title: [Familial bullous disease of the lungs as a cause of spontaneous pneumothorax].
abstract: Problems of surgical treatment of familial spontaneous pneumothorax, which is a manifestation of a hereditary form of bullous disease of the lungs, are discussed. Study of 2 families showed that the disease is inherited according to the autosome-dominant type with incomplete penetrance and/or variation expressivity. Operation was performed on 5 of 9 patients. Bullectomy and pleurodesis by means of parietal pleurectomy were conducted. Follow-up for periods of 1 to 27 years showed surgical treatment to be effective.
authors: A A
authors: AA
authors: Vishnevskiĭ
authors: G D
authors: GD
authors: Nikoladze
authors: Iu V
authors: IuV
authors: Romanov
mesh_terms: D005260:Female; D006801:Humans; D008297:Male; D010375:Pedigree; D011030:Pneumothorax / Q000209:etiology / Q000235:genetics* / Q000601:surgery; D011656:Pulmonary Emphysema / Q000150:complications / Q000235:genetics* / Q000601:surgery
vernacular_title: Semeĭnaia bulleznaia bolezn' legkikh, kak prichina spontannogo pnevmotoraksa.