title: [Observations on the Camurati-Engelmann syndrome. Demonstration of changes of the petrous bone using high-resolution computed tomography].
abstract: In Camurati-Engelmann disease HR-CT can impressively demonstrate the involvement of the skull base and also correlate well with the clinical symptoms of deafness, vestibular disturbances and facial paralysis. Since conservative treatment with corticosteroids, calcitonin and diphosphonates is hardly successful and compression of the cranial nerves practically absent, surgical treatment with decompression should be considered. Differential diagnosis against other bone affections with deafness depends on age, typical x-ray findings, local distribution and clinical signs.
authors.affiliation: Abteilung für Neuroradiologie, Universität Tübingen.
authors.forename: B
authors.initials: B
authors.lastname: Dannenmaier
authors.forename: B
authors.initials: B
authors.lastname: Weber
mesh_terms: D000328:Adult; D003966:Camurati-Engelmann Syndrome / Q000000981:diagnostic imaging* / Q000235:genetics / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D010009:Osteochondrodysplasias / Q000000981:diagnostic imaging*; D010579:Petrous Bone / Q000000981:diagnostic imaging* / Q000473:pathology; D014057:Tomography, X-Ray Computed
vernacular_title: Beobachtungen zum Camurati-Engelmann-Syndrom. Darstellung der Veränderungen im Bereich der Felsenbeine mit Hilfe der HR-Computertomographie.