Florid pulmonary veno-occlusive disease.
A young woman presented with rapidly progressive dyspnea and clinical findings strongly suggestive of primary pulmonary hypertension or possible pulmonary embolism (or both). She died of acute right-sided heart failure. A diagnosis of pulmonary veno-occlusive disease was made at autopsy. Approximately 100 cases of this disease have been reported previously in the literature. We describe a patient with a particularly florid progression of this unusual disease. Death occurred within six weeks of the onset of symptoms.
Nawaz
S
S
Department of Pathology, University of Colorado Health Sciences Center, Denver.
Dobersen
M J
MJ
Blount
S G
SG
Firminger
H I
HI
Petty
T L
TL
D000328:Adult; D002303:Cardiac Output, Low / Q000209:etiology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D011668:Pulmonary Veno-Occlusive Disease / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D011859:Radiography