Thoraco-abdominal enteric duplication with meningocele, skeletal anomalies and dextrocardia.
We describe an infant with an enteric thoraco-abdominal duplication arising in the proximal jejunum and associated with a dorsal meningocele, dextrocardia, agenesis of ribs and hypoplasia of the left arm. Diagnosis was reached post-operatively and the infant died of cytomegalovirus pneumonitis. Results of the postmortem examination are presented. Awareness of this rare malformation is required in order to reach a timely diagnosis and to plan a suitable operative approach.
Wolf
Y G
YG
Department of Paediatric Surgery, Hadassah University Hospital, Jerusalem, Israel.
Merlob
P
P
Horev
G
G
Litwin
A
A
Katz
S
S
D000015:Abnormalities, Multiple; D003914:Dextrocardia / Q000150:complications*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007421:Intestine, Small / Q000002:abnormalities*; D008588:Meningocele / Q000150:complications*; D012272:Ribs / Q000002:abnormalities*