[Ectopia cordis. Report of a prenatally diagnosed cases and a short review of the literature].
Ectopia cordis is defined as a congenital malposition of the heart partially or completely outside the thorax. Severe structural malformations of the heart are very frequently associated and are responsible for the extremely poor prognosis. Only 16 out of 219 cases reported in the literature up to now have survived. We report on a case of Ectopia cordis thoraco-abdominalis associated with an univentricular heart and a hypoplastic pulmonary vascular bed detected prenatally in the 32nd week of gestation. The male newborn died 23 h after a spontaneous and uneventful delivery at term. Considering the poor prognosis no surgical attempts had been undertaken to correct the malformation.
Ulmer
H E
HE
Abteilung Pädiatrische Kardiologie, Kinderklinik, Universität Heidelberg.
Stolz
W
W
Kühl
G
G
Mechtersheimer
G
G
D000009:Abdominal Muscles / Q000002:abnormalities; D000328:Adult; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011247:Pregnancy; D011296:Prenatal Diagnosis; D014463:Ultrasonography
Ectopia cordis. Bericht über einen pränatal diagnostizierten Fall und eine kurze Ubersicht über die Literatur.