Nephronophthisis with bronchiectasis.
A boy with nephronophthisis and bronchiectasis, a previously unrecognised association is described. Electron-microscopic examination of a renal biopsy from an asymptomatic sibling revealed marked thickening and lamination of the tubular basement membranes.
Bagga
A
A
Department of Paediatrics, Radiology and Pathology, All India Institute of Medical Sciences, New Delhi.
Vasudev
A
A
Kabra
S K
SK
Mukhopadhyay
S
S
Bhuyan
U N
UN
Srivastava
R
R
D001706:Biopsy; D001987:Bronchiectasis / Q000150:complications*; D002648:Child; D006801:Humans; D007672:Kidney Cortex / Q000473:pathology; D007679:Kidney Medulla / Q000473:pathology; D008297:Male; D007690:Polycystic Kidney Diseases / Q000150:complications* / Q000473:pathology