Dandy-Walker syndrome: follow up of an unoperated case and her identical twin.
A child who had the Dandy-Walker syndrome along with her healthy twin sibling were followed regularly for a period of 2 years. Both of the twins had normal development regarding the fine motor movements and social adaptation. The main neurological defect on the affected twin was a severe hearing loss clinically and reduced responses on auditory brainstem evoked potential examination. We present this rare instance in which Dandy-Walker syndrome involved discordantly in only one of a set of identical twins.
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D003616:Dandy-Walker Syndrome / Q000150:complications / Q000503:physiopathology; D003638:Deafness / Q000209:etiology; D004200:Diseases in Twins; D005072:Evoked Potentials, Auditory; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D006849:Hydrocephalus / Q000150:complications / Q000503:physiopathology; D007231:Infant, Newborn