Longitudinal tibial epiphyseal bracket in Nievergelt syndrome.
A patient is described with lower extremity mesomelic dwarfism associated with bilateral congenital elbow, hip, and knee dislocations. Rhomboid-shaped tibiae and delayed ossification of the primary fibular ossification centers were demonstrated at birth. Plain films and magnetic resonance imaging revealed that the tibial deformities were due to the presence of longitudinal epiphyseal brackets. These brackets were observed at surgery and confirmed histologically. Recognition of the longitudinal epiphyseal bracket and its relationship to the tibial deformities seen in this patient with Nievergelt syndrome is important for planning surgical treatment.
Burnstein
M I
MI
Department of Radiology, University of Wisconsin Hospital and Clinics, Madison 53792.
De Smet
A A
AA
Breed
A L
AL
Thomas
J R
JR
Hafez
G R
GR
D002675:Child, Preschool; D004392:Dwarfism / Q000175:diagnosis*; D004838:Epiphyses / Q000002:abnormalities / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D004204:Joint Dislocations / Q000151:congenital; D008279:Magnetic Resonance Imaging; D011859:Radiography; D013577:Syndrome; D013977:Tibia / Q000002:abnormalities* / Q000000981:diagnostic imaging