A congenital orbital defect with periorbital-dural tissue adhesion.
This case demonstrates a previously unreported congenital orbital deformity. The patient was born with a unilateral exophthalmos. The etiology of the defect was demonstrated by CT scan as a convex bowing of the right superomedial orbital wall behind the axis of the eye. At surgery, this convexity was revealed to be a small bony defect through which the periorbital tissue and dura mater adhered. This sort of orbital deformity, although subtle, must be considered in the differential diagnosis of congenital unilateral exophthalmos.
Skvaril
J
J
Bowman Gray School of Medicine, Winston-Salem, N.C.
Pearl
R M
RM
Ousterhaut
D K
DK
D005094:Exophthalmos / Q000151:congenital* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D009915:Orbit / Q000002:abnormalities* / Q000601:surgery; D000267:Tissue Adhesions / Q000151:congenital / Q000601:surgery