[Multiple endocrine neoplasia of the II B type].
Multiple endocrine neoplasia, type II B (MEN II B) includes thyroid carcinoma, pheochromocytoma, ganglioneuromatosis and marfanoid habitus. Its short-term prognosis is determined by the tumour of the adrenal gland, whereas long-term prognosis is determined by the thyroid carcinoma. Often the well-defined but rare syndrome is diagnosed late. The MEN II B's therapy consists of thyroidectomy and adrenalectomy uni- or bilateral. The 5 year-rate of survival is 75%. Own observations are reported.
Schickedanz
H
H
Abteilung für Kinderchirurgie der Klinik und Poliklinik für Chirurgie des Bereiches Medizin der Friedrich-Schiller-Universität Jena, DDR.
Hesse
V
V
Kauf
E
E
Mohr
F
F
D000310:Adrenal Gland Neoplasms / Q000601:surgery; D000328:Adult; D002277:Carcinoma / Q000601:surgery; D006801:Humans; D008297:Male; D009377:Multiple Endocrine Neoplasia / Q000235:genetics / Q000601:surgery*; D010641:Phenotype; D010673:Pheochromocytoma / Q000601:surgery; D013964:Thyroid Neoplasms / Q000601:surgery; D013965:Thyroidectomy
Die multiple endokrine Neoplasie des Typs II B.