Epiretinal membranes and cystoid macular edema in gyrate atrophy of the choroid and retina.
A 26-year-old woman with gyrate atrophy of the choroid and retina and hyperornithinemia lost central visual acuity because of cystoid macular edema associated with epiretinal membrane formation. Dietary manipulation over a 5-month interval reduced the plasma ornithine levels 37% but did not halt the progression of the gyrate atrophy nor influence the cystoid edema or visual acuity.
Feldman
R B
RB
Department of Ophthalmology, Mayo Clinic Foundation, Rochester, Minnesota 55905.
Mayo
S S
SS
Robertson
D M
DM
Jones
J D
JD
Rostvold
J A
JA
D000328:Adult; D001284:Atrophy / Q000473:pathology; D002386:Cataract / Q000150:complications; D002829:Choroid / Q000473:pathology*; D004038:Diet, Reducing; D005260:Female; D006801:Humans; D008269:Macular Edema / Q000150:complications* / Q000178:diet therapy; D008566:Membranes; D009952:Ornithine / Q000097:blood / Q000652:urine; D012160:Retina / Q000473:pathology*; D014792:Visual Acuity; D058609:Visual Field Tests; D014794:Visual Fields; D014822:Vitreous Body / Q000473:pathology
D009952:Ornithine