[Gardner syndrome].
Three patients, sisters of B, 12 and 14 years of age with a diagnosis of Gardner's Syndrome are reported. The family history indicated that their mother died of a carcinoma of the intestine at the age of 30. This Syndrome, which is of dominant autosomic inheritance, can be seen in aur city, with so heterogeneous hereditary features. Dentists must know the oral cavity characteristics of this disease (odontomas, cementomas, cysts, supernumerary teeth) that accompany gastric, intestinal, skeletal and tissular disturbances an of other organs (polyps, osteomas, cysts, adenomas), being intestinal poliposis of the colon the most important feature that becomes an "Adenocarcinoma", in the third ald fourth decade in a 100% of the cases. Its incidence in our city is real. The proper diagnosis is made when the clinical study is completed and the dentist may be the first one to watch this syndrome's feature in the oral cavity. A proper medical diagnosis would allow a preventive procedure and a patient's control until the "total surgery of the colon", which is the appropriate therapeutic procedure, is achieved; although there are controversies as regards the time to be carried out.
de Hidalgo
P K
PK
de Irazuzta
V A
VA
Tramunt
B
B
D000293:Adolescent; D002485:Cementoma; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D005736:Gardner Syndrome / Q000175:diagnosis / Q000473:pathology; D006801:Humans; D007573:Jaw Neoplasms; D008310:Malocclusion; D009810:Odontoma; D014071:Tooth Abnormalities; D014097:Tooth, Unerupted
Sindrome de Gardner.