Malignant rhabdoid tumor of the orbit.
Malignant rhabdoid tumor (MRT), originally described as a sarcomatous variant of Wilms' tumor, is now recognized as a distinct, highly malignant entity. The authors describe, for the first time, a primary tumor of the orbit with histologic, immunohistochemical, and ultrastructural features of MRT. Their findings suggest both epithelial and mesenchymal differentiation of this unique tumor.
Rootman
J
J
Department of Ophthalmology, University of British Columbia, Vancouver, Canada.
Damji
K F
KF
Dimmick
J E
JE
D001706:Biopsy; D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D007124:Immunoenzyme Techniques; D007223:Infant; D008297:Male; D009918:Orbital Neoplasms / Q000175:diagnosis* / Q000648:ultrastructure; D012208:Rhabdomyosarcoma / Q000175:diagnosis; D014057:Tomography, X-Ray Computed