Moyamoya disease associated with polycystic kidney disease and eosinophilic granuloma.
Moyamoya disease has been associated with renal artery stenosis, cerebral hemorrhage, and multiple cranial traumas. We report a unique case of moyamoya disease associated with polycystic kidney disease and eosinophilic granuloma. Although the etiology of moyamoya disease is unknown, a familial pattern of occurrence has been documented. Of particular importance is its presentation with polycystic kidney disease, an autosomal dominant disease, suggesting a hereditary component to the etiology of this unusual vasculitic disease.
Department of Medicine, Duke University Medical Center, Durham, NC 27710.
J B
JB
Pracyk
J M
JM
Massey
D000328:Adult; D001157:Arterial Occlusive Diseases / Q000150:complications*; D004803:Eosinophilic Granuloma / Q000150:complications*; D005260:Female; D006801:Humans; D009072:Moyamoya Disease / Q000150:complications* / Q000000981:diagnostic imaging; D007690:Polycystic Kidney Diseases / Q000150:complications*; D011859:Radiography