[The CREST syndrome associated with the sicca syndrome].
A case of CREST syndrome (calcinosis, Raynaud's phenomenon, esophageal hypomotility, sclerodactyly, and telangiectasia) that initially showed Raynaud's phenomenon, sclerodactyly and polyarthralgias, 3 years later completing the process, associated to sicca syndrome, is presented. The esophageal affectation showed a loss of peristalsis of the inferior 2/3, as well as hypotonia of the gastroesophageal sphincter. We comment the prognostic relationship between CREST syndrome and the centromeric region antibodies.
González Perez
J A
JA
Calvo Catala
J
J
Almela Requena
J V
JV
González-Cruz Cervellera
A
A
Sospedra Lara
E M
EM
Hurtado Vicente
M J
MJ
D000906:Antibodies / Q000032:analysis; D002114:Calcinosis / Q000175:diagnosis*; D002503:Centromere / Q000276:immunology; D004935:Esophageal Diseases / Q000175:diagnosis*; D005260:Female; D006801:Humans; D008875:Middle Aged; D011379:Prognosis; D011928:Raynaud Disease / Q000175:diagnosis*; D012595:Scleroderma, Systemic / Q000175:diagnosis*; D012859:Sjogren's Syndrome / Q000175:diagnosis*; D013577:Syndrome; D013684:Telangiectasis / Q000175:diagnosis*
D000906:Antibodies
Síndrome de CREST asociado a síndrome seco.