Proteus syndrome: course of a severe case.
We report on the course of a 4 1/2-year-old boy with Proteus syndrome who was first described 3 years ago. Details are given on the phenotypic changes, the complications of corrective surgery on tissue overgrowth, and the development of a mesothelioma of the tunica vaginalis of the testis.
Malamitsi-Puchner
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A
Department of Neonatology, General Hospital Alexandra, Athens, Greece.
Dimitriadis
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D
Bartsocas
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C
Wiedemann
H R
HR
D002675:Child, Preschool; D005532:Foot Deformities, Congenital / Q000150:complications; D005877:Gigantism / Q000150:complications*; D006130:Growth Disorders / Q000473:pathology*; D006228:Hand Deformities, Congenital / Q000150:complications; D006801:Humans; D006984:Hypertrophy / Q000150:complications*; D008297:Male; D013577:Syndrome; D013736:Testicular Neoplasms / Q000473:pathology*