Intrathoracic lymphangiomatosis mimicking lymphangioleiomyomatosis in a young woman.
In this report, we describe a case of lymphangiomatosis that mimicked lymphangioleiomyomatosis in a 20-year-old woman. Lung biopsy specimens showed proliferation of anastomosing lymphatic channels in the visceral pleura and dilated peribronchiolar and septal lymphatic channels. During 8 years of follow-up, this process behaved like lymphangioleiomyomatosis with reticulonodular infiltrates and worsening obstructive and restrictive changes evident on pulmonary function tests.
Swank
D W
DW
Department of Laboratory Medicine, University of North Dakota, Minot.
Hepper
N G
NG
Folkert
K E
KE
Colby
T V
TV
D000328:Adult; D002916:Chylothorax / Q000209:etiology*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008202:Lymphangioma / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008203:Lymphangiomyoma / Q000175:diagnosis*; D008232:Lymphoproliferative Disorders; D010997:Pleural Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology