[Histiocytosis X. Review of the literature and a case report].
Histiocytosis X is a non-lipid reticuloendotheliosis, characterized by histiocyte proliferation. The proliferating cells resemble the Langerhan's cells in the epidermis. The main clinical types include eosinophile granuloma, Hand-Schüller-Christian's disease (HSC) and Letterer-Siwe's disease (LS). Eosinophile granuloma is localized to the skeleton and runs a spontaneously benign course. HSC and LS are serious, generalized conditions. HSC runs a chronic and occasionally lethal course. LS usually runs a rapidly lethal course. LS commences before the age of three years while HSC occurs both in children and young adults. A case of HSC is described.
B
B
Hansen
P
P
Schwarz
D000328:Adult; D006646:Histiocytosis, Langerhans-Cell / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000188:drug therapy; D006801:Humans; D008297:Male; D011379:Prognosis; D011859:Radiography
Histiocytosis X. Litteraturgennemgang og en sygehistorie.