[Cerebellar cavernous angioma, cervical dystonia and crossed cortical diaschisis].
On four occasions since 1978, this 53 year-old woman presented with a right hemicorporal hypotonia, symptomatic of a hemispheric cerebellar syndrome. In 1981, she experienced the progressive development of a cervical dystonia. CT scan and RM scan showed a cavernous angioma in the right cerebellar hemisphere. The 18F-2-fluoro-2-deoxy-glucose PET scan revealed a right cerebellar and a contralateral cortical and striatal hypometabolism. This crossed cerebello-cortical diaschisis can be interpreted as a functional interruption of the cerebello-cerebral pathways. This case raises the question of the role played by a cerebellar lesion in the development of a focal dystonia.
Tranchant
C
C
Clinique Neurologique, Hôpital Central, Strasbourg.
Maquet
J
J
Eber
A M
AM
Dietemann
J L
JL
Franck
P
P
Warter
J M
JM
D002528:Cerebellar Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging; D002531:Cerebellum / Q000378:metabolism*; D002540:Cerebral Cortex / Q000378:metabolism*; D004421:Dystonia / Q000209:etiology*; D005260:Female; D006392:Hemangioma, Cavernous / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D008875:Middle Aged; D009334:Neck Muscles; D014055:Tomography, Emission-Computed
Angiome caverneux cérébelleux, dystonie cervicale et diaschisis cortical croisé.