Turcot's syndrome with intestinal lymphoma in a child: an unusual case of triple tumor.
Turcot's syndrome, the association of brain tumor (usually glioblastoma, medullo-blastoma, or astrocytoma) and colonic polyps, is a very rare condition of which about 20 cases have been reported. It has been described only once previously with cancer in a third organ system. In this paper, we report a child affected with colonic polyposis and astrocytoma (i.e., Turcot's syndrome) associated with intestinal non-Hodgkin's lymphoma.
Aricó
M
M
Department of Pediatrics, University of Pavia, IRCCS Policlinico S. Matteo, Italy.
Parigi
G B
GB
Locatelli
D
D
Bragheri
R
R
Lombardi
F
F
Zangrandi
A
A
D011125:Adenomatous Polyposis Coli; D001254:Astrocytoma; D001932:Brain Neoplasms; D002675:Child, Preschool; D006801:Humans; D007414:Intestinal Neoplasms; D008228:Lymphoma, Non-Hodgkin; D008297:Male; D009378:Neoplasms, Multiple Primary; D013577:Syndrome