Childhood cicatricial pemphigoid with linear IgA deposits: a case report.
A 16-year-old boy with a bullous eruption from the age of thirteen, also presented symptoms of scarring conjunctivitis and involvement of oral mucosal membranes. Linear IgA deposits were demonstrated in the basement membrane zone in skin and conjunctiva. The eruptions improved during therapy with aldesulfonsodium, but complete remission was not obtained. Gluten-free diet did not significantly influence the activity of the disease. The described patient seems to fit in a recently described entity of chronic bullous diseases.
Langeland
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D000293:Adolescent; D003231:Conjunctivitis / Q000473:pathology; D003622:Dapsone / Q000031:analogs & derivatives / Q000627:therapeutic use; D006801:Humans; D007070:Immunoglobulin A / Q000378:metabolism*; D008297:Male; D009061:Mouth Mucosa / Q000473:pathology; D010390:Pemphigoid, Benign Mucous Membrane / Q000276:immunology* / Q000473:pathology / Q000628:therapy; D012872:Skin Diseases, Vesiculobullous / Q000276:immunology*
D007070:Immunoglobulin A; C036115:sulfoxone; D003622:Dapsone