title: Alpha 1-antitrypsin deficiency (Pi SZ) and biliary atresia.
abstract: We report an infant who presented at 2 days of age with conjugated hyperbilirubinemia. Serological, radiographic, and surgical investigations revealed the concurrence of alpha-1-antitrypsin deficiency, protease inhibitor type SZ, and extrahepatic biliary atresia.
authors.affiliation: Department of Pediatrics, University of Iowa Hospitals, Iowa City 52242.
authors.forename: N
authors.initials: N
authors.lastname: Tolaymat
authors.forename: R
authors.initials: R
authors.lastname: Figueroa-Colon
authors.forename: F A
authors.initials: FA
authors.lastname: Mitros
mesh_terms: D001656:Biliary Atresia / Q000150:complications* / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D019896:alpha 1-Antitrypsin Deficiency