Plexiform neurofibromatosis: a difficult surgical problem.
A severe case of plexiform neurofibromatosis with elephantiasis neuromatosa involving the right lower limb and pelvis, leading to a right hip disarticulation, is reported. Abnormal vasculature can make surgical intervention hazardous.
Kuo
L A
LA
Department of Traumatic and Orthopaedic Surgery, Prince of Wales Hospital, Sydney.
Kuo
R S
RS
D000328:Adult; D001803:Blood Transfusion; D004188:Disarticulation / Q000379:methods; D004604:Elephantiasis / Q000150:complications*; D005260:Female; D006488:Hemostasis, Surgical; D006621:Hip Joint / Q000098:blood supply / Q000601:surgery; D006801:Humans; D007871:Leg Ulcer / Q000209:etiology / Q000601:surgery; D008209:Lymphedema / Q000150:complications*; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000000981:diagnostic imaging / Q000235:genetics; D010375:Pedigree; D011859:Radiography