Progressive hearing loss in Usher's syndrome.
In 18 patients with Usher's syndrome, progressive hearing loss was verified audiologically in eight cases. Despite poor auditory threshold values and low speech discrimination scores, there was only one patient who could not communicate with speech. The possibility of hearing impairment being mainly progressive in Usher's syndrome is discussed.
Karjalainen
S
S
Department of Otolaryngology, Kuopio University Central Hospital, Finland.
Pakarinen
L
L
Teräsvirta
M
M
Kääriäinen
H
H
Vartiainen
E
E
D000293:Adolescent; D000328:Adult; D001301:Audiometry, Pure-Tone; D001309:Auditory Threshold; D005260:Female; D006311:Hearing Disorders / Q000175:diagnosis / Q000235:genetics*; D006801:Humans; D008297:Male; D008875:Middle Aged; D012174:Retinitis Pigmentosa / Q000235:genetics*; D013063:Speech Discrimination Tests; D013577:Syndrome