Long-term follow-up of a child with idiopathic restrictive cardiomyopathy.
A ten-year-old male with palpebral edema was proved to have a restrictive hemodynamic pattern by cardiac catheterization. Sequential echocardiographic examination revealed uniformly depressed left ventricular diastolic properties, well-maintained left ventricular systolic function, and a progression of obliterative change of the left ventricular cavity. Myocardial biopsy at 17 years of age disclosed a normal endocardium and marked interstitial fibrosis of the myocardium. Consequently, a decrease of cardiac output and a marked biatrial enlargement have developed in association with persistent atrial fibrillation.
Miyazaki
A
A
Department of Pediatrics, Toyama Medical and Pharmaceutical University, Japan.
Ichida
F
F
Suzuki
Y
Y
Okada
T
T
D000293:Adolescent; D001281:Atrial Fibrillation / Q000150:complications / Q000473:pathology; D001706:Biopsy; D002313:Cardiomyopathy, Restrictive / Q000150:complications / Q000473:pathology* / Q000503:physiopathology; D002648:Child; D004452:Echocardiography; D004719:Endomyocardial Fibrosis / Q000150:complications / Q000473:pathology; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D013997:Time Factors