The hyperimmunoglobulinaemia E and recurrent infections syndrome in an adult.
A 27 year old white woman with a history of chronic eczema and episodes of serious infection of the chest, skin, and bone presented with acute respiratory failure. She was found to have a spontaneous right pneumothorax and a pneumatocele in the left upper lobe. Despite a left upper lobectomy she was left with chronic respiratory failure, bullous lung disease, and bilateral bronchiectasis. The hyperimmunoglobulinaemia E and recurrent infections syndrome was diagnosed only in adult life.
L'Huillier
J P
JP
Service de Pneumologie, Centre Hospitalier Régional et Universitaire, Rennes, France.
Thoreux
P H
PH
Delaval
P
P
Desrues
B
B
Le Gall
E
E
Kernec
J
J
Delambre
J F
JF
D000328:Adult; D001424:Bacterial Infections / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D006942:Hypergammaglobulinemia / Q000150:complications* / Q000000981:diagnostic imaging; D007073:Immunoglobulin E; D007589:Job Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D008168:Lung / Q000000981:diagnostic imaging; D008171:Lung Diseases / Q000000981:diagnostic imaging; D011859:Radiography; D012008:Recurrence
D007073:Immunoglobulin E