[Acquired hyalinosis cutis et mucosae in plasmacytoma with monoclonal IgG-lambda gammopathy].
A 66-year-old female patient developed within 2 years clinical symptoms of hyalinosis cutis et mucosae due to a plasmocytoma with monoclonal IgG-light-chain gammopathy. The clinical diagnosis was supported by light- and electron-microscope studies. The form of hyalinosis cutis et mucosae described by Urbach and Wiethe is a genetic disease with its onset in early childhood. For this reason, we propose the designation "acquired hyalinosis cutis et mucosae" for the case reported here.
von der Helm
D
D
Dermatologische Klinik und Poliklinik Ludwig-Maximilians-Universität München.
Ring
J
J
Schmoeckel
C
C
Braun-Falco
O
O
D000368:Aged; D005260:Female; D006801:Humans; D007146:Immunoglobulin lambda-Chains / Q000032:analysis*; D008064:Lipidoses / Q000473:pathology*; D008065:Lipoid Proteinosis of Urbach and Wiethe / Q000473:pathology*; D008854:Microscopy, Electron; D009101:Multiple Myeloma / Q000473:pathology*; D010257:Paraneoplastic Syndromes / Q000473:pathology*; D010265:Paraproteinemias / Q000473:pathology*; D012867:Skin / Q000473:pathology; D012871:Skin Diseases / Q000473:pathology*
D007146:Immunoglobulin lambda-Chains
Erworbene Hyalinosis cutis et mucosae bei Plasmozytom mit monoklonaler IgG-lambda-Gammopathie.