The cranio-facio-cervical scoliosis complex.
Six patients are presented with facial asymmetry including vertical orbital dystopia in association with torticollis. All six have also had other abnormalities. Some degree of hemifacial microsomia was present in five of the six, a so-called plagiocephalic or rhomboid skull with normal cranial sutures in four of the six, and cervical spine anomalies in four of the six. Other deformities have also been noted. The condition is best named the cranio-facio-cervical scoliosis complex. The implications for treatment of the facial asymmetry, in particular the unequal levels of the orbits in the established deformity, are discussed and a surgical plan which has been used in four patients described.
Poole
M D
MD
Oxford Craniofacial Unit, Radcliffe Infirmary.
Briggs
M
M
D000015:Abnormalities, Multiple / Q000601:surgery*; D005146:Facial Asymmetry / Q000151:congenital* / Q000601:surgery; D005260:Female; D006801:Humans; D008297:Male; D009915:Orbit / Q000002:abnormalities* / Q000601:surgery; D012600:Scoliosis / Q000151:congenital* / Q000601:surgery; D012886:Skull / Q000002:abnormalities; D013518:Surgery, Plastic / Q000379:methods; D014103:Torticollis / Q000151:congenital / Q000601:surgery