[Anesthetic management of a patient with Conradi's syndrome (chondrodysplasia punctata)--a case report].
Conradi's syndrome is a rare hereditary disease characterized by punctate epiphyseal calcifications. The symptoms include short stature, typical facies with hypertelorism, saddle nose, short neck, tracheal stenosis and scoliosis. The deformities of airway and thoracic cage are expected to bring about ventilatory failure during anesthesia and operation. Although there has been a brief report of a death of a child with this syndrome during induction of anesthesia, we cannot find any other report concerning the perioperative respiratory management. This is a report on a girl with Conradi's disease who developed respiratory problems due possibly to gastric aspiration during ophthalmic surgery under general anesthesia. Several anesthetic problems raised by this case are discussed.
Yorozu
T
T
Takino
Y
Y
Shimada
M
M
Sumida
Y
Y
Hayashi
H
H
D000768:Anesthesia, General; D002648:Child; D002806:Chondrodysplasia Punctata / Q000150:complications*; D005260:Female; D006801:Humans; D007431:Intraoperative Complications; D013508:Ophthalmologic Surgical Procedures; D012120:Respiration Disorders / Q000209:etiology