[Pulmonary involvement in a case of CREST syndrome].
The paper describes the clinical, X-ray and functional aspects of lung involvement in a case of CREST syndrome, a variant of systemic sclerosis. The characteristic signs of the disease were associated in this patient with lung involvement in the form of widespread interstitial fibrosis complicated by the presence of alveolar cysts in the lower lobes. The state of severe chronic respiratory insufficiency was the most unfavourable factor in the prognosis for this patient, in particular in the light of the disappointing response to corticosteroid therapy.
Vignale
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Divisione di Pneumologia, USL 1 Lunigiana, Ospedale di Fivizzano.
Rossi
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PC
Parentini
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GC
D002114:Calcinosis; D004417:Dyspnea / Q000000981:diagnostic imaging / Q000209:etiology*; D015154:Esophageal Motility Disorders; D006801:Humans; D008297:Male; D008875:Middle Aged; D011859:Radiography; D011928:Raynaud Disease; D012595:Scleroderma, Systemic / Q000150:complications / Q000000981:diagnostic imaging; D013577:Syndrome; D013684:Telangiectasis
Interessamento polmonare in un caso di sindrome CREST.