title: Maffucci's syndrome with bilateral cartilaginous tumors of the cerebellopontine angle.
abstract: Maffucci's syndrome is characterized by the combination of multiple enchondromas (Ollier's disease) and hemangiomatosis. These hemangiomas develop in the subcutaneous tissue and form red-blue tumors dispersed over the whole body. Intracranial involvement is rare, making a preoperative radiological diagnosis and differentiation from other tumors rather difficult. The radiological characteristics and successful removal of the intracranial part of a chondrosarcoma of the cerebellopontine angle in a case of Maffucci's syndrome are reported in this paper.
authors.affiliation: Department of Neurosurgery, University of Würzburg, Federal Republic of Germany.
authors.forename: K A
authors.initials: KA
authors.lastname: Bushe
authors.forename: M
authors.initials: M
authors.lastname: Naumann
authors.forename: M
authors.initials: M
authors.lastname: Warmuth-Metz
authors.forename: J
authors.initials: J
authors.lastname: Meixensberger
authors.forename: J
authors.initials: J
authors.lastname: Müller
mesh_terms: D000328:Adult; D002530:Cerebellopontine Angle; D002813:Chondrosarcoma / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D004687:Enchondromatosis / Q000150:complications* / Q000473:pathology; D006225:Hand / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D011859:Radiography; D012886:Skull / Q000473:pathology; D012888:Skull Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery