[Singular clinical form of intramedullary cavity revealed by a loss of proprioceptive sensation in the upper limbs].
A 47-year-old woman developed a progressive sensory deficit of the upper limbs. She lost perception of joint position, vibratory sense, skin-writing and stereognosis. Repeated tests by several examiners, up to 10 years after the onset, demonstrated normal pain and temperature sensation. The right hypoglossal nerve was involved at a late stage of the disease. CT and MRI showed an intramedullary cavity from C1 to T7. Somato-sensory evoked potentials from stimulation of the median nerves confirmed the bilateral impairment of the lemniscal pathways.
Penisson-Besnier
I
I
Service de Neurologie A, INSERM U 298, Angers.
Dubas
F
F
Emile
J
J
D001132:Arm / Q000294:innervation*; D005073:Evoked Potentials, Somatosensory; D005260:Female; D006801:Humans; D007002:Hypoglossal Nerve / Q000503:physiopathology; D008279:Magnetic Resonance Imaging; D008475:Median Nerve / Q000503:physiopathology; D008875:Middle Aged; D011434:Proprioception; D013118:Spinal Cord Diseases / Q000473:pathology / Q000503:physiopathology*; D014057:Tomography, X-Ray Computed
Forme clinique singulière de cavité intra-médullaire révélée par un déficit suspendu de la sensibilité proprioceptive.