title: [Esophageal stenosis in children with recessive epidermolysis bullosa dystrophica. Presentation of 6 cases].
abstract: Esophageal strictures may complice Dystrophic Recessive + Epidermolysis Bullosa (DREB). We report six consecutive cases of DREB with this type of lesion as the main gastrointestinal manifestation. In three children the stenosis was unique and located in the upper third one in the middle third, and the last two children showed a double stenosis (Upper and middle third) of the esophagus.
authors.affiliation: Servicio de Gastroenterología, INPed SS., México, D.F.
authors.forename: J A
authors.initials: JA
authors.lastname: Ramírez Mayans
authors.forename: R J
authors.initials: RJ
authors.lastname: Michel Aceves
authors.forename: P
authors.initials: P
authors.lastname: Casaubón Garcín
authors.forename: M
authors.initials: M
authors.lastname: Rivera Echegoyen
authors.forename: A
authors.initials: A
authors.lastname: Mora Tiscareño
mesh_terms: D000293:Adolescent; D002648:Child; D016108:Epidermolysis Bullosa Dystrophica / Q000145:classification / Q000150:complications*; D004940:Esophageal Stenosis / Q000209:etiology*; D005260:Female; D005808:Genes, Recessive; D006801:Humans; D008297:Male
vernacular_title: Estenosis esofágica en niños con epidermólisis bulosa distrófica recesiva. Presentación de 6 casos.