[Retractile mesenteritis. Diagnostic and therapeutic aspects].
An 18-year-old boy, who had severe abdominal pain for 18 months associated with marked weight loss, was found to have a stenosed ileal sling on double-contrast radiology of the small intestine. At operation a plate-like tumour was extending from the pancreas to the aortic bifurcation. Histological examination of removed tissue revealed retractile mesenteritis (mesenteric panniculitis; liposclerotic mesenteritis). The symptoms regressed and the patient again gained weight under immunotherapy with 1 mg/kg of prednisone and 2 mg/kg of cyclophosphamide daily. Subsequently, under prednisone alone, there was a recurrence, which responded within five weeks to daily 60 mg prednisone and 125 mg cyclophosphamide. The patient remains symptom-free on 125 mg cyclophosphamide and 10 mg prednisone daily.
Trautwein
C
C
Medizinische Klinik und Poliklinik, Universität Mainz.
Hermann
E
E
Rambow
A
A
Löhr
H
H
Klose
P
P
Gabbert
H
H
Poralla
T
T
D015746:Abdominal Pain / Q000209:etiology; D000293:Adolescent; D003520:Cyclophosphamide / Q000627:therapeutic use*; D003937:Diagnosis, Differential; D006801:Humans; D007421:Intestine, Small / Q000000981:diagnostic imaging; D008297:Male; D008643:Mesentery / Q000473:pathology; D015436:Panniculitis, Peritoneal / Q000175:diagnosis* / Q000188:drug therapy; D011239:Prednisolone / Q000627:therapeutic use*; D012008:Recurrence; D014057:Tomography, X-Ray Computed; D015431:Weight Loss
D003520:Cyclophosphamide; D011239:Prednisolone
Die retraktile Mesenteritis. Diagnostische und therapeutische Aspekte.