[The clinical aspects and treatment of renal angiolipomas in patients with tuberous sclerosis].
The incidence of multiple and bilateral renal angiomyolipomas in tuberous sclerosis patients is 40-80%. These benign abundantly vascularised tumours are almost always asymptomatic. Most of the symptomatic renal angiomyolipomas measure more than 4 cm. These lesions are attended by a high risk of spontaneous rupture and massive haemorrhage. In our series of 23 tuberous sclerosis patients with renal angiomyolipomas 4 became symptomatic. Three of them were successfully treated wtih transcatheter selective embolization. Preventive embolization of renal angiomyolipomas appears indicated if these measure more than 4 cm. A fifth patient became symptomatic before the diagnosis of tuberous sclerosis was made. She had a forme fruste. She was also successfully treated by the same method.
van Baal
J G
JG
Ziekenhuis St. Franciscus, afd. Chirurgie, Roosendaal.
Fleury
P
P
Brummelkamp
W H
WH
D000293:Adolescent; D000328:Adult; D004621:Embolization, Therapeutic; D005260:Female; D006391:Hemangioma / Q000150:complications* / Q000628:therapy; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications* / Q000628:therapy; D008067:Lipoma / Q000150:complications* / Q000628:therapy; D008297:Male; D014402:Tuberous Sclerosis / Q000150:complications*
Het klinische beeld en de behandeling van renal angiomyolipomen bij patiënten met tubereuze sclerose.