title: [Cyanotic patient with right ventricular dilatation and ventricular arrhythmias].
abstract: Uhl's disease is a very rare congenital anomaly of the heart. Extreme dilatation of the right ventricle is accompanied by virtual absence of the right ventricular myocardium. We report on a 30-year-old woman with ventricular arrhythmias and atrial-septal defect where the diagnosis was made by echocardiography and confirmed by angiocardiography. Diagnostic and therapeutic possibilities are discussed.
mesh_terms: D000328:Adult; D006328:Cardiac Catheterization; D005117:Cardiac Complexes, Premature / Q000175:diagnosis*; D002311:Cardiomyopathy, Dilated / Q000151:congenital; D004452:Echocardiography; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000175:diagnosis; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans
vernacular_title: Zyanotische Patientin mit rechtsventrikulärer Dilatation und ventrikulären Herzrhythmusstörungen.