The nevoid basal cell carcinoma syndrome--Gorlin's syndrome. Multiple jaw cysts and skin cancer.
The nevoid basal cell carcinoma (NBS) syndrome with its characteristic multiple cysts of the jaws and skin cancer is of great interest to the dentist, the dermatologist and the oncologist. The dentist may have the opportunity of making an early diagnosis as the multiple cysts appear mostly in the ramus of the lower jaw. There is a great risk of recurrence as surgical removal is often very complicated. The disease is hereditary and is transmitted through females. The skin cancer can in most cases be treated surgically. It is essential that the family with the syndrome is investigated regularly and at periods of about six months.
Gustafson
G
G
Department of Oral Radiology, University of Lund, Sweden.
Lindahl
B
B
Dahl
E
E
Svensson
A
A
D000328:Adult; D000368:Aged; D001478:Basal Cell Nevus Syndrome / Q000000981:diagnostic imaging / Q000473:pathology*; D002280:Basal Cell Carcinoma / Q000473:pathology*; D005260:Female; D006229:Hand Dermatoses / Q000235:genetics / Q000473:pathology; D006801:Humans; D007570:Jaw Cysts / Q000235:genetics* / Q000473:pathology; D007642:Keratosis / Q000235:genetics / Q000473:pathology; D008297:Male; D008875:Middle Aged; D011859:Radiography; D012878:Skin Neoplasms / Q000235:genetics* / Q000473:pathology