title: [Sarcoidosis simulating a pulmonary veno-occlusive disease].
abstract: We report the case of a man of 43 years old presenting with sarcoidosis which produced pulmonary hypertension and respiratory failure without radiological evidence of interstitial fibrosis. In spite of treatment with steroids and corticosteroids (1 mg/kg) there was progression over 2 1/2 years to respiratory failure and irreversible right heart failure and the death of the patient. At autopsy the pulmonary veins were obliterated by non caseating granulomas and there were minimal fibrotic parenchymal lesions. To our knowledge this is only the second case of sarcoidosis resulting in a veno occlusive pulmonary disorder.
authors.affiliation: Service de Pneumologie, Hôpital de Bois-Guillaume.
authors.forename: F
authors.initials: F
authors.lastname: Portier
authors.forename: G
authors.initials: G
authors.lastname: Lerebours-Pigeonniere
authors.forename: L
authors.initials: L
authors.lastname: Thiberville
authors.forename: S
authors.initials: S
authors.lastname: Dominique
authors.forename: J
authors.initials: J
authors.lastname: Tayot
authors.forename: J F
authors.initials: JF
authors.lastname: Muir
authors.forename: G
authors.initials: G
authors.lastname: Nouvet
mesh_terms: D000328:Adult; D006801:Humans; D008168:Lung / Q000098:blood supply*; D008171:Lung Diseases / Q000473:pathology; D008297:Male; D011658:Pulmonary Fibrosis / Q000473:pathology; D012507:Sarcoidosis / Q000473:pathology; D014680:Veins / Q000473:pathology
vernacular_title: Sarcoïdose simulant une maladie veino-occlusive pulmonaire.