Congenital unilateral absence of a pulmonary artery: a report of two adult cases.
Congenital unilateral absence of a pulmonary artery (UAPA) is a rare anomaly that is generally diagnosed in childhood and frequently associated with other cardiovascular abnormalities. Two patients with unilateral absence of a pulmonary artery first diagnosed as adults are reported. Our two cases demonstrate that presentation of UAPA may range from an incidental finding to chronic, life-threatening symptoms. Because UAPA may require urgent intervention, physicians should be alerted to the possibility of this entity presenting later in life.
Ko
T
T
Department of Medicine Truman Medical Center, Kansas City.
Gatz
M G
MG
Reisz
G R
GR
D000328:Adult; D001706:Biopsy; D005260:Female; D006801:Humans; D008168:Lung / Q000473:pathology; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D013902:Radiography, Thoracic