Multiple arteriovenous malformations of the small intestine in a patient with protein S deficiency.
The authors report a case of arteriovenous malformations (AVMs) of the small intestine in a young patient with protein S deficiency. These disorders have not been previously reported to occur together. Protein S deficiency may cause thromboses in unusual sites, including the mesenteric veins. Several mechanisms linking protein S deficiency to the occurrence of AVMs in this patient are offered.
Guarner
J
J
Department of Pathology, Grady Memorial Hospital, Emory University School of Medicine, Atlanta, Georgia.
Grossman
B
B
Judd
R
R
Wideman
C
C
Evatt
B
B
D000328:Adult; D001165:Arteriovenous Malformations / Q000150:complications* / Q000473:pathology; D001808:Blood Vessels / Q000473:pathology; D006023:Glycoproteins / Q000172:deficiency*; D006801:Humans; D007421:Intestine, Small / Q000098:blood supply*; D008297:Male; D010375:Pedigree; D017293:Protein S
D006023:Glycoproteins; D017293:Protein S