title: Nevoid basal cell carcinoma syndrome and acrokeratosis verruciformis. Occurrence of two rare inherited autosomal dominant conditions in the same patient.
abstract: An exceptional case of nevoid basal cell carcinoma (NBCC) syndrome occurring with acrokeratosis verruciformis (AKV) in the same patient is presented. The occurrence of two rare autosomal dominant diseases in a patient suggests that AKV might be one of the different dyskeratoses of the NBCC syndrome. The clinical aspect of the flesh-colored papules of AKV, indistinguishable from flat warts, might nevertheless prompt performance of a biopsy.
authors.affiliation: Service de Dermatologie, Hôpital Saint-Jacques, Besançon, France.
authors.forename: P
authors.initials: P
authors.lastname: Humbert
authors.forename: R
authors.initials: R
authors.lastname: Laurent
authors.forename: B
authors.initials: B
authors.lastname: Faivre
authors.forename: P
authors.initials: P
authors.lastname: Agache
mesh_terms: D001478:Basal Cell Nevus Syndrome / Q000150:complications / Q000235:genetics* / Q000473:pathology; D002280:Basal Cell Carcinoma / Q000235:genetics*; D003937:Diagnosis, Differential; D006229:Hand Dermatoses / Q000150:complications / Q000235:genetics* / Q000473:pathology; D006801:Humans; D007642:Keratosis / Q000150:complications / Q000235:genetics / Q000473:pathology; D008297:Male; D008875:Middle Aged