Multiple unilateral renal angiomyolipomas with regional lymphangioleiomyomatosis.
We present an unusual case of multiple unilateral renal angiomyolipomas occurring together with lymphangioleiomyomatosis of the regional lymph nodes. The association of these 2 hamartomatous lesions has been described only rarely but lends support to the concept that they represent a forme fruste of the tuberous sclerosis disease complex.
McIntosh
G S
GS
Department of Urology, Royal Free Hospital, London, England.
Dutoit
S H
SH
Chronos
N V
NV
Kaisary
A V
AV
D005260:Female; D006391:Hemangioma / Q000473:pathology*; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology*; D008067:Lipoma / Q000473:pathology*; D008203:Lymphangiomyoma / Q000473:pathology*; D008232:Lymphoproliferative Disorders / Q000473:pathology*; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000473:pathology*