title: Creutzfeldt-Jakob's disease presenting with ataxia and a movement disorder.
abstract: We describe a 62-year-old patient who presented with ataxia and dystonia with mild dementia and was shown at autopsy to have Creutzfeldt-Jakob's disease. Movement disorders may be the presenting feature of Creutzfeldt-Jakob's disease, and this entity should be considered in the differential diagnosis of an otherwise obscure movement disorder even when the typical electroencephalographic pattern is absent.
authors.affiliation: Department of Neurology, Medical College of Georgia, Augusta 30912.
authors.forename: K D
authors.initials: KD
authors.lastname: Sethi
authors.forename: D C
authors.initials: DC
authors.lastname: Hess
mesh_terms: D001921:Brain / Q000473:pathology; D002524:Cerebellar Ataxia / Q000175:diagnosis / Q000209:etiology* / Q000473:pathology; D007562:Creutzfeldt-Jakob Syndrome / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D003937:Diagnosis, Differential; D004421:Dystonia / Q000175:diagnosis / Q000209:etiology* / Q000473:pathology; D005911:Gliosis / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D009460:Neurologic Examination; D009474:Neurons / Q000473:pathology; D009483:Neuropsychological Tests