[Peutz-Jeghers syndrome. Description of a case and literature review].
The authors describe the case of a 7 year old boy who presented an intestinal intussusception due to a large jejunal hamartomatous jejunal polyp. The preoperative diagnosis of Peutz-Jeghers syndrome was based on typical mucocutaneous pigmentation and confirmed by radiological examination including computerized tomography of the abdomen. Following recent data from the literature, a long-term surveillance is justified after diagnosis of this syndrome, since malignant degeneration may occur within the intestinal polyps as well as in other organs.
Mendes da Costa
P
P
Service de Chirurgie, Hôpital Français-U.L.B., Bruxelles.
Reygaerts
D
D
Desorgher
G
G
Vandendael
P
P
Rutsaert
J
J
De Temmerman
P
P
D002648:Child; D003952:Diagnostic Imaging; D006801:Humans; D007443:Intussusception / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D007579:Jejunal Diseases / Q000209:etiology* / Q000601:surgery; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000150:complications* / Q000175:diagnosis
Syndrome de Peutz-Jeghers. Description d'un cas et revue de la littérature.