title: Congenital cystic adenomatoid malformation of the lung.
abstract: Twenty cases of cystic adenomatoid malformation of the lung were observed: 2 had died in utero; the diagnosis was made at birth in 13 infants of which 3 were premature. A Bochdalek's hernia had been diagnosed before birth in 2 cases by echo-tomography. The correct antenatal diagnosis had been made in 2 cases. Two infants had no symptoms, 3 were dyspneic, 8 were in respiratory distress and had to be intubated and ventilated. Two had a prune belly syndrome. Eight infants had a thoracotomy during their first week of life. Pulmonary resections concerning those 13 patients comprised 10 lower lobectomies, 1 of which was associated with a lingulectomy, and 2 upper lobectomies, 1 of which was associated with a middle lobe resection. Five patients were diagnosed and operated upon between 10 months and 8 years of age; 4 had recurrent bronchitis and 1 was diagnosed during the treatment of a gastroenteritis. They had 3 lower and 2 upper lobectomies. Recovery was uneventful in all patients except for 1 who was reoperated upon for intestinal obstruction. Antenatal diagnosis of cystic adenomatoid malformation should become standard. The malformation may be mistaken for a pulmonary sequestration or bronchogenic cyst. Differential diagnosis of a congenital hernia is important.
authors.affiliation: Clinique Chirurgicale Quest, CHU, Lille, France.
authors.forename: M
authors.initials: M
authors.lastname: Ribet
authors.forename: F R
authors.initials: FR
authors.lastname: Pruvot
authors.forename: J P
authors.initials: JP
authors.lastname: Dubos
authors.forename: J
authors.initials: J
authors.lastname: Remy
authors.forename: M C
authors.initials: MC
authors.lastname: Sault
authors.forename: B
authors.initials: B
authors.lastname: Gosselin
authors.forename: J L
authors.initials: JL
authors.lastname: Linder
mesh_terms: D002648:Child; D002675:Child, Preschool; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000175:diagnosis* / Q000601:surgery; D005260:Female; D005315:Fetal Diseases / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011296:Prenatal Diagnosis; D014463:Ultrasonography