Vulvar leiomyomatosis in a patient with esophagogastric leiomyomatosis: review of the syndrome.
A case of vulvar leiomyomatosis in a young adult with a history of esophagogastrectomy as a child for esophagogastric leiomyomatosis is presented. The steroid receptor profile of the tumor is described. Therapy with a combination of gonadotropin suppression and surgery was undertaken. The literature pertaining to this rare combination is discussed.
Faber
K
K
Department of Obstetrics and Gynecology, Maine Medical Center, Portland, Maine 04102.
Jones
M A
MA
Spratt
D
D
Tarraza
H M
HM
D000328:Adult; D004938:Esophageal Neoplasms / Q000473:pathology*; D005260:Female; D006801:Humans; D007889:Leiomyoma / Q000473:pathology*; D013274:Stomach Neoplasms / Q000473:pathology*; D013577:Syndrome; D014846:Vulvar Neoplasms / Q000473:pathology*