Non-immune fetal hydrops with hepatic hemangioendothelioma and Kasabach-Merritt syndrome: a case report.
A premature infant presented with non-immune hydrops fetalis, a liver mass, thrombocytopenia, and hypofibrinogenemia. Histologic examination of the liver tumor showed an infantile hemangioendothelioma. The clinical features of this case can be explained by anemia, hypoalbuminemia, and coagulopathy. The association with Kasabach-Merritt syndrome, the pathophysiology of non-immune hydrops fetalis, and primary hepatic neoplasms of the neonate are discussed.
Skopec
L L
LL
Department of Anatomical and Clinical Pathology, St. Paul-Ramsey Medical Center, Minneapolis, Minnesota 55101.
Lakatua
D J
DJ
D000328:Adult; D004211:Disseminated Intravascular Coagulation / Q000150:complications*; D005260:Female; D006390:Hemangioendothelioma / Q000150:complications* / Q000473:pathology; D006801:Humans; D015160:Hydrops Fetalis / Q000150:complications*; D007231:Infant, Newborn; D007235:Infant, Premature, Diseases / Q000150:complications* / Q000473:pathology; D008113:Liver Neoplasms / Q000150:complications* / Q000473:pathology; D011247:Pregnancy; D011248:Pregnancy Complications; D013577:Syndrome