title: Clear cell sarcoma of the kidney--a case report.
abstract: Clear cell sarcoma of the kidney (CCSK) is a highly malignant childhood tumor, distinguished from classic Wilms' tumor by its propensity to metastasize to the skeletal system. Authors described a case of CCSK from a 3-year-old boy in the right kidney, showing various histologic features, such as classic, epithelioid, trabecular, neurilemmoma-like, cystic and entrapped collecting tubular pattern. Ultrastructurally epithelial differentiation was absent. Immunohistochemically, none of the intrinsic tumor cells showed positive staining with the antibodies against the keratin, S-100 protein, carcinoembryonic antigen, vimentin, desmin and myoglobin, suggesting primitive mesenchymal cell in origin.
authors.affiliation: Department of Pathology, College of Medicine, Chung-Ang University, Seoul, Korea.
authors.forename: J S
authors.initials: JS
authors.lastname: Seo
authors.forename: Y W
authors.initials: YW
authors.lastname: Park
authors.forename: K Y
authors.initials: KY
authors.lastname: Song
authors.forename: S T
authors.initials: ST
authors.lastname: Chang
mesh_terms: D002675:Child, Preschool; D006801:Humans; D007150:Immunohistochemistry; D007680:Kidney Neoplasms / Q000378:metabolism / Q000473:pathology*; D008297:Male; D009362:Neoplasm Metastasis; D012509:Sarcoma / Q000378:metabolism / Q000473:pathology*