Choledochal cyst and congenital hepatic fibrosis.
A case of choledochal cyst with congenital hepatic fibrosis is described. This association is known but insufficiently recognized, as is the association between Caroli disease and choledochal cyst. We urge that a specific search be made for these related disorders when patients present with manifestations of one of these disorders.
Evans-Jones
G
G
Department of Paediatrics, Countess of Chester Hospital, England.
Cudmore
R
R
D002675:Child, Preschool; D015529:Choledochal Cyst / Q000150:complications* / Q000175:diagnosis; D006529:Hepatomegaly / Q000175:diagnosis / Q000209:etiology; D006801:Humans; D008103:Liver Cirrhosis / Q000150:complications / Q000151:congenital* / Q000175:diagnosis; D008297:Male; D013163:Splenomegaly / Q000175:diagnosis / Q000209:etiology