[Sclerosing cholangitis revealing histiocytosis X].
The case of a 3 year-old boy who presented isolated cholestasis as the initial symptom of histiocytosis X is described. Other symptoms occurred later on. Despite treatment (corticosteroid and Vinblastin), the disease continued to progress and the child died at the age of 4 1/2 years with HIV infection (contaminated blood product) and tuberculosis.
Neveu
I
I
Service de Pédiatrie, Hôpital Antoine-Béclère, Clamart.
Labrune
P
P
Huguet
P
P
Musset
D
D
Chaussain
J L
JL
Odièvre
M
M
D002675:Child, Preschool; D002758:Cholangiography; D015209:Cholangitis, Sclerosing / Q000150:complications* / Q000000981:diagnostic imaging; D015658:HIV Infections / Q000175:diagnosis / Q000209:etiology*; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008297:Male; D014376:Tuberculosis / Q000150:complications / Q000175:diagnosis
Cholangite sclérosante révélatrice d'une histiocytose X.