Portal hypertension secondary to intrahepatic arterio-portal shunt in primary amyloidosis: a case report.
Portal hypertension is a rare complication in hepatic amyloidosis. We experienced a case of a 40-year-old man with primary amyloidosis and advanced esophageal varices. Angiographic procedures clearly demonstrated portal hypertension secondary to intrahepatic arterio-portal shunting. Hepatic arterial embolization brought about a disappearance of the A-P shunt and portal hypertension, though rebleeding occurred. To our knowledge, this is the first case report in which the pathogenesis of portal hypertension in hepatic amyloidosis was elucidated.
First Department of Internal Medicine, Nippon Medical School, Tokyo, Japan.
T
T
Aramaki
H
H
Terada
H
H
Okumura
H
H
Tsutsui
S
S
Fujita
T
T
Tajiri
T
T
Ohya
H
H
Tajima
D000328:Adult; D000686:Amyloidosis / Q000150:complications*; D001164:Arteriovenous Fistula / Q000209:etiology* / Q000628:therapy; D004621:Embolization, Therapeutic; D004932:Esophageal and Gastric Varices / Q000209:etiology; D006499:Hepatic Artery; D006801:Humans; D006975:Hypertension, Portal / Q000209:etiology* / Q000628:therapy; D008107:Liver Diseases / Q000150:complications*; D008297:Male; D011169:Portal Vein