title: [Multiple endocrine neoplasia of the II B type].
abstract: Multiple endocrine neoplasia, type II B (MEN II B) includes thyroid carcinoma, pheochromocytoma, ganglioneuromatosis and marfanoid habitus. Its short-term prognosis is determined by the tumour of the adrenal gland, whereas long-term prognosis is determined by the thyroid carcinoma. Often the well-defined but rare syndrome is diagnosed late. The MEN II B's therapy consists of thyroidectomy and adrenalectomy uni- or bilateral. The 5 year-rate of survival is 75%. Own observations are reported.
authors.affiliation: Abteilung für Kinderchirurgie der Klinik und Poliklinik für Chirurgie des Bereiches Medizin der Friedrich-Schiller-Universität Jena, DDR.
authors.forename: H
authors.initials: H
authors.lastname: Schickedanz
authors.forename: V
authors.initials: V
authors.lastname: Hesse
authors.forename: E
authors.initials: E
authors.lastname: Kauf
authors.forename: F
authors.initials: F
authors.lastname: Mohr
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000601:surgery; D000328:Adult; D002277:Carcinoma / Q000601:surgery; D006801:Humans; D008297:Male; D009377:Multiple Endocrine Neoplasia / Q000235:genetics / Q000601:surgery*; D010641:Phenotype; D010673:Pheochromocytoma / Q000601:surgery; D013964:Thyroid Neoplasms / Q000601:surgery; D013965:Thyroidectomy
vernacular_title: Die multiple endokrine Neoplasie des Typs II B.