Sensorineural hearing loss and the Marinesco-Sjögren syndrome.
Sensorineural hearing loss has not been previously reported in patients with the Marinesco-Sjögren Syndrome. Two siblings are described where hearing was initially normal but subsequently deteriorated.
Newton
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Centre for Audiology, School of Education, University, Manchester.
D001299:Audiometry; D002648:Child; D003638:Deafness / Q000209:etiology* / Q000235:genetics; D005260:Female; D006801:Humans; D008297:Male; D013132:Spinocerebellar Degenerations / Q000150:complications* / Q000235:genetics