[Unusual cause of ascites: the POEMS syndrome].
A 39-year-old woman presented with polyneuropathy, hepatomegaly, splenomegaly, endocrinopathy, monoclonal protein and skin changes, several of the many clinical features of the recently described POEMS syndrome. In addition, she had a Castleman's disease (angiofollicular lymph node hyperplasia). In this case ascites was a main presenting feature. Thus, the POEMS syndrome must be added to the list of rare causes of ascites. Electron microscopy of the liver showed perisinusoidal fibrosis.
Berson
A
A
Service des Maladies du Foie et de l'Appareil Digestif, Hôpital Bicêtre, Le Kremlin Bicêtre.
Fabre
M
M
Buffet
C
C
Rougier
P
P
Guillaume
J C
JC
Venencie
P Y
PY
Schaison
G
G
Pateron
D
D
Charpentier
P
P
Etienne
J P
JP
D000328:Adult; D001201:Ascites / Q000150:complications*; D005871:Castleman Disease / Q000150:complications*; D004700:Endocrine System Diseases / Q000150:complications; D005260:Female; D006529:Hepatomegaly / Q000150:complications; D006801:Humans; D009422:Nervous System Diseases / Q000150:complications; D012871:Skin Diseases / Q000150:complications; D013163:Splenomegaly / Q000150:complications; D013577:Syndrome
Une cause rare d'ascite : le syndrome POEMS.