[Cardiac surgery of tetralogy of Fallot associated with DiGeorge syndrome: a case report].
A case of 7-year-old boy with tetralogy of Fallot associated with DiGeorge syndrome was reported. He had been diagnosed as cardio-facial syndrome with hypoparathyroidism because of hypocalcemia, convulsion, cardiac defect and the characteristic face. But immunologic study showed hypofunction of cellular immunity and cardiac catheterization and angiogram revealed the Tetralogy of Fallot. So we diagnosed as DiGeorge syndrome and performed operation. The thymus was not found and we close the ventricular defect with patch and reconstructed right ventricular outflow tract with transannular patch. We often measured serum ionized calcium level and corrected with calcium gluconate intravenously. Peritoneal dialysis was done due to oliguria and much inotropic support was necessary.
Satokawa
H
H
Hoshino
S
S
Iwaya
F
F
Igari
T
T
Ando
M
M
Abe
T
T
Takano
K
K
Hagiwara
K
K
Tanji
M
M
Watanabe
M
M
D002648:Child; D004062:DiGeorge Syndrome / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D007153:Immunologic Deficiency Syndromes / Q000150:complications*; D008297:Male; D008722:Methods; D013771:Tetralogy of Fallot / Q000150:complications / Q000601:surgery*