Trapeziometacarpal abnormalities in Ehlers-Danlos syndrome.
We studied 24 patients with Ehlers-Danlos syndrome with particular attention to the thumb and the trapeziometacarpal joint. The 11 males and 13 females had a mean age of 15.9 years. Symptomatic complaints included pinch, grip and twisting weakness; measurements showed dominant hand strength deficits of 71% for tip pinch, 55% for palmar pinch, 46% for key pinch, and 70% for grip. All finger joint ranges of motion were increased. Sixty-six percent of all the patients had trapeziometacarpal subluxation; 29% had dislocation. Sixteen percent had radiographic evidence of arthritis. Early occupational therapy evaluation and education can help these patients better understand and adapt to their limitations.
Gamble
J G
JG
Department of Surgery, Stanford University School of Medicine, Palo Alto, Calif.
Mochizuki
C
C
Rinsky
L A
LA
D000293:Adolescent; D000328:Adult; D001696:Biomechanical Phenomena; D002648:Child; D002675:Child, Preschool; D003430:Cross-Sectional Studies; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005260:Female; D006228:Hand Deformities, Congenital / Q000000981:diagnostic imaging*; D006801:Humans; D007593:Joint Instability / Q000000981:diagnostic imaging*; D008297:Male; D008875:Middle Aged; D011859:Radiography; D013933:Thumb; D014955:Wrist Joint / Q000000981:diagnostic imaging*