[Severe pulmonary arterial hypertension caused by protein C deficiency reversible after medical treatment].
We report the case of a young man with severe pulmonary hypertension caused by multiple thromboembolism subsequent to congenital protein C deficit. During the previous phase to haematological treatment we showed a very poor response to vasodilators evaluated by Doppler-Echocardiography. The etiological diagnosis was confirmed and initialized the anticoagulant treatment. We had observed a significant regression of peak gradient atrioventricular by continuous wave Doppler and a complete clinical normalization.
Martínez Ferrer
J
J
Unidad Funcional de Cardiología, Hospital de Txagorritxu, Vitoria-Gasteiz.
Menchaca
C
C
Alonso Gómez
A
A
Camacho
I
I
Cordo
J C
JC
Martín
C
C
D000328:Adult; D000925:Anticoagulants / Q000627:therapeutic use; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology*; D008297:Male; D020151:Protein C Deficiency; D011655:Pulmonary Embolism / Q000150:complications* / Q000209:etiology
D000925:Anticoagulants
Hipertensión arterial pulmonar severa por déficit de proteína C reversible tras tratamiento médico.