[Elastic nevi of a familial nature. Buschke-Ollendorf syndrome. Forme frustre?].
Four cases of "connective naevus" have been revised in a family, mother and her two daughters and son. The histology shows as principal characteristic hyperplasia, thickness and crossing disposition of elastic fibers, forming an image similar to the one of an "elastic naevus". Because of its familiar features and the absence of osteopoikilosis, we postulate a frustrate form of the Buschke-Ollendorf syndrome.
Macedo
N
N
Clinica de Dermatología, Facultad de Medicina de Montevideo, Uruguay.
Vignale
R
R
González
V
V
Bravo
D
D
de Anda
G
G
D000293:Adolescent; D000328:Adult; D002648:Child; D004547:Elastic Tissue / Q000473:pathology*; D005260:Female; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000235:genetics; D009506:Nevus / Q000235:genetics* / Q000473:pathology; D010023:Osteopoikilosis / Q000235:genetics / Q000473:pathology; D012878:Skin Neoplasms / Q000235:genetics* / Q000473:pathology; D013577:Syndrome
Nevos elásticos de carácter familiar. Síndrome de Buschke-Ollendorf. Forma frustra?