[Familial bullous disease of the lungs as a cause of spontaneous pneumothorax].
Problems of surgical treatment of familial spontaneous pneumothorax, which is a manifestation of a hereditary form of bullous disease of the lungs, are discussed. Study of 2 families showed that the disease is inherited according to the autosome-dominant type with incomplete penetrance and/or variation expressivity. Operation was performed on 5 of 9 patients. Bullectomy and pleurodesis by means of parietal pleurectomy were conducted. Follow-up for periods of 1 to 27 years showed surgical treatment to be effective.
Vishnevskiĭ
A A
AA
Nikoladze
G D
GD
Romanov
Iu V
IuV
D005260:Female; D006801:Humans; D008297:Male; D010375:Pedigree; D011030:Pneumothorax / Q000209:etiology / Q000235:genetics* / Q000601:surgery; D011656:Pulmonary Emphysema / Q000150:complications / Q000235:genetics* / Q000601:surgery
Semeĭnaia bulleznaia bolezn' legkikh, kak prichina spontannogo pnevmotoraksa.