[Megacystis microcolon intestinal hypoperistalsis syndrome: A neuropathy?].
2 cases of megacystis microcolon intestinal hypoperistalsis are presented. A female newborn was capable of being fed completely enterally after three months. Laparotomy was not performed. A male newborn was subjected to laparotomy after 3 days and an ileal stoma was applied. The infant died after 6 months of complete parenteral feeding without any peristalsis having been initiated. Biopsies of the colon and small intestine of the patient showed normal HE staining findings. Histochemical examination revealed type B neuronal dysplasia with neuronal hypogenesis. The findings of 27 cases described in the literature are discussed with special reference to the histological findings of the intestinal wall.
Bindl
L
L
Kinderklinik der Rheinischen Friedrich-Wilhelm-Universität Bonn.
Emons
D
D
Haverkamp
F
F
Fahnenstich
H
H
Kowalewski
S
S
Meier-Ruge
W
W
D002908:Chronic Disease; D003106:Colon / Q000294:innervation; D003112:Colonic Pseudo-Obstruction / Q000151:congenital / Q000473:pathology* / Q000503:physiopathology; D006801:Humans; D007231:Infant, Newborn; D007418:Intestinal Pseudo-Obstruction / Q000473:pathology*; D008297:Male; D009422:Nervous System Diseases / Q000151:congenital / Q000473:pathology* / Q000503:physiopathology; D010528:Peristalsis
Das Megazystis-Mikrokolon-intestinale Hypoperistaltik-Syndrom: Eine Neuropathie?