Scintigraphic findings and follow up in Erdheim-Chester disease.
Two cases of Erdheim-Chester disease are presented: a 26-year-old white male patient with lipoidgranulomatosis of numerous long and flat bones and infiltration of pericardium, pleura, liver, spleen, thyroid, skin, conjunctiva, gingiva, and false vocal cord; and a 54-year-old white male with involvement of bones, orbits, brain, pericardium, and retroperitoneum. The scintigraphic findings in this disease are described, and a comprehensive review of the 27 previously reported cases is given including an assessment of the value of scintigraphy for diagnosis and follow up of this rare disease.
Sandrock
D
D
Department of Nuclear Medicine, Warren G. Magnuson Clinical Center, National Institutes of Health, Bethesda, MD 20892.
Merino
M J
MJ
Scheffknecht
B H
BH
Neumann
R D
RD
D000328:Adult; D001847:Bone Diseases / Q000000981:diagnostic imaging; D002784:Cholesterol; D005500:Follow-Up Studies; D006099:Granuloma / Q000000981:diagnostic imaging*; D006801:Humans; D008064:Lipidoses / Q000000981:diagnostic imaging*; D008297:Male; D008875:Middle Aged; D011877:Radionuclide Imaging; D013577:Syndrome; D013669:Technetium Tc 99m Medronate; D013671:Technetium Tc 99m Sulfur Colloid
D013671:Technetium Tc 99m Sulfur Colloid; D002784:Cholesterol; D013669:Technetium Tc 99m Medronate