Polysplenia and jejunal atresia with agenesis of the dorsal mesentery.
Polysplenia syndrome has been well described. It is associated with gastrointestinal atresia in patients with situs inversus abdominus; however, it appears that this case represents the first occurrence of polysplenia with jejunal atresia having agenesis of the dorsal mesentery and partial situs inversus abdominus.
Barber
G A
GA
Division of Pediatric Surgery, Naval Hospital, Portsmouth, VA 3708-5000.
Whalen
T V
TV
Moore
G
G
D000015:Abnormalities, Multiple; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007409:Intestinal Atresia; D007583:Jejunum / Q000002:abnormalities*; D008638:Mesenteric Arteries / Q000002:abnormalities*; D012857:Situs Inversus; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome