Tricuspid and pulmonary atresia with coarctation of the aorta: a rare combination possibly explained by persistence of the fifth aortic arch with a systemic-to-pulmonary arterial connection.
A ten-day old baby was found to have tricuspid and pulmonary atresia, and a "ductal-dependent" pulmonary circulation that was prostaglandin-sensitive. An unusual coarctation of the aorta was not recognised until an autopsy was performed, some 11 days after construction of an aortopulmonary shunt. A previously undefined anomaly in this neonate was persistence of the fifth aortic arch with a systemic-to-pulmonary artery connection on the same side as the definitive aorta. The histology of the fifth aortic arch is consistent with the pattern of an arterial duct.
Freedom
R M
RM
Department of Pathology, University of Toronto Faculty of Medicine, Canada.
Silver
M
M
Miyamura
H
H
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology; D001017:Aortic Coarctation / Q000473:pathology*; D006325:Heart Atria / Q000473:pathology; D006344:Heart Septal Defects, Atrial / Q000473:pathology; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000473:pathology; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000473:pathology