Malignant renal tumors in tuberous sclerosis.
Although the frequency of renal carcinoma in tuberous sclerosis is lower than that in von Hippel-Lindau syndrome, it occurs bilaterally in 43 percent of patients at a median age of twenty-eight years. Concomitant hamartomas and hyperplastic cystic components may confound the histologic diagnosis of renal carcinoma in tuberous sclerosis.
Washecka
R
R
Department of Pediatric Urology, New York University Medical Center, New York.
Hanna
M
M
D000328:Adult; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000209:etiology* / Q000473:pathology; D009378:Neoplasms, Multiple Primary / Q000209:etiology* / Q000473:pathology; D014402:Tuberous Sclerosis / Q000150:complications*