Incontinentia pigmenti (Bloch-Sulzberger syndrome). A case report.
Incontinentia pigmenti is a rare genodermatosis with multiple manifestations affecting the skeletal, ocular, dental, and other tissues. More than 95% of reported cases occur in females, and more than 60% of reported cases involve some dental abnormality. A brief review of the literature and a case in a 7-year-old girl with the disease are presented.
Vogt
J
J
Dental Department, Portsmouth Naval Hospital, Va.
Matheson
J
J
D000848:Anodontia / Q000473:pathology; D002648:Child; D003731:Dental Caries / Q000473:pathology; D005260:Female; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D007184:Incontinentia Pigmenti / Q000473:pathology; D008963:Molar / Q000473:pathology; D014094:Tooth, Deciduous / Q000002:abnormalities