Malignant peripheral nerve sheath tumor (malignant schwannoma) of urinary bladder in von Recklinghausen neurofibromatosis.
Von Recklinghausen neurofibromatosis occurs in 1 in 3,000 live births; however, urologic manifestations are rare. There have been over 40 reported cases of neurofibroma of the bladder. Malignant degeneration of subcutaneous neurofibroma occurs in about 5 to 10 percent of patients. We believe we present the second reported case of a malignant peripheral nerve sheath tumor involving the bladder in a patient with this disorder.
Rober
P E
PE
Department of Urology, Wayne State University, Detroit, Michigan.
Smith
J B
JB
Sakr
W
W
Pierce
J M
JM
D000328:Adult; D006801:Humans; D008297:Male; D009442:Neurilemmoma / Q000209:etiology* / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000150:complications*; D001749:Urinary Bladder Neoplasms / Q000209:etiology* / Q000473:pathology