Lipoid proteinosis: Urbach-Wiethe disease.
An otherwise healthy patient with Urbach-Wiethe disease required surgical removal of two 3rd molar teeth. In this multisystem disorder infiltration of the buccal, pharyngeal and laryngeal mucosa may cause difficulties with tracheal intubation and increase the likelihood of trauma. The anaesthetic implications and management are described.
Kelly
J E
JE
Department of Anaesthetics, St George's Hospital, London.
Simpson
M T
MT
Jonathan
D
D
Hollway
T E
TE
D000328:Adult; D000766:Anesthesia, Dental; D000768:Anesthesia, General; D006801:Humans; D007442:Intubation, Intratracheal; D008064:Lipidoses / Q000150:complications*; D008065:Lipoid Proteinosis of Urbach and Wiethe / Q000150:complications*; D008297:Male; D008963:Molar; D014081:Tooth Extraction