A forme fruste of Marfan's syndrome: case history.
A thirty nine year old woman presented with multiple aneurysms and dissections of the arterial system secondary to cystic medial necrosis is presented. After assessment of the family history a diagnosis of a forme fruste of Marfan's syndrome was made. Preoperative consideration of this rare diagnosis is important for treatment and surgical management.
Lamers
R J
RJ
Department of Radiology, University Hospital Maastricht, State University of Limburg, The Netherlands.
Janevski
B K
BK
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000328:Adult; D000784:Aortic Dissection / Q000000981:diagnostic imaging*; D005192:Family Health; D005260:Female; D006801:Humans; D008382:Marfan Syndrome / Q000000981:diagnostic imaging*; D011859:Radiography