Patterns of mortality from hereditary ataxias in the United States, 1971 and 1973-1978.
Mortality rates for deaths 'due to' and 'with' hereditary ataxias are presented for the first time. Age-adjusted mortality rates were higher for whites than for nonwhites of either sex, and for men in both racial groups. Age-specific mortality rates for whites showed a peak for 'hereditary spinal ataxia' in the 20-29 age group. For the other types of ataxias they were low until age 40 and increased thereafter. Heart diseases were a frequent cause of death in people dying 'with' hereditary ataxias. The median survival (from birth) for hereditary spinal ataxia in whites was 35 years.
Leone
M
M
Neuroepidemiology Branch, National Institute of Neurological and Communicative Disorders and Stroke, Bethesda, Md.
Chandra
V
V
Schoenberg
B S
BS
D000293:Adolescent; D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D008875:Middle Aged; D013132:Spinocerebellar Degenerations / Q000453:epidemiology / Q000401:mortality*; D014481:United States