title: [Obstetrical management in dysfibrinogenemia].
abstract: Dysfibrinogenaemia is an inherited disorder, characterised by a plasmafibrinogen in normal concentration, but of abnormal quality due to impaired release of fibrinopeptides and/or impaired aggregation of fibrinomonomers. The typical abnormalities of the laboratory findings will be demonstrated by presenting the case reports of 4 patients with 5 pregnancies (1 ectopic pregnancy); the importance of clinical exploration is emphasized. Newborn infants must be subjected to careful clinical and biochemical examination, because of factors of Mendelian dominant inheritance.
authors.affiliation: Frauenklinik im Klinikum Bamberg.
authors.forename: H
authors.initials: H
authors.lastname: Heidegger
authors.forename: M
authors.initials: M
authors.lastname: Spannagel
authors.forename: W
authors.initials: W
authors.lastname: Schramm
mesh_terms: D000328:Adult; D000347:Afibrinogenemia / Q000235:genetics / Q000628:therapy*; D001780:Blood Coagulation Tests; D002585:Cesarean Section; D005260:Female; D006474:Hemorrhagic Disorders / Q000628:therapy; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D007744:Obstetric Labor Complications / Q000628:therapy*; D011247:Pregnancy; D011250:Pregnancy Complications, Hematologic / Q000628:therapy*; D011274:Pregnancy, Tubal / Q000601:surgery; D012307:Risk Factors
vernacular_title: Geburtshilfliches Management bei Dysfibrinogenämie.