title: Adult Fanconi syndrome in primary amyloidosis with lambda light-chain proteinuria.
abstract: A 57-year-old woman who had had renal amyloidosis with nephrotic syndrome for five years was found to have the Fanconi syndrome and monoclonal lambda light-chain proteinuria. The amyloidosis of this patient was of primary type on the basis of the permanganate-resistant amyloid, the presence of monoclonal light-chain proteinuria, and the absence of clinical and histologic evidence of multiple myeloma. To best of our knowledge, this is the first case report in which primary amyloidosis with monoclonal lambda light-chain proteinuria was accompanied by adult Fanconi syndrome.
authors.affiliation: Department of Internal Medicine, Saga Medical School, Japan.
authors.forename: O
authors.initials: O
authors.lastname: Rikitake
authors.forename: T
authors.initials: T
authors.lastname: Sakemi
authors.forename: Y
authors.initials: Y
authors.lastname: Yoshikawa
authors.forename: Y
authors.initials: Y
authors.lastname: Nagano
authors.forename: T
authors.initials: T
authors.lastname: Watanabe
mesh_terms: D000686:Amyloidosis / Q000150:complications* / Q000473:pathology / Q000652:urine; D005198:Fanconi Syndrome / Q000150:complications* / Q000473:pathology / Q000652:urine; D005260:Female; D006801:Humans; D007147:Immunoglobulin Light Chains / Q000652:urine*; D007146:Immunoglobulin lambda-Chains / Q000652:urine*; D007678:Kidney Glomerulus / Q000473:pathology; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000209:etiology; D011507:Proteinuria / Q000150:complications* / Q000652:urine
chemical_list: D007147:Immunoglobulin Light Chains; D007146:Immunoglobulin lambda-Chains