[Juvenile aponeurotic fibroma (Keasbey's tumor) with metastatic progression. Apropos of a case].
The juvenile aponeurotic fibroma, isolated in 1953 by Louisa Keasbey is a rare tumour which is characterized by its recurrence and infiltration, but which has no tendency to metastasis. The case we report differs in its long-term outcome. The tumour diagnosed in a seven-year-old child has recurred locally for seven years, necessitated hand amputation, and finally developed a fibroblastic process extending to lung and pleura which caused the child's death. After this new finding in Keasbey's disease, we are led to reconsider the nosological situation in juvenile fibromatoses and its character of benign disease.
Benichou
M
M
Service de Chirurgie Orthopédique et Chirurgie de la Main, Hôpital Lapeyronie CHU, Montpellier.
Balmes
P
P
Marty-Double
C H
CH
Allieu
Y
Y
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005350:Fibroma / Q000473:pathology / Q000556:secondary*; D006225:Hand / Q000473:pathology; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary*; D008297:Male; D009364:Neoplasm Recurrence, Local; D010997:Pleural Neoplasms / Q000556:secondary*
Fibrome aponévrotique juvénile (tumeur de Keasbey) à evolution métastatique. A propos d'un cas.