title: [Classification of circumscribed scleroderma. A multicenter study of 286 patients. The Scleroderma Study Group of the Society of Dermatologic Research].
abstract: In a multicentre study performed by the German Working Group for Dermatological Research a total of 286 female and male patients with circumscribed scleroderma (morphoea) were examined with reference to form and extent of their skin manifestations (e.g. progressive idiopathic atrophodermia, Pasini-Pierini Type) and systemic involvement. On the basis of the literature and our observation of circumscribed scleroderma classification into three types appears to be appropriate: a plaque-type (with generalized circumscribed scleroderma as the most severe variant), a linear type (with pansclerotic disabling morphoea as the most severe variant) and a profound type (with eosinophilic fasciitis as the most severe variant).
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D000974:Antibodies, Antinuclear / Q000032:analysis; D002648:Child; D002675:Child, Preschool; D004247:DNA / Q000276:immunology; D005860:Germany, West; D006801:Humans; D007223:Infant; D008875:Middle Aged; D015337:Multicenter Studies as Topic; D012594:Scleroderma, Localized / Q000145:classification* / Q000175:diagnosis; D012595:Scleroderma, Systemic / Q000175:diagnosis; D012867:Skin / Q000473:pathology
chemical_list: D000974:Antibodies, Antinuclear; D004247:DNA
vernacular_title: Zur Klassifikation der zirkumskripten Sklerodermie (CS). Multizentrische Untersuchung an 286 Patienten. Arbeitsgruppe Sklerodermie der Arbeitsgemeinschaft Dermatologische Forschung (ADF).