title: A prevalence study of Rett syndrome in an institutionalized population.
abstract: An institution for the mentally retarded was surveyed to determine the prevalence rate of Rett syndrome (RS). Four patients with definite RS and one with probable RS were identified in a population of 350, yielding a prevalence rate of 1 in 87, about 1% of institutionalized male and female patients with mental retardation. In this population of patients with severe and profound mental retardation (N = 297), 138 females were surveyed, suggesting a prevalence rate among females of 1 in 34 in an institutional population of persons with mental retardation. Surveys of institutions for persons with mental retardation may be an effective method to identify adults with RS.
authors.affiliation: Child Evaluation and Treatment Program, Medical Center Rehabilitation Hospital, Grand Forks, ND 58202.
authors.forename: L
authors.initials: L
authors.lastname: Burd
authors.forename: J T
authors.initials: JT
authors.lastname: Martsolf
authors.forename: T
authors.initials: T
authors.lastname: Randall
mesh_terms: D000293:Adolescent; D000328:Adult; D005260:Female; D006801:Humans; D007326:Institutionalization; D008607:Intellectual Disability; D008297:Male; D008875:Middle Aged; D009658:North Dakota / Q000453:epidemiology; D015518:Rett Syndrome / Q000453:epidemiology*