Long-term survival of a harlequin fetus.
Harlequin ichthyosis is a rare, severe form of congenital ichthyosis, which probably represents a heterogeneous group of disorders. Unfortunately very little is known regarding the pathogenesis, course, and prognosis of harlequin ichthyosis because most of these infants die within a few weeks of birth. A case of an 9-year-old girl that had been a harlequin fetus, with clinical and histologic features similar to nonbullous congenital ichthyosiform erythroderma, is described.
Roberts
L J
LJ
Department of Dermatology, University of Texas Health Science Center/Southwestern Medical School, Dallas 75235.
D001706:Biopsy; D002648:Child; D004643:Emollients / Q000008:administration & dosage; D005260:Female; D006801:Humans; D007057:Ichthyosis / Q000188:drug therapy / Q000473:pathology; D008136:Longevity; D011379:Prognosis; D013997:Time Factors
D004643:Emollients