Total colonic aganglionosis.
All cases of total colonic aganglionosis (TCA) diagnosed in Dublin, Ireland, from 1978 to 1986 are reviewed. Nine patients were found to have TCA, and eight have undergone definitive surgery. There have been no deaths, and all patients are continuing to thrive. The diagnostic and operative features of the disease are described.
Dykes
E H
EH
Our Lady's Hospital For Sick Children, Dublin, Ireland.
Guiney
E J
EJ
D005260:Female; D006627:Hirschsprung Disease / Q000175:diagnosis* / Q000453:epidemiology / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007494:Ireland; D008297:Male