title: [Diffuse retroperitoneal lymphangioleiomatosis].
abstract: A case of diffuse retroperitoneal lymphangiomatosis manifested by oedema of the left lower limb is reported. Non-invasive exploratory methods revealed a retroperitoneal pseudo-tumoral image. At laparotomy, a retro- and subperitoneal infiltration was discovered, and histology showed benign smooth muscle proliferation developed from the muscular layer of lymph vessels. There is no known successful surgical procedure for this type of lesion, and none of the treatments tested (oophorectomy or hormonal therapy) has proved to be effective.
authors.affiliation: Département de Chirurgie, Hôpital Américain de Paris, Neuilly.
authors.forename: P
authors.initials: P
authors.lastname: Bloch
authors.forename: G
authors.initials: G
authors.lastname: Meshaka
authors.forename: E
authors.initials: E
authors.lastname: Takeara
authors.forename: M
authors.initials: M
authors.lastname: Hamdan
mesh_terms: D000328:Adult; D004487:Edema / Q000209:etiology; D005260:Female; D006801:Humans; D007866:Leg; D008203:Lymphangiomyoma / Q000150:complications / Q000473:pathology* / Q000628:therapy; D008232:Lymphoproliferative Disorders / Q000473:pathology*; D010052:Ovariectomy; D012186:Retroperitoneal Neoplasms / Q000150:complications / Q000473:pathology* / Q000628:therapy
vernacular_title: Lymphangioléiomyomatose diffuse rétropéritonéale.