Posterior fossa epidermoid in a member of a kindred with von Hippel-Lindau disease.
The authors describe the case of a middle-aged member of a kindred with von Hippel-Lindau disease in whom a posterior fossa epidermoid developed. The epidermoid was initially thought to be a hemangioblastoma, a tumor to which those who have von Hippel-Lindau disease are predisposed. Radiologic investigations, especially magnetic resonance imaging, were useful in demonstrating the extra-axial nature of the tumor and also in characterizing it as an epidermoid.
Department of Diagnostic Radiology, Victoria General Hospital.
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S
Aggarwal
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Byrne
D001927:Brain Diseases / Q000473:pathology*; D003388:Cranial Fossa, Posterior; D003937:Diagnosis, Differential; D004814:Epidermal Cyst / Q000473:pathology*; D006394:Hemangiosarcoma / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D006623:von Hippel-Lindau Disease / Q000235:genetics* / Q000473:pathology