title: Anatomic correction for transposition of the great arteries: first follow-up (38 patients).
abstract: Between April 1983 and October 1985, 38 consecutive patients with transposition of the great arteries (TGA) underwent anatomic correction. Ages ranged from 1 day to 284 weeks (mean 26.2 weeks). Simple TGA was present in 17 patients, 17 had an associated ventricular septal defect, and the remaining four had a Taussig-Bing anomaly. Hospital mortality was 2 of 38, with 1 late death. Follow-up time varied from 6 to 35 months. Postoperative cardiac catheterization was performed in 34 of the 36 early survivors. Right ventricular outflow tract obstruction with a systolic gradient greater than 20 mmHg was found in four. A residual left-to-right shunt was found in nine; Qp/Qs exceeded 2.0 in only one. In four, the pulmonary-to-systemic resistance ratio calculated was greater than 0.3. All 35 survivors are in excellent condition. Only one patient has slight aortic insufficiency. Most pre- and postoperative electrocardiographic abnormalities disappeared in due course. Echocardiography revealed normal left ventricular dimensions and fractional shortening. The aortic root diameter showed in almost all a value above the 95th percentile of normal. Postoperatively, the aortic root has grown parallel to, but above, the 95th percentile and as yet has shown no tendency to normalization.
authors.affiliation: Department of Pediatric Cardiology, Leiden University Hospital, The Netherlands.
authors.forename: R J
authors.initials: RJ
authors.lastname: Klautz
authors.forename: J
authors.initials: J
authors.lastname: Ottenkamp
authors.forename: J M
authors.initials: JM
authors.lastname: Quaegebeur
authors.forename: T N
authors.initials: TN
authors.lastname: Buis-Liem
authors.forename: J
authors.initials: J
authors.lastname: Rohmer
mesh_terms: D000790:Angiocardiography; D006328:Cardiac Catheterization; D002302:Cardiac Output; D002675:Child, Preschool; D004310:Double Outlet Right Ventricle / Q000601:surgery; D004452:Echocardiography; D004562:Electrocardiography; D005500:Follow-Up Studies; D006345:Heart Septal Defects, Ventricular / Q000601:surgery; D006439:Hemodynamics; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D009200:Myocardial Contraction; D011183:Postoperative Complications / Q000401:mortality*; D014188:Transposition of Great Vessels / Q000601:surgery*