Michel's anomaly, type I microtia and microdontia.
Michel's anomaly is an extremely rare cause of congenital sensorineural hearing loss. We present a 2-1/2 year old white female with this inner ear defect associated with type I microtia and microdontia. Assessment of anatomic structures of the ear is critical in an infant with abnormal auditory brainstem responses to determine whether a structural lesion is present and the most appropriate rehabilitative approach available.
Hersh
J H
JH
Department of Pediatrics, Child Evaluation Center, Louisville, Kentucky.
Ganzel
T M
TM
Fellows
R A
RA
D000015:Abnormalities, Multiple; D004431:Ear, External / Q000002:abnormalities*; D007758:Ear, Inner / Q000002:abnormalities*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008844:Micrognathism; D014071:Tooth Abnormalities