[Clinical aspects and problems in thoracic dystrophy].
We report about a child with Jeune-syndrome in whom surgical enlargement of the thorax at the age of 4 months was performed. In the beginning there was a significant improvement of the respiratory situation. Due to resorption of the interposed ribs there was again a shrinking of the thorax and a deterioration in the child's condition. A reoperation at the age of 8 months couldn't improve the situation anymore, because at that time the child had already additional problems such as pulmonary hypertension and broncho-pulmonary dysplasia. We overview the literature and line out our opinion about the indication for surgical enlargement of the thorax in children with Jeune syndrome.
Hofmann
D
D
Kinderchirurgische Klinik im Dr. von Haunerschen Kinderspital der Universität München.
Hofmann
U
U
Hecker
W C
WC
D001238:Asphyxia Neonatorum / Q000601:surgery*; D016025:Bone Transplantation; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D010009:Osteochondrodysplasias / Q000601:surgery*; D012127:Respiratory Distress Syndrome, Newborn / Q000601:surgery*; D012272:Ribs / Q000601:surgery; D012779:Short Rib-Polydactyly Syndrome / Q000601:surgery*; D013905:Thoracoplasty / Q000379:methods; D013909:Thorax / Q000002:abnormalities
Zur Klinik und Problematik der Thoraxdystrophie.