[Anesthesia for a patient with Ehlers-Danlos syndrome and factor XIII deficiency].
Emergency anesthesia was carried out for a patient with Ehlers-Danlos syndrome (type IV) and factor XIII deficiency. The operation was a ligation of the bleeding right subclavian artery. One month later, a transverse colectomy and splenectomy was performed for a necrotic perforation of the colon, but the wound did not heal completely. The patient died of another perforation of the intestine two months later. Anesthetic management of a patient with Ehlers-Danlos syndrome and factor XIII deficiency was reviewed. Particular problems concerning a genetic disease were also discussed.
Suzuki
T
T
Tsuchiyama
Y
Y
Kawaguchi
Y
Y
Sougawa
T
T
Nakamura
H
H
Kinoshita
T
T
D000328:Adult; D000758:Anesthesia / Q000379:methods*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005177:Factor XIII Deficiency / Q000150:complications*; D006801:Humans; D008297:Male