Juvenile pemphigus vulgaris.
Pemphigus vulgaris is extremely rare in childhood. Only 35 cases of juvenile pemphigus vulgaris have been reported in the literature up until to now. During the pre-steroid era, the outcome of the disease was usually regarded as fatal. Today, the prognosis has improved because of the possibility of early diagnosis by immunofluorescent techniques, determination of antibodies against epidermal intercellular substance and early therapy with systemic steroids. A case of juvenile pemphigus vulgaris with a favourable outcome in a 13-year old girl is described.
Graff-Lonnevig
V
V
Sachs' Children's Hospital, Stockholm, Sweden.
Kaaman
T
T
D000293:Adolescent; D005260:Female; D006801:Humans; D010392:Pemphigus / Q000175:diagnosis* / Q000188:drug therapy / Q000473:pathology; D011241:Prednisone / Q000627:therapeutic use; D011379:Prognosis
D011241:Prednisone