Innominate artery involvement in type IV Ehlers-Danlos syndrome.
We report two cases of innominate artery involvement in patients with Ehlers-Danlos syndrome. In the first patient, spontaneous dissection of the innominate artery was treated successfully. In the other, the patient died of spontaneous rupture of the innominate artery in the early postoperative course after operation for aneurysm of the celiac artery. Arterial complications occurring in Ehlers-Danlos syndrome are rare but pose difficult diagnostic and therapeutic problems for the vascular surgeon due to arterial wall fragility.
Valverde
A
A
Service de Chirurgie Vasculaire et Thoracique, Hôpital André Mignot, Le Chesnay, France.
Tricot
J F
JF
de Crepy
B
B
Bakdach
H
H
Djabbari
K
K
D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D016122:Brachiocephalic Trunk / Q000000981:diagnostic imaging / Q000601:surgery; D002445:Celiac Artery / Q000000981:diagnostic imaging / Q000601:surgery; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000473:pathology; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011859:Radiography; D012422:Rupture, Spontaneous