title: [A rare facial disorder: cherubism].
abstract: A rare disorder involving primarily the maxillary region of the face, cherubism has a special place in the galaxy of osteolytic maxillary tumors. This disease is genetically transmitted and its pathogenesis is unknown at present. Its prognosis is considered as favorable since it progresses toward phases of regression and then disappearance--at least partial--of lesions. The main sequelae involve the teeth since agenesis often occurs which--as in the case presented here--is not very easy to correct.
authors.forename: M
authors.initials: M
authors.lastname: Corduant
authors.forename: P J
authors.initials: PJ
authors.lastname: Gugny
mesh_terms: D000848:Anodontia / Q000209:etiology / Q000628:therapy; D002636:Cherubism / Q000150:complications* / Q000628:therapy; D002675:Child, Preschool; D006801:Humans; D008297:Male; D009967:Orthodontic Appliances; D014071:Tooth Abnormalities / Q000209:etiology* / Q000628:therapy; D014079:Tooth Eruption, Ectopic
vernacular_title: Une affection rare de la face: le chérubisme.