[Generalized lymphangiomatosis. 25-year follow-up of a case of lymphangiomatosis].
Lymphangiomatosis is a rare systemic lymphatic malformation with intra- and extraosseous lesions. The etiology is poorly understood. Presented is the case of a patient with a generalized lymphangiomatosis manifested by cystic formations in many bones and a large cavernous lymph sac behind her sternum. Clinical, diagnostic, prognostic and therapeutic aspects are reviewed. The condition of the patient remained without complications for more than 25 years, except for two episodes of rather severe respiratory infections.
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D000293:Adolescent; D000328:Adult; D001859:Bone Neoplasms / Q000000981:diagnostic imaging*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008202:Lymphangioma / Q000000981:diagnostic imaging*; D009378:Neoplasms, Multiple Primary / Q000000981:diagnostic imaging*; D011859:Radiography; D013899:Thoracic Neoplasms / Q000000981:diagnostic imaging*
Lymphangiomatosis generalisata. 25 jaar follow-up van een geval van lymfangiomatosis.