Transcultural understanding of a hereditary disorder. Mucopolysaccharidosis VI in a Vietnamese family.
A case study of a family referred for clarification of cultural issues illustrates how a transcultural psychiatric service developed in the pediatric hospital setting can be used to advantage. A Vietnamese family with an inherited disorder. Mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome, MPS VI), resisted genetic counseling and contraception. Three out of their six children were affected, one with a fatal outcome. The transcultural consultation offered an understanding of their behavior and facilitated subsequent management.
Handelman
L
L
Department of Child and Family Psychiatry, Royal Children's Hospital, Melbourne, Australia.
Menahem
S
S
Eisenbruch
I M
IM
D001294:Attitude to Health; D003469:Culture; D005260:Female; D005817:Genetic Counseling; D006801:Humans; D007223:Infant; D008297:Male; D009083:Mucopolysaccharidoses / Q000235:genetics*; D009087:Mucopolysaccharidosis VI / Q000235:genetics*; D014744:Vietnam