Avascular necrosis of the capital femoral epiphysis in metachondromatosis.
A 6-year-old boy with metachondromatosis, an inherited disorder characterized by multiple enchondromas and exostoses, developed avascular necrosis of the capital femoral epiphysis mimicking Perthes disease. Despite containment, significant coxa magna occurred with flattening and lateral extrusion, requiring intertrochanteric osteotomy and shelf augmentation.
Alfred I. duPont Institute, Wilmington, DE 19899.
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Keret
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Bassett
D001859:Bone Neoplasms / Q000150:complications* / Q000235:genetics; D002675:Child, Preschool; D002812:Chondroma / Q000150:complications* / Q000235:genetics; D004838:Epiphyses / Q000098:blood supply; D005097:Exostoses, Multiple Hereditary / Q000150:complications / Q000000981:diagnostic imaging; D005271:Femur Head Necrosis / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery; D006801:Humans; D008297:Male; D011859:Radiography