Anaesthesia and Rett syndrome: a case report.
Rett syndrome is a neurological disorder of females characterized by dementia, autism, movement disorders and an abnormality of respiratory control. A 14-year-old girl with Rett Syndrome underwent spinal fusion surgery under general anaesthesia. No exacerbation of the respiratory control defect with surgery and anaesthesia was observed. Hypothermia, ongoing blood loss and a normal anion gap acidosis were encountered, but were not attributable to features of this disorder.
Maguire
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D
Department of Anaesthesia, University of Manitoba Children's Hospital, Winnepeg.
Bachman
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C
D000293:Adolescent; D000641:Ammonia / Q000097:blood; D000768:Anesthesia, General; D001321:Autistic Disorder / Q000150:complications*; D003704:Dementia / Q000150:complications*; D005260:Female; D006801:Humans; D009069:Movement Disorders / Q000150:complications; D012120:Respiration Disorders / Q000150:complications*; D012600:Scoliosis / Q000601:surgery*; D013577:Syndrome
D000641:Ammonia