Primary alveolar capillary dysplasia.
We describe two neonates with a lethal form of pulmonary maldevelopment. Both infants had bilateral dysplastic immature lungs with poor capillary formation and lack of alveolar development. This rare entity should be considered in the differential diagnosis of a newborn infant with mild diffuse radiographic pulmonary abnormality and severe respiratory distress.
Newman
B
B
University of Pittsburgh School of Medicine, PA.
Yunis
E
E
D002196:Capillaries / Q000002:abnormalities; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000473:pathology; D007231:Infant, Newborn; D008168:Lung / Q000002:abnormalities*; D008297:Male; D011650:Pulmonary Alveoli / Q000002:abnormalities* / Q000098:blood supply; D011654:Pulmonary Edema / Q000473:pathology; D012127:Respiratory Distress Syndrome, Newborn / Q000473:pathology*; D012131:Respiratory Insufficiency / Q000473:pathology