[A case report of pulmonary arterio-venous fistula complicated with hereditary hemorrhagic telangiectasis].
A 5-year-old girl with multiple pulmonary arterio-venous fistulae was reported. Both her mother and grandmother have been diagnosed as the same disease previously. Her grandmother was treated with resection of the right basal segment for arterio-venous fistulae. Her mother is well with fistulae for more than 20 years. The patient was operated upon to enucleate two larger fistulae in segments 3 and 6 of right lung. Her postoperative course was uneventful. She was discharged from the hospital on the 22nd postoperative day. Pulmonary arteriovenous fistulae are thought to be a part of the hereditary hemorrhagic telangiectasis. Enucleation of the larger fistulae of the lung are preferable even for multiple lesions.
Hamada
Y
Y
Sudo
K
K
Nakagomi
E
E
Unno
T
T
Hayashi
N
N
Noguchi
K
K
Tadokoro
M
M
Mizuno
A
A
Kobayashi
M
M
Koto
K
K
D001164:Arteriovenous Fistula / Q000150:complications*; D002675:Child, Preschool; D005260:Female; D006801:Humans; D011651:Pulmonary Artery; D011667:Pulmonary Veins; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*