Surgical management of familial spontaneous pneumothorax.
Fifty-four members of two families were studied, nine of whom had familial spontaneous pneumothorax. The disease was inherited by autosomal-dominant type, with incomplete penetration and (or) variable expression. Five patients underwent bullectomy and parietal pleurectomy simultaneously on both sides via median sternotomy. Postoperative recovery was uneventful. Follow-up at 3 years shows no recurrences of pneumothorax.
Nickoladze
G D
GD
Department of Thoracic Surgery, Eristavy Institute of Surgery, Georgia, USSR.
D000293:Adolescent; D000328:Adult; D000368:Aged; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D010375:Pedigree; D011030:Pneumothorax / Q000209:etiology / Q000235:genetics / Q000601:surgery*; D011656:Pulmonary Emphysema / Q000150:complications / Q000235:genetics / Q000473:pathology