[Chronic intestinal pseudo-obstruction syndrome in infants and associated anomalies].
The authors report 2 cases of functional intestinal pseudo-obstruction in infancy associated with intestinal and urologic anomalies. In the first case many intestinal obstructions occurred from the age of 3 weeks and the boy was operated on at 14 months of age. A short small bowel and an intestinal malrotation were found at surgery; the alimentary canal was completely aperistaltic, and an ileostomy was performed. Further operations were carried out, for obstruction due to adhesions, and lastly to perform another ileostomy. An antenatal diagnosis of megacystis had been made with ultrasonography. In the second case, the pseudo-obstruction syndrome occurred at the age of 1 month, due to a volvulus of the small bowel with malrotation. A second operation, one month later because of lack of intestinal transit showed an aperistaltic bowel and a colostomy was performed. The intestinal continuity was set up again at the age of 9 months and a fractional feeding was started. A megacystis was found during urologic investigations. Growth is correct for both children at 3 years of age. A review of the literature allowed to list the most frequent digestive or extradigestive anomalies associated with this syndrome.
Destuynder
R
R
Services de Pédiatrie, CHU Saint-Jacques, Besançon.
Menget
A
A
Destuynder
O
O
Lassauge
F
F
Amsallem
D
D
Aubert
D
D
Noir
A
A
D000015:Abnormalities, Multiple; D005260:Female; D006801:Humans; D007223:Infant; D007418:Intestinal Pseudo-Obstruction / Q000151:congenital*; D008297:Male; D008643:Mesentery / Q000002:abnormalities*; D013577:Syndrome; D001743:Urinary Bladder / Q000002:abnormalities*
Le syndrome de pseudo-obstruction intestinale chronique du nourrisson et les anomalies associées.