[Splenectomy in Gaucher's disease. Apropos of 2 cases, one of which was preceded by embolization].
Two cases of Gaucher's disease type I are reported Splenectomy was indicated because of hypersplenism and massive splenomegaly. In one case hypersplenism was treated with pre-operative selective embolization because of the volume of the spleen (20 kg). The embolization corrected the thrombopenia but not the size of the spleen. Four years after operation for case 1 and eight months for case two, there is an improvement in the clinical status.
G
G
Samama
J L
JL
Brefort
M
M
Dolley
M
M
Leporrier
D002648:Child; D004621:Embolization, Therapeutic; D005260:Female; D005500:Follow-Up Studies; D005776:Gaucher Disease / Q000150:complications / Q000601:surgery* / Q000628:therapy; D006801:Humans; D013156:Splenectomy; D013163:Splenomegaly / Q000209:etiology* / Q000601:surgery / Q000628:therapy
La splénectomie dans la maladie de Gaucher. A propos de deux cas dont l'un précédé d'une embolisation.