A case of the Budd Chiari syndrome attributed to a deficit in protein C.
We report a case of Budd Chiari syndrome associated with a deficit in protein C, in a young women admitted to hospital for investigation of thromboembolic disease and ascites. This coagulation defect was thought to be an aetiological factor in the suprahepatic vein thrombosis. The diagnosis and treatment of this rare form of the syndrome are discussed.
Couffinhal
T
T
Hôpital Cardiologique, Pessac, France.
Bonnet
J
J
Benchimol
D
D
Dos Santos
P
P
Besse
P
P
Bricaud
H
H
D006502:Budd-Chiari Syndrome / Q000000981:diagnostic imaging / Q000209:etiology* / Q000235:genetics; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D020151:Protein C Deficiency; D011655:Pulmonary Embolism / Q000000981:diagnostic imaging / Q000209:etiology / Q000235:genetics; D013924:Thrombophlebitis / Q000000981:diagnostic imaging / Q000209:etiology / Q000235:genetics; D014057:Tomography, X-Ray Computed