title: [A registry of medullary thyroid cancer in West Germany].
abstract: A register for medullary thyroid carcinoma (MTC) in FRG has been set up by the "German Medullary Thyroid Carcinoma Study Group" in 1988. The aim is to provide a basis for collaborative work on MTC especially in the hereditary forms (i.e. multiple endocrine neoplasia [MEN] type IIa, IIb). For these hereditary varieties reliable screening tests exist and, if the disease is detected by family screening in an early stage, curative surgery is possible. Until now 408 patients (234 female, 174 male) with MTC have been reported by 17 cooperative centers. The mean age at diagnosis was 45.5 years. 25% (n = 104) are hereditary forms, most of them MEN IIa (n = 86), 13 are MEN IIb and 18 belong to the familial variety without other endocrinopathy. The mean age at diagnosis for MEN IIa was 36.5 years, MEN IIb 26.9 and for the pure familial form 27.5 years. As 33 patients per year have been diagnosed since 1982, nearly 25% of all expected cases of MTC in FRG have been registered.
authors.affiliation: Medizinische Universitätsklinik, Heidelberg.
authors.forename: F
authors.initials: F
authors.lastname: Raue
authors.forename: M
authors.initials: M
authors.lastname: Späth-Röger
authors.forename: J
authors.initials: J
authors.lastname: Winter
authors.forename: G
authors.initials: G
authors.lastname: Benker
authors.forename: P
authors.initials: P
authors.lastname: Buhr
authors.forename: R
authors.initials: R
authors.lastname: Dorn
authors.forename: H
authors.initials: H
authors.lastname: Dralle
authors.forename: A
authors.initials: A
authors.lastname: Frilling
authors.forename: J
authors.initials: J
authors.lastname: Herrmann
authors.forename: I
authors.initials: I
authors.lastname: Hörnig
mesh_terms: D000328:Adult; D000368:Aged; D002277:Carcinoma / Q000453:epidemiology*; D003430:Cross-Sectional Studies; D005260:Female; D005860:Germany, West / Q000453:epidemiology; D006801:Humans; D015994:Incidence; D008297:Male; D008875:Middle Aged; D009377:Multiple Endocrine Neoplasia / Q000453:epidemiology*; D012042:Registries; D013964:Thyroid Neoplasms / Q000453:epidemiology*
vernacular_title: Register für das medulläre Schilddrüsenkarzinom in der Bundesrepublik Deutschland.