[The Finnish-type congenital nephrotic syndrome. Comments on 2 cases].
The authors described the clinical, biologic and histologic particularities of two cases of congenital nephrotic syndrome, Finnish type. Clinically, the hydropic syndrome was represented by anasarca: biologically by marked proteinuria, hypoproteinemia with dysproteinemia and hyperlipemia with dyslipemia. Histologically both cases presented microcystic dilatation of the proximal tubuli contorti. The evolution was unfavorable and ended in death.
Sabău
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Potencz
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D005260:Female; D006801:Humans; D007223:Infant; D007668:Kidney / Q000473:pathology; D009404:Nephrotic Syndrome / Q000151:congenital* / Q000175:diagnosis / Q000473:pathology
Sindromul nefrotic congenital tip finlandez. Consideraţii pe margineaa două cazuri.