Early home management of patients with Pierre Robin sequence.
Robin Sequence is a well-described disorder with a reported incidence of 1 in 2000 births. It is characterized by glossoptosis and micrognathia often associated with a cleft palate. Respiratory obstruction at the level of the tongue occurs in many affected children. Prior to routine intensive care unit management, it was the primary factor in the mortality reported in patients with moderately severe to severe deformity. Treatment of this obstruction is controversial and may include a long stay in an intensive care setting. We report two cases that demonstrate properly placed and constructed nasopharyngeal tubes allow a non-surgical treatment with early discharge of the patient and without the risks and morbidity of surgery or the complications of tracheostomy.
Olson
T S
TS
Department of Otolaryngology, Children's Hospital, San Diego, CA.
Kearns
D B
DB
Pransky
S M
SM
Seid
A B
AB
D000402:Airway Obstruction / Q000628:therapy*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007442:Intubation, Intratracheal / Q000295:instrumentation / Q000379:methods*; D008297:Male; D009305:Nasopharynx; D010855:Pierre Robin Syndrome / Q000628:therapy*; D013997:Time Factors