title: [Systemic mastocytosis. A case report].
abstract: The authors report a case of systemic mastocytosis in a 65 year-old woman. The clinical picture was generalized abdominal and extra abdominal lymph nodes, ascites, splenomegaly, and hepatomegaly. As gastro-intestinal symptoms led to suspect a digestive malignant lymphoma; the patient underwent an exploratory laparotomy. The diagnosis of systemic mastocytosis was established by demonstrating an excessive number of mast cells in the cutaneous and extracutaneous tissues (liver, mesenteric lymph, nodes, spleen and bone marrow). Bone marrow biopsy revealed extensive myelofibrosis.
authors.affiliation: Service d'Anatomie et Cytologie pathologiques, Hôpital H. Thameur, Tunis.
authors.forename: K
authors.initials: K
authors.lastname: Ben Romdhane
authors.forename: N
authors.initials: N
authors.lastname: Ben Romdhane
authors.forename: M R
authors.initials: MR
authors.lastname: Ben Younes
authors.forename: S
authors.initials: S
authors.lastname: Ayadi
authors.forename: M
authors.initials: M
authors.lastname: Ben Ayed
mesh_terms: D000368:Aged; D001201:Ascites / Q000209:etiology; D005260:Female; D006529:Hepatomegaly / Q000209:etiology; D006801:Humans; D008206:Lymphatic Diseases / Q000209:etiology; D008415:Mastocytosis / Q000150:complications / Q000473:pathology*; D013163:Splenomegaly / Q000209:etiology
vernacular_title: Mastocytose systémique. A propos d'un cas.