title: Development of pulmonary arteriovenous malformations after modified Fontan operations.
abstract: Two patients with complex cyanotic congenital heart disease and without previous Glenn anastomosis underwent modified Fontan operations. Postoperatively, pulmonary arteriovenous malformations developed that resulted in cyanosis from significant intrapulmonary right-to-left shunting. These malformations were detected by pulmonary angiograms and contrast echocardiograms. Pulmonary arteriovenous malformations may be a major cause of late clinical deterioration in patients treated with modified Fontan operations.
authors.affiliation: Section of Pediatric Cardiology, Walter Reed Army Medical Center, Washington, DC 20307-5001.
authors.forename: J W
authors.initials: JW
authors.lastname: Moore
authors.forename: W C
authors.initials: WC
authors.lastname: Kirby
authors.forename: W A
authors.initials: WA
authors.lastname: Madden
authors.forename: N S
authors.initials: NS
authors.lastname: Gaither
mesh_terms: D001164:Arteriovenous Fistula / Q000000981:diagnostic imaging / Q000209:etiology*; D006348:Cardiac Surgical Procedures / Q000009:adverse effects*; D002675:Child, Preschool; D005260:Female; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000000981:diagnostic imaging; D011652:Pulmonary Circulation; D011667:Pulmonary Veins / Q000000981:diagnostic imaging; D011859:Radiography