[A case of Marfan syndrome with recurrent bilateral pneumothorax and anuloaortic ectasia].
A 17-year-old male patient with Marfan syndrome was admitted due to recurrent bilateral pneumothorax which had recurred totally 11 times during the past 3 years. For the treatment of obstinately continuing right pneumothorax resection of bullae in combination with pleuropexy using OK 432 was effective. Two months thereafter Bentall operation with a composite graft consisting of a woven Dacron tube and a Björk-Shiley 27 mm aortic valve prosthesis was performed for his anuloartic ectasia. Left pneumothorax recurred 2 weeks after Bentall operation. But it was treated successfully with OK 432 injection into the left pleural cavity. Now, he is doing well as a student.
Yoshimura
N
N
Division of Cardiovascular Surgery, Hyogo Brain and Heart Center at Himeji.
Asada
T
T
Matsuda
H
H
Nohara
H
H
Higami
T
T
Nishiwaki
M
M
Mukohara
N
N
Chibana
M
M
Ogawa
K
K
D000368:Aged; D001014:Aortic Aneurysm / Q000209:etiology / Q000601:surgery*; D001807:Blood Vessel Prosthesis; D006350:Heart Valve Prosthesis; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D010844:Picibanil / Q000627:therapeutic use; D011030:Pneumothorax / Q000209:etiology*
D010844:Picibanil