Pulsating orbital plexiform neurofibroma and optic nerve glioma.
A 13-year old Nigerian boy presented with a painless swelling which had grown, over ten years, into a pulsatile monstrous deformity of the left side of the face. Histology of the excised tissue showed a plexiform neurofibroma. It manifested with cutaneous, ocular and bony features. There was also a left eye optic nerve glioma. The case is presented and used to highlight the clinicopathological manifestations of orbital plexiform neurofibroma.
Binitie
O P
OP
Obikili
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AG
D000293:Adolescent; D003390:Cranial Nerve Neoplasms / Q000150:complications*; D005910:Glioma / Q000150:complications* / Q000601:surgery; D006801:Humans; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis; D009455:Neurofibroma / Q000150:complications*; D009549:Nigeria; D009901:Optic Nerve Diseases / Q000150:complications*; D009918:Orbital Neoplasms / Q000150:complications*