[Sturge-Weber disease].
Morphological changes in the vascular malformations of pia mater and neighbouring parts of the brain surgically removed in 9 patients with Sturge-Weber syndrome were studied light- and electron-microscopically. On the basis of the results obtained the concept of Sturge-Weber syndrome pathogenesis is formulated. According to this concept the disease develops due to the brain hypoxia resulting from the long-lasting congestion in the pia mater with angiomatosis. Respectively, the surgical treatment of the disease is founded and the necessity of such a treatment at young age is outlined. The authors' own data on the nearest (up to one year) and remote (up to 15 years) results of such treatment are presented.
Matsko
D E
DE
Shlepakov
I M
IM
D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D006801:Humans; D008854:Microscopy, Electron; D010841:Pia Mater / Q000098:blood supply / Q000473:pathology; D012867:Skin / Q000098:blood supply / Q000473:pathology; D013341:Sturge-Weber Syndrome / Q000209:etiology / Q000473:pathology* / Q000601:surgery
Bolezn' Sterdzha--Vebera.