title: [Anesthesia for a patient with Ehlers-Danlos syndrome and factor XIII deficiency].
abstract: Emergency anesthesia was carried out for a patient with Ehlers-Danlos syndrome (type IV) and factor XIII deficiency. The operation was a ligation of the bleeding right subclavian artery. One month later, a transverse colectomy and splenectomy was performed for a necrotic perforation of the colon, but the wound did not heal completely. The patient died of another perforation of the intestine two months later. Anesthetic management of a patient with Ehlers-Danlos syndrome and factor XIII deficiency was reviewed. Particular problems concerning a genetic disease were also discussed.
authors.forename: T
authors.initials: T
authors.lastname: Suzuki
authors.forename: Y
authors.initials: Y
authors.lastname: Tsuchiyama
authors.forename: Y
authors.initials: Y
authors.lastname: Kawaguchi
authors.forename: T
authors.initials: T
authors.lastname: Sougawa
authors.forename: H
authors.initials: H
authors.lastname: Nakamura
authors.forename: T
authors.initials: T
authors.lastname: Kinoshita
mesh_terms: D000328:Adult; D000758:Anesthesia / Q000379:methods*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005177:Factor XIII Deficiency / Q000150:complications*; D006801:Humans; D008297:Male