title: Glaucoma in the Maroteaux-Lamy syndrome.
abstract: We report four patients who had glaucoma in association with the Maroteaux-Lamy syndrome. Two of these patients had acute angle-closure glaucoma, one had chronic angle-closure glaucoma, and one was treated for open-angle glaucoma; however, the angle structures could not be seen by gonioscopy. Standard peripheral iridectomy was inadequate for treatment of this angle-closure glaucoma because of the considerably increased thickness of the peripheral cornea that occurs in these patients. Our findings suggest that glaucoma may be more common in the Maroteaux-Lamy syndrome than has been realized and that the initial mechanism is secondary acute or chronic angle closure not related to pupillary block.
authors.affiliation: Department of Ophthalmology, Indiana University School Of Medicine, Indianapolis.
authors.forename: L B
authors.initials: LB
authors.lastname: Cantor
authors.forename: J A
authors.initials: JA
authors.lastname: Disseler
authors.forename: F M
authors.initials: FM
authors.lastname: Wilson
mesh_terms: D000328:Adult; D000959:Antihypertensive Agents / Q000627:therapeutic use; D003315:Cornea / Q000473:pathology; D003452:Cryosurgery; D005260:Female; D005901:Glaucoma / Q000209:etiology* / Q000473:pathology / Q000628:therapy; D006068:Gonioscopy; D006801:Humans; D007429:Intraocular Pressure; D007498:Iris / Q000601:surgery; D009085:Mucopolysaccharidosis IV / Q000150:complications*
chemical_list: D000959:Antihypertensive Agents