[The rigid spine syndrome].
Five patients with the clinical picture of rigid spine syndrome are presented. Three of them were females. All these patients fulfilled the clinical criteria for rigid spine syndrome. On the basis of the analysis of these patients and the data from literature, it was established that Dystrophia musculorum progressiva--Emery-Dreifuse was one of the causes of rigid spine syndrome in one patient. In the other four patients unspecific myopathic changes were found. The only common feature was marked proliferation of endomysium and perimysium (connective tissue). An effort was made to solve the nosological problems on the contemporary level of knowledge. The heterogenous group of rigid spine syndrome was divided into the three subgroups: 1) Rigid spine syndrome with nosologically determined neuromuscular disorder; 2) Rigid spine syndrome on myopathic basis, but nonspecific and unrecognizable as an entity; 3) Rigid spine syndrome with disorders of non-neuromuscular origin, but with that related to bones, joints or connective tissue.
Drndarski
I
I
Todorović
S
S
D000293:Adolescent; D000328:Adult; D005260:Female; D006801:Humans; D008297:Male; D013122:Spinal Diseases / Q000209:etiology / Q000473:pathology; D013577:Syndrome
Sindrom ukocene kicme.