Reconstruction of the external genitalia in the adrenogenital syndrome by means of a personal one-stage procedure.
The techniques for correction of the external genitalia in the adrenogenital syndrome, as far as known by the author, are reviewed. The goals of repair and timing of surgery are discussed. The author's one-stage technique, first published in 1974, is described with intraoperative illustrations, and the results obtained in nine patients are discussed. The advantages of the technique are preservation of a clitoral glans with erogenous sensation based exclusively on the deep dorsal neurovascular bundle. The glans of the megaloclitoris is obliquely reduced in size at its base toward the ventral surface and by resection of up to two-thirds of the ventral segment. It is relocated at its anatomic female position. The labia minora and the introitus vaginae are reconstructed at the same stage with the skin of the megaloclitoris displaced in posterior direction after a cutback incision. Dispareunia is prevented by total excision of the corpora cavernosa, including the crura.
Hinderer
U T
UT
Clinica Mirasierra, Madrid, Spain.
D000312:Adrenal Hyperplasia, Congenital / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D005260:Female; D005500:Follow-Up Studies; D005835:Genitalia / Q000002:abnormalities / Q000601:surgery*; D006801:Humans; D007223:Infant; D013518:Surgery, Plastic / Q000379:methods*