Generalised lymphangiomatosis with chylothorax.
A 9 month old boy presented with acute respiratory distress and was found to have a left pleural effusion. The chylous nature of the effusion, multiple bony lytic lesions, and splenic cysts lead to the diagnosis of congenital lymphangiomatosis with chylothorax. Surgical intervention including pleurectomy was required after unsuccessful conservative management.
Dunkelman
H
H
Northwick Park Hospital, Harrow.
Sharief
N
N
Berman
L
L
Ninan
T
T
D001859:Bone Neoplasms / Q000150:complications*; D002916:Chylothorax / Q000209:etiology* / Q000628:therapy; D004322:Drainage; D006801:Humans; D007223:Infant; D008202:Lymphangioma / Q000150:complications*; D008297:Male; D010996:Pleural Effusion / Q000209:etiology