Foix-Chavany-Marie-syndrome--neurological, neuropsychological, CT, MRI, and SPECT findings in a case progressive for more than 10 years.
In a 66-year-old woman signs and symptoms of bilateral opercular syndrome (Foix-Chavany-Marie-syndrome) developed progressively over a period of more than 10 years. Facio-linguo-velopharyngeo-masticatory diplegia with automatic-voluntary dissociation was accompanied by motor aphasia and oral apraxia leading to a state of almost complete anarthria. Although it initially resembled the anterior biopercular syndrome there are also features indicating involvement of the posterior opercula. Although the aetiology remains obscure without pathological data, a bilateral focal brain atrophy is assumed. This is probably the first case documented by MRI and SPECT.
Lang
C
C
Department of Neurology, University of Erlangen-Nürnberg, Federal Republic of Germany.
Reichwein
J
J
Iro
H
H
Treig
T
T
D000368:Aged; D001072:Apraxias / Q000175:diagnosis; D001284:Atrophy; D001921:Brain / Q000473:pathology; D001925:Brain Damage, Chronic / Q000175:diagnosis*; D010244:Bulbar Palsy, Progressive / Q000175:diagnosis*; D003937:Diagnosis, Differential; D004401:Dysarthria / Q000175:diagnosis; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008279:Magnetic Resonance Imaging; D009483:Neuropsychological Tests; D013577:Syndrome; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed; D014681:Velopharyngeal Insufficiency / Q000175:diagnosis