Hereditary vestibulo-cochlear dysfunction and vascular disorders.
A family is described with a progressive autosomal dominant vestibulocochlear dysfunction resulting in a Dandy syndrome, head movement dependent oscillopsia and hearing loss. The history was negative for other neurological or otological diseases (including infectious diseases) or use of neuro-ototoxic drugs, except for a high incidence of vascular disorders (hypertension, stroke, and heart infarction).
Verhagen
W I
WI
Department of Neurology, Canisius-Wilhelmina Hospital, Nijmegen, The Netherlands.
Huygen
P L
PL
Theunissen
E J
EJ
Joosten
E M
EM
D000328:Adult; D003051:Cochlea; D005260:Female; D034381:Hearing Loss / Q000175:diagnosis / Q000209:etiology / Q000235:genetics*; D006320:Hearing Tests; D006801:Humans; D007759:Labyrinth Diseases / Q000175:diagnosis / Q000235:genetics; D008297:Male; D008875:Middle Aged; D009759:Nystagmus, Pathologic; D009802:Oculomotor Nerve / Q000503:physiopathology; D010375:Pedigree; D014652:Vascular Diseases / Q000175:diagnosis / Q000235:genetics*; D014722:Vestibule, Labyrinth