Portal hypertension secondary to intrahepatic arterio-portal shunt in primary amyloidosis: a case report.
Portal hypertension is a rare complication in hepatic amyloidosis. We experienced a case of a 40-year-old man with primary amyloidosis and advanced esophageal varices. Angiographic procedures clearly demonstrated portal hypertension secondary to intrahepatic arterio-portal shunting. Hepatic arterial embolization brought about a disappearance of the A-P shunt and portal hypertension, though rebleeding occurred. To our knowledge, this is the first case report in which the pathogenesis of portal hypertension in hepatic amyloidosis was elucidated.
Aramaki
T
T
First Department of Internal Medicine, Nippon Medical School, Tokyo, Japan.
Terada
H
H
Okumura
H
H
Tsutsui
H
H
Fujita
S
S
Tajiri
T
T
Ohya
T
T
Tajima
H
H
D000328:Adult; D000686:Amyloidosis / Q000150:complications*; D001164:Arteriovenous Fistula / Q000209:etiology* / Q000628:therapy; D004621:Embolization, Therapeutic; D004932:Esophageal and Gastric Varices / Q000209:etiology; D006499:Hepatic Artery; D006801:Humans; D006975:Hypertension, Portal / Q000209:etiology* / Q000628:therapy; D008107:Liver Diseases / Q000150:complications*; D008297:Male; D011169:Portal Vein