Two-stage correction of thumb adduction contracture in Freeman-Sheldon syndrome (craniocarpotarsal dysplasia).
Freeman-Sheldon syndrome is a rare congenital anomaly that is characterized by facial, hand, and foot deformities. We describe a female infant who had severe adduction contractures of the thumbs. A two-stage reconstruction was done. The first web space soft tissues were stretched with a transversely oriented external skeletal distractor, then a conventional first web space deepening and release was performed.
Wenner
S M
SM
Shriner's Hospital for Crippled Children, Springfield, Mass.
Shalvoy
R M
RM
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000534:rehabilitation / Q000601:surgery*; D005147:Facial Bones / Q000002:abnormalities; D005260:Female; D005532:Foot Deformities, Congenital / Q000473:pathology; D006228:Hand Deformities, Congenital / Q000000981:diagnostic imaging / Q000534:rehabilitation / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D011859:Radiography; D013933:Thumb / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery