Idiopathic fibrosis of the upper aero-digestive tract.
Idiopathic fibrosis of different areas of the body such as retroperitoneal fibrosis, mediastinal fibrosis, sclerosing cholangitis, Reidel's thyroiditis and pseudo-tumour of the orbit are well recognised entities that manifest individually or in combination. A case of idiopathic fibrosis of the upper aerodigestive tract is presented, which caused dense fibrosis of the floor of mouth, tongue, pharynx and larynx leading to aphonia and severe dysphagia. A permanent tracheostomy was performed and regular bouginage is necessary. This is the first such case reported in the literature.
Violaris
N S
NS
Plymouth General Hospital, Devon.
Windle-Taylor
P C
PC
D000368:Aged; D005260:Female; D005355:Fibrosis; D006801:Humans; D007830:Larynx / Q000473:pathology*; D009055:Mouth / Q000473:pathology*; D010614:Pharynx / Q000473:pathology*