[Carney's syndrome disclosed by hemoperitoneum].
The authors report a case of Carney's triad in a blood-group O woman who successively sustained a) at age 13, a multicentric gastric leiomyoblastoma revealed by an hemoperitoneum; b) 6 years later, a pulmonary chondroma diagnosed by chest standard roentgenogram and CT scan, associated with leiomyoblastoma recurrence and hepatic metastases; c) 10 years later, a juxta-carotid tumor of unknown (paraganglion?) origin. This patient is presently in good clinical condition, in spite of hepatic metastases known for 5 years. Based on this case and the 33 previously reported cases, the main features of this very unusual entity are analyzed.
Tossou
H
H
Service d'Hépato-Gastroentérologie, CHU Nord, Amiens.
Delamarre
J
J
Sevestre
H
H
Deschepper
B
B
Jouet-Gondry
C
C
Capron
J P
JP
D000293:Adolescent; D002812:Chondroma / Q000150:complications*; D005260:Female; D005500:Follow-Up Studies; D006258:Head and Neck Neoplasms / Q000150:complications; D006465:Hemoperitoneum / Q000209:etiology*; D006801:Humans; D007889:Leiomyoma / Q000150:complications* / Q000556:secondary; D008113:Liver Neoplasms / Q000556:secondary; D008175:Lung Neoplasms / Q000150:complications*; D009378:Neoplasms, Multiple Primary / Q000150:complications; D010236:Paraganglioma, Extra-Adrenal / Q000150:complications; D013274:Stomach Neoplasms / Q000150:complications*; D013577:Syndrome
Syndrome de Carney révélé par un hémopéritoine.