Scintigraphic findings and follow up in Erdheim-Chester disease.
Two cases of Erdheim-Chester disease are presented: a 26-year-old white male patient with lipoidgranulomatosis of numerous long and flat bones and infiltration of pericardium, pleura, liver, spleen, thyroid, skin, conjunctiva, gingiva, and false vocal cord; and a 54-year-old white male with involvement of bones, orbits, brain, pericardium, and retroperitoneum. The scintigraphic findings in this disease are described, and a comprehensive review of the 27 previously reported cases is given including an assessment of the value of scintigraphy for diagnosis and follow up of this rare disease.
Department of Nuclear Medicine, Warren G. Magnuson Clinical Center, National Institutes of Health, Bethesda, MD 20892.
D
D
Sandrock
M J
MJ
Merino
B H
BH
Scheffknecht
R D
RD
Neumann
D000328:Adult; D001847:Bone Diseases / Q000000981:diagnostic imaging; D002784:Cholesterol; D005500:Follow-Up Studies; D006099:Granuloma / Q000000981:diagnostic imaging*; D006801:Humans; D008064:Lipidoses / Q000000981:diagnostic imaging*; D008297:Male; D008875:Middle Aged; D011877:Radionuclide Imaging; D013577:Syndrome; D013669:Technetium Tc 99m Medronate; D013671:Technetium Tc 99m Sulfur Colloid
D013671:Technetium Tc 99m Sulfur Colloid; D002784:Cholesterol; D013669:Technetium Tc 99m Medronate