[Epilepsy and bilateral occipital calcifications: 3 cases].
We report 3 cases of epilepsy with bilateral occipital calcifications followed up for several years. These cases were compared with 21 published cases and were found to differ from the classical Sturge-Weber syndrome on several points: 1) the disease appeared around the age of 5 years and consisted of focal epilepsy without neurological or mental disorders; 2) the epilepsy was easy to control during 2 to 5 years. This was followed by a diffuse encephalopathy with severe, treatment-resistant epilepsy, Gerstmann's syndrome, optic ataxia, cerebellar syndrome and slow activity at EEG. It appears from these 3 cases that: 1) occipital calcifications may be unilateral at the onset of the disease; 2) visual evoked potentials are affected at a late stage, and 3) CT scans are of considerable value in the prognosis of benign epilepsy in childhood.
Service de Neurologie, Hôpital Général, Dijon.
M
M
Giroud
J P
JP
Borsotti
R
R
Michiels
M
M
Tommasi
R
R
Dumas
D001927:Brain Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology; D002114:Calcinosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology; D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D004827:Epilepsy / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology; D005260:Female; D006801:Humans; D008297:Male; D009778:Occipital Lobe; D013341:Sturge-Weber Syndrome / Q000175:diagnosis; D013997:Time Factors; D014057:Tomography, X-Ray Computed
Epilepsie et calcifications occipitales bilatérales: 3 cas.