[Fluctuating muscular dystonia. Segawa's syndrome. Value of the treatment with L-dopa].
The case of an 8 year-old boy presenting with walking difficulties due to dystonia, peculiar because it was more pronounced during daytime is reported. Improvement with treatment with L-Dopa was dramatic. This diurnal fluctuation and excellent response to L-Dopa suggest the diagnosis of Segawa syndrome. The precise mechanism of the dystonia remains unknown.
Puel
O
O
Service de Pédiatrie, Hôpital des Efants, Bordeaux.
Fontan
D
D
Hehunstre
J P
JP
Guillard
J M
JM
D002648:Child; D004421:Dystonia / Q000188:drug therapy*; D006801:Humans; D007980:Levodopa / Q000627:therapeutic use*; D008297:Male
D007980:Levodopa
Dystonie musculaire fluctuante. Syndrome de Segawa. Intérêt du traitement par la L-dopa.