[A case of modified Fontan operation for complete atrioventricular canal of right dominance with double-outlet right ventricle, common atrioventricular valve regurgitation].
A 6-year-old boy was diagnosed to have complete atrioventricular canal (CAVC) with double-outlet right ventricle (DORV), common atrium and common atrioventricular valve regurgitation. The atrioventricular junction predominantly connected to the right ventricle (right dominance) and the left ventricle was hypoplastic (LVEDV = 64% of normal). The combination of DORV with right dominant CAVC makes more difficult to make intra-ventricular rerouting. A modified Fontan procedure, atrial partition and DeVega's annuloplasty were successfully performed. It is concluded that Fontan procedure might be preferable rather than intra-ventricular rerouting in this case.
Eishi
K
K
Department of Cardiovascular Surgery, Cardiovascular Center Sakakibara Hospital.
Hata
T
T
Taniguchi
G
G
Shinoka
S
S
Namba
H
H
Sone
Y
Y
Takata
S
S
Kuinose
M
M
Ueda
M
M
Mori
K
K
D002648:Child; D004310:Double Outlet Right Ventricle / Q000150:complications / Q000601:surgery*; D004694:Endocardial Cushion Defects / Q000150:complications / Q000601:surgery*; D006325:Heart Atria / Q000002:abnormalities / Q000601:surgery*; D006343:Heart Septal Defects / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D008297:Male; D008722:Methods; D011651:Pulmonary Artery / Q000601:surgery*; D011666:Pulmonary Valve Stenosis / Q000150:complications; D014262:Tricuspid Valve Insufficiency / Q000601:surgery*