Pulmonary bullous disease in Marfan syndrome.
Two young adults with marfanoid features who had pulmonary bullous disease are presented. One a young soldier, presented with increasing dyspnoea and an enlarging large pulmonary bulla on the right side. The bulla was under tension and was operated on. The other case was a young housewife who also presented with dyspnoea, and was found to have a cardiac murmur and multiple ectopic beats on initial examination. X-Ray chest revealed bilateral pulmonary bullous emphysema. Both the subjects had many features which are accepted as forme fruste of the Marfan syndrome.
Tewari
S C
SC
Jayaswal
R
R
Jetley
R K
RK
Rao
P B
PB
D000328:Adult; D001768:Blister; D004646:Emphysema / Q000150:complications*; D005260:Female; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*