Primary Budd-Chiari syndrome: its significance for the choice of surgical management of a patent right inferior hepatic vein.
Budd-Chiari syndrome is still a major problem and the overall prognosis for the patients is dismal and disappointing. The case history of a patient with not only outflow obstruction of the hepatic vein but also complete obstruction of the retrohepatic inferior vena cava is presented. She had a patent right inferior hepatic vein which partially decompressed the liver via a rich network of venous collaterals. Management included an inferior vena cava to inferior vena cava shunt using a Goretex graft. The patient fared well and the postoperative course was satisfactory. The case history of this patient illustrates the importance of precise pre-operative investigations for the choice of the type of surgical management. Each patient has to be considered individually on the basis of his or her mechanical peculiarities.
Department of Surgery, P.D. Hinduja National Hospital, Bombay, India.
N J
NJ
Lygidakis
R A
RA
Bhalerao
T E
TE
Udwadia
D000328:Adult; D001807:Blood Vessel Prosthesis; D006502:Budd-Chiari Syndrome / Q000601:surgery*; D003097:Collateral Circulation / Q000502:physiology; D005260:Female; D006503:Hepatic Veins / Q000601:surgery*; D006801:Humans; D011138:Polytetrafluoroethylene; D014682:Vena Cava, Inferior / Q000601:surgery
D011138:Polytetrafluoroethylene