title: Myopathic form of arthrogryposis and microcirculation lesion.
abstract: A microvascular lesion characterized by extensive platelet aggregation, thrombosis, vascular damage with hemorrhages was found in the muscle of a 2-month-old boy with a myopathic form of the arthrogryposis syndrome. The lesion morphologically resembled the vascular leakage seen in immunologically mediated tissue injury. A degradative effect of proteases released during platelet and neutrophil aggregation on the muscle and joints is suggested.
authors: Department of Neurology, Medical Academy, Warsaw, Poland.
authors: A
authors: A
authors: Fidziańska
authors: H H
authors: HH
authors: Goebel
authors: U
authors: U
authors: Burck-Lehmann
mesh_terms: D001176:Arthrogryposis / Q000150:complications / Q000473:pathology / Q000503:physiopathology*; D001778:Blood Coagulation Disorders / Q000150:complications* / Q000473:pathology / Q000503:physiopathology; D006801:Humans; D007223:Infant; D008297:Male; D009132:Muscles / Q000098:blood supply / Q000473:pathology*; D009135:Muscular Diseases / Q000209:etiology / Q000473:pathology / Q000503:physiopathology*