Long-term survival in an infant with urethral atresia.
Complete urethral atresia is an anomaly that previously was incompatible with life. We report on a surviving infant with this anomaly. As a fetus urinary decompression was accomplished with a vesicoamniotic shunt. Peritoneal dialysis was initiated shortly after birth and at 9 months supramembranous scrotal inlay urethroplasty was performed to provide for egress of urine from the bladder. A maternal renal allograft was performed when he was 12 months old. When the patient was 3 1/2 years old he had normal renal function and emptied the bladder to completion through the reconstructed urethra. Although mildly delayed, he continues to progress with all developmental milestones.
Steinhardt
G
G
Department of Pediatrics, St. Louis University School of Medicine, Missouri.
Hogan
W
W
Wood
E
E
Weber
T
T
Lynch
R
R
D003559:Cystostomy; D005333:Fetus / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D016030:Kidney Transplantation; D008297:Male; D010530:Peritoneal Dialysis; D013997:Time Factors; D014521:Urethra / Q000002:abnormalities* / Q000601:surgery