Congenital perilymphatic fistula: an overlooked diagnosis?
Congenital perilymphatic fistula (CPLF) often is the sole cause of sensorineural hearing loss in children that is both progressive and subtle and, therefore, can elude detection by physicians. A 3-year prospective study of 244 children with sensorineural hearing loss of unknown etiology demonstrated that at least 6% (15/244) had CPLF. Close audiologic monitoring and radiologic imaging of the temporal bone of children with sensorineural hearing loss are recommended to detect CPLF.
Reilly
J S
JS
University of Alabama, Birmingham.
Kenna
M A
MA
D002648:Child; D004432:Ear, Middle / Q000002:abnormalities*; D005260:Female; D005402:Fistula / Q000150:complications / Q000151:congenital* / Q000175:diagnosis / Q000453:epidemiology; D006319:Hearing Loss, Sensorineural / Q000209:etiology; D006801:Humans; D007761:Labyrinthine Fluids; D008297:Male; D010498:Perilymph; D015995:Prevalence; D011446:Prospective Studies