[Hereditary epidermolysis bullosa and laryngeal involvement].
Two cases of epidermolysis bullosa (EB) with laryngeal involvement are reported in 2 Algerian girls, aged 6 and 7 years. The first one with a junctional EB, received local treatment with good results. For the second, with an EB dystrophica, tracheostomy was necessary and remained so. Laryngeal involvement is rare in EB. It and remained so can be serious and life-threatening. Eight cases where previously reported. Their clinical and therapeutical particularities are discussed.
Nègre
V
V
Clinique de Pédiatrie, Hôpital Ambroise Paré, Boulogne.
Denoyelle
F
F
Chevallier
B
B
Garabedian
E N
EN
Prigent
F
F
Lagardère
B
B
D002648:Child; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000235:genetics; D005260:Female; D006801:Humans; D007818:Laryngeal Diseases / Q000209:etiology*
Epidermolyse bulleuse héréditaire et atteinte laryngée.