[A review of pulmonary histiocytosis X].
The article contains a review and two case reports of pulmonary histiocytosis-X. This is a rare disease entity comprising about 3% of all chronic interstitial lung diseases. Diagnosis is confirmed by histological and electronmicroscopic demonstration of the typical histiocytosis-X cell. The course of the disease varies. About 25% of the patients show spontaneous remission, in 40% the changes remain stationary, while 35% progress and eventually die from respiratory insufficiency or cor pulmonale. Treatment with glucocorticoids and cytostatics should be initiated at high disease activity, with progressive X-ray changes and decreasing pulmonary function.
Laub
M
M
Milman
N
N
Junker
K
K
Nielsen
P L
PL
D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006646:Histiocytosis, Langerhans-Cell / Q000188:drug therapy / Q000209:etiology / Q000473:pathology; D006801:Humans; D008171:Lung Diseases / Q000188:drug therapy / Q000209:etiology / Q000473:pathology; D008297:Male; D008875:Middle Aged
Pulmonal histiocytosis X--eosinofilt granulom i lungerne.