Maffucci's syndrome with frontal lobe astrocytoma.
Maffucci's syndrome is a particularly rare clinical form of mesodermal dysplasia. It consists of angiomatosis, chondromatosis and sometimes dyschromic cutaneous lesions. The syndrome is usually associated with a high incidence of malignancy, originating primarily from mesodermal derivatives. The present case is the second in the literature in which the syndrome is associated with a frontal lobe astrocytoma. This patient and those reported in the literature, suggest the potential involvement of non-mesodermal tumors in the Maffucci's syndrome.
Department of Orthopaedics and Rehabilitation Medicine, Faculty of Medicine, Khon Kaen University, Thailand.
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K
Jirarattanaphochai
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Jitpimolmard
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K
Jirarattanaphochai
D000328:Adult; D001254:Astrocytoma / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D001932:Brain Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D004687:Enchondromatosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D005260:Female; D006801:Humans; D014057:Tomography, X-Ray Computed