title: [Sclerosing cholangitis revealing histiocytosis X].
abstract: The case of a 3 year-old boy who presented isolated cholestasis as the initial symptom of histiocytosis X is described. Other symptoms occurred later on. Despite treatment (corticosteroid and Vinblastin), the disease continued to progress and the child died at the age of 4 1/2 years with HIV infection (contaminated blood product) and tuberculosis.
authors.affiliation: Service de Pédiatrie, Hôpital Antoine-Béclère, Clamart.
authors.forename: I
authors.initials: I
authors.lastname: Neveu
authors.forename: P
authors.initials: P
authors.lastname: Labrune
authors.forename: P
authors.initials: P
authors.lastname: Huguet
authors.forename: D
authors.initials: D
authors.lastname: Musset
authors.forename: J L
authors.initials: JL
authors.lastname: Chaussain
authors.forename: M
authors.initials: M
authors.lastname: Odièvre
mesh_terms: D002675:Child, Preschool; D002758:Cholangiography; D015209:Cholangitis, Sclerosing / Q000150:complications* / Q000000981:diagnostic imaging; D015658:HIV Infections / Q000175:diagnosis / Q000209:etiology*; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D008297:Male; D014376:Tuberculosis / Q000150:complications / Q000175:diagnosis
vernacular_title: Cholangite sclérosante révélatrice d'une histiocytose X.