[Recurrent Budd-Chiari syndrome as a complication of nocturnal paroxysmal hemoglobinuria].
Budd-Chiari syndrome is a frequent complication of nocturnal paroxysmal hemoglobinuria, histologic and angiographic study being fundamental for diagnosis. We emphasize the importance of ultrasonography and abdominal CAT as noninvasive methods of early diagnosis, and the value of ultrasonography in the follow-up of these patients. Radical therapy of the disease from onset is a determinant of the final prognosis of these patients, as well as early treatment of thrombosis with thrombolytics and/or anticoagulants.
Cutrín Prieto
C
C
Otero Echart
M
M
Carballo Fernández
C
C
Pazos González
G
G
Bugarín González
R
R
Tomé Martínez de Rituerto
S
S
Barrio Gómez
E
E
D000368:Aged; D006502:Budd-Chiari Syndrome / Q000175:diagnosis / Q000209:etiology*; D006457:Hemoglobinuria, Paroxysmal / Q000150:complications*; D006503:Hepatic Veins / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D012008:Recurrence; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
Síndrome de Budd-Chiari recidivante como complicación de una hemoglobinuria paroxística nocturna.