Tricuspid and pulmonary atresia with coarctation of the aorta: a rare combination possibly explained by persistence of the fifth aortic arch with a systemic-to-pulmonary arterial connection.
A ten-day old baby was found to have tricuspid and pulmonary atresia, and a "ductal-dependent" pulmonary circulation that was prostaglandin-sensitive. An unusual coarctation of the aorta was not recognised until an autopsy was performed, some 11 days after construction of an aortopulmonary shunt. A previously undefined anomaly in this neonate was persistence of the fifth aortic arch with a systemic-to-pulmonary artery connection on the same side as the definitive aorta. The histology of the fifth aortic arch is consistent with the pattern of an arterial duct.
Department of Pathology, University of Toronto Faculty of Medicine, Canada.
R M
RM
Freedom
M
M
Silver
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H
Miyamura
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology; D001017:Aortic Coarctation / Q000473:pathology*; D006325:Heart Atria / Q000473:pathology; D006344:Heart Septal Defects, Atrial / Q000473:pathology; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000473:pathology; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000473:pathology