[Middle-term result of surgery in 78 cases of complete atrioventricular canal before one year of age].
Between 1970 and 1985, 78 children with complete atrioventricular canal were operated upon before the age of one year at the Marie-Lannelongue Surgical Centre. Forty-seven survivors were followed up for periods of 3 months to 13 years after the initial operation; 2 were lost of following. Among the 13 children who survived banding, 1 died spontaneously, 1 had Blalock-Taussig anastomosis and 11 underwent full repair with 5 deaths; out of 6 survivors, 4 are doing well without any treatment, 1 was reoperated upon twice and died during the second operation, and 1 was lost sight of; the survival rates at 5 and 10 years are 46 +/- 23 p. 100 and 29 +/- 23 p. 100 respectively. Among the 34 children who survived an initial complete repair, 2 were reoperated upon 3 months after the repair, with 1 death, 7 subsequently died of infection (6 had trisomy 21); out of 26 survivors followed up for 3 years and 3 months on average after the complete repair (2 to 13 years), 18 show an excellent result and 3 a mediocre result; the survival rates at 5 and 10 years are 45 +/- 9 p. 100 and 30 +/- 27 p. 100 respectively. Whether the patients initially had banding followed by complete repair or complete repair from the start, the probability of survival at 5 and 10 years was the same. The presence of trisomy 21 is an unfavourable prognostic factor at medium-term.(ABSTRACT TRUNCATED AT 250 WORDS)
Barazer
P Y
PY
Centre chirurgical Marie-Lannelongue, Le Plessis-Robinson.
Losay
J
J
Lacour-Gayet
F
F
Planché
C
C
Binet
J P
JP
D004314:Down Syndrome / Q000150:complications / Q000401:mortality; D005260:Female; D005500:Follow-Up Studies; D006343:Heart Septal Defects / Q000150:complications / Q000401:mortality / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011184:Postoperative Period; D011379:Prognosis; D012086:Reoperation
Résultat à moyen terme de la chirurgie dans 78 canaux atrio-ventriculaires complets opérés avant l'âge d'un an.