title: [Severe pulmonary arterial hypertension caused by protein C deficiency reversible after medical treatment].
abstract: We report the case of a young man with severe pulmonary hypertension caused by multiple thromboembolism subsequent to congenital protein C deficit. During the previous phase to haematological treatment we showed a very poor response to vasodilators evaluated by Doppler-Echocardiography. The etiological diagnosis was confirmed and initialized the anticoagulant treatment. We had observed a significant regression of peak gradient atrioventricular by continuous wave Doppler and a complete clinical normalization.
authors.affiliation: Unidad Funcional de Cardiología, Hospital de Txagorritxu, Vitoria-Gasteiz.
authors.forename: J
authors.initials: J
authors.lastname: Martínez Ferrer
authors.forename: C
authors.initials: C
authors.lastname: Menchaca
authors.forename: A
authors.initials: A
authors.lastname: Alonso Gómez
authors.forename: I
authors.initials: I
authors.lastname: Camacho
authors.forename: J C
authors.initials: JC
authors.lastname: Cordo
authors.forename: C
authors.initials: C
authors.lastname: Martín
mesh_terms: D000328:Adult; D000925:Anticoagulants / Q000627:therapeutic use; D006801:Humans; D006976:Hypertension, Pulmonary / Q000188:drug therapy / Q000209:etiology*; D008297:Male; D020151:Protein C Deficiency; D011655:Pulmonary Embolism / Q000150:complications* / Q000209:etiology
chemical_list: D000925:Anticoagulants
vernacular_title: Hipertensión arterial pulmonar severa por déficit de proteína C reversible tras tratamiento médico.