[The Sneddon syndrome--diagnostic, etiological and therapeutic aspects].
Sneddon's syndrome represents a neurocutaneous disorder that, as a nosological entity, has first been described in 1965. This syndrome is characterized by the association between generalized racemose livedo and disorders of the central nervous system, predominantly being present as cerebrovascular lesions and seizures. So far, Sneddon's syndrome has received little attention, though a considerable part of patients with cerebrovascular events are suffering from this disease. The usual onset of clinical manifestations is in the third to fourth decade. Vascular risk factors are commonly found. For introduction of Sneddon's syndrome to a wider audience a case is reported, the clinical features, aspects of diagnosis and differential diagnosis, pathogenesis, prognosis, and treatment are discussed.
Aldenhövel
H B
HB
Klinik für Epilepsie und Neurorehabilitation, Bethesda, Tschugg.
D000328:Adult; D002561:Cerebrovascular Disorders / Q000150:complications* / Q000175:diagnosis; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D006334:Heart Function Tests; D006801:Humans; D008297:Male; D009460:Neurologic Examination; D012871:Skin Diseases / Q000150:complications* / Q000175:diagnosis; D013577:Syndrome
Das Sneddon-Syndrom--diagnostische, ätiologische und therapeutische Gesichtspunkte.