title: Familial occurrence of congenital bile duct dilatation.
abstract: The occurrence of congenital bile duct dilatation (CBD) in both a mother and her daughter was recently experienced at Niigata University Hospital and Niigata Shimin Hospital. Bile duct dilatation with anomalous pancreaticobiliary ductal junction (AP-BDJ) was disclosed in both. Intrahepatic bile duct dilatation was only in the mother. Removal of dilated bile duct, cholecystectomy, and hepaticojejunostomy were performed in both. Fourteen cases of CBD from seven families were collected from literature and discussed.
authors.affiliation: Department of Pediatric Surgery, Niigata University Hospital, Japan.
authors.forename: M
authors.initials: M
authors.lastname: Iwafuchi
authors.forename: Y
authors.initials: Y
authors.lastname: Ohsawa
authors.forename: S
authors.initials: S
authors.lastname: Naito
authors.forename: M
authors.initials: M
authors.lastname: Naito
authors.forename: Y
authors.initials: Y
authors.lastname: Maruta
authors.forename: H
authors.initials: H
authors.lastname: Saito
mesh_terms: D000328:Adult; D002675:Child, Preschool; D002767:Cholecystostomy; D003137:Common Bile Duct Diseases / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D003560:Cysts / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D005190:Family; D005192:Family Health; D005260:Female; D006801:Humans; D007564:Japan; D010375:Pedigree