[Surgery of the adrenal glands in Sipple's syndrome. Apropos of 8 cases].
In a series of 82 pheochromocytomas operated on, the authors report 8 cases of Sipple's syndrome, currently classified by Steiner among the type II multiple endocrine neoplasia (MEN II). Six patients were operated on, the mean follow up being 4 years. These patients all underwent total thyroidectomy and 4 of them total bilateral adrenalectomy. Gluco and mineralocorticoid and thyroid hormone replacement therapy was instituted. No clinical or biological recurrence has been noted. The ideal therapeutic schema is difficult to define given the rarity of MEN II.
Henry
J F
JF
Unité de Chirurgie Endocrinienne, CHU de la Timone, Marseille.
Audiffret
J
J
Denizot
A
A
D000310:Adrenal Gland Neoplasms / Q000453:epidemiology / Q000601:surgery*; D000328:Adult; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D009377:Multiple Endocrine Neoplasia / Q000601:surgery*; D010673:Pheochromocytoma / Q000453:epidemiology / Q000601:surgery*; D013964:Thyroid Neoplasms / Q000601:surgery*
Chirurgie des surrénales dans le syndrome de Sipple. A propos de 8 cas.