Primary Budd-Chiari syndrome: its significance for the choice of surgical management of a patent right inferior hepatic vein.
Budd-Chiari syndrome is still a major problem and the overall prognosis for the patients is dismal and disappointing. The case history of a patient with not only outflow obstruction of the hepatic vein but also complete obstruction of the retrohepatic inferior vena cava is presented. She had a patent right inferior hepatic vein which partially decompressed the liver via a rich network of venous collaterals. Management included an inferior vena cava to inferior vena cava shunt using a Goretex graft. The patient fared well and the postoperative course was satisfactory. The case history of this patient illustrates the importance of precise pre-operative investigations for the choice of the type of surgical management. Each patient has to be considered individually on the basis of his or her mechanical peculiarities.
Lygidakis
N J
NJ
Department of Surgery, P.D. Hinduja National Hospital, Bombay, India.
Bhalerao
R A
RA
Udwadia
T E
TE
D000328:Adult; D001807:Blood Vessel Prosthesis; D006502:Budd-Chiari Syndrome / Q000601:surgery*; D003097:Collateral Circulation / Q000502:physiology; D005260:Female; D006503:Hepatic Veins / Q000601:surgery*; D006801:Humans; D011138:Polytetrafluoroethylene; D014682:Vena Cava, Inferior / Q000601:surgery
D011138:Polytetrafluoroethylene