Papillon-Lefevre syndrome: report of two brothers.
Papillon-Lefevre syndrome was observed in two boys in the same family, and the topic of this report, the second to appear in the Greek dental literature. Both patients presented with hyperkeratosis of the palms and soles and severe periodontal destruction; the latter was more prominent in the younger boy. The children will lose their teeth before reaching maturity.
Vassilopoulou
A
A
Department of Pedodontics, School of Dentistry, Athens University, Greece.
Laskaris
G
G
D001862:Bone Resorption / Q000235:genetics / Q000473:pathology; D002648:Child; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000235:genetics*; D008297:Male; D010214:Papillon-Lefevre Disease / Q000235:genetics* / Q000473:pathology; D010510:Periodontal Diseases / Q000235:genetics / Q000473:pathology; D014086:Tooth Mobility / Q000235:genetics / Q000473:pathology