Hypertrophic peripheral neuropathy (Dejerine-Sottas disease) associated with heart block. Case report presentation and review of the literature.
We present a case of a male suffering from hypertrophic peripheral neuropathy (Dejerine-Sottas disease) and severe involvement of the cardiac conductive tissue causing syncopal attacks. It is the first time that an association of this neuromuscular disease with cardiac involvement is described.
Kouvaras
G
G
Department of Cardiology, Tzanio State Hospital, Piraeus, Greece.
Chronopoulos
G
G
Pistis
G
G
Cokkinos
D
D
D000328:Adult; D004562:Electrocardiography; D006327:Heart Block / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D015417:Hereditary Sensory and Motor Neuropathy / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D010138:Pacemaker, Artificial; D013497:Sural Nerve / Q000473:pathology