authors.initials: JB
authors.lastname: Smith
authors.forename: W
authors.initials: W
authors.lastname: Sakr
authors.forename: J M
authors.initials: JM
authors.lastname: Pierce
mesh_terms: D000328:Adult; D006801:Humans; D008297:Male; D009442:Neurilemmoma / Q000209:etiology* / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000150:complications*; D001749:Urinary Bladder Neoplasms / Q000209:etiology* / Q000473:pathology