[A new diagnostic approach in lymphangiomatosis. Apropos of a case].
Lymphangiomyomatosis is a rare disease affecting exclusively women usually in child-bearing age. It is characterized by proliferation of an atypical smooth muscle involving the pulmonary, mediastinal and retroperitoneal lymph system. The case reported here concerns a 53-year old woman presenting with an interstitial pulmonary lesion giving a characteristic image at CT. The patient also had recurrent chylothorax and a renal angiomyolipoma explored by CT and magnetic resonance imaging. The diagnosis of lymphangiomyomatosis was made on a cluster of arguments, without having recourse to surgical lung biopsy.
Humbert
M
M
Service de Pneumologie, Hôpital Tenon, Paris.
Liote
H
H
Carette
M F
MF
Rosencher
L
L
Akoun
G M
GM
D002916:Chylothorax / Q000209:etiology; D004417:Dyspnea / Q000209:etiology; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging; D007889:Leiomyoma / Q000150:complications; D008203:Lymphangiomyoma / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging; D008232:Lymphoproliferative Disorders / Q000175:diagnosis*; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D010996:Pleural Effusion / Q000209:etiology; D011658:Pulmonary Fibrosis / Q000175:diagnosis / Q000209:etiology*; D014057:Tomography, X-Ray Computed; D014594:Uterine Neoplasms / Q000150:complications
Nouvelle approche diagnostique de la lymphangiomyomatose. A propos d'une observation.