[Value of various radiological study results in the follow-up of Camurati-Engelmann disease].
Camurati-Engelmann disease is a rare progressive bone dysplasia; involvement of the skull base can lead to deafness, vestibular disturbances, facial paralysis and damage to the optic nerves. Treatment with corticosteroids, calcitonin and diphosphonates promises only very limited success. Conservative treatment of compression of the cranial nerves is almost ineffective, but the aim of surgical treatment is decompression of involved nerves. The differential diagnosis depends on radiological findings and clinical symptoms. Follow-up depends on radiographic examination and skeletal scintigraphy for showing the extent of the disease. CT may help in demonstrating compression of cranial nerves and define the indications for surgical decompression.
Wilhelm
K R
KR
Nuklearmedizinische Abteilung der Universitäts-Strahlenklinik Heidelberg.
Lenarz
T
T
Weise
D
D
Baldauf
G
G
Fritz
P
P
Bihl
H
H
D000328:Adult; D001848:Bone Diseases, Developmental / Q000175:diagnosis; D003966:Camurati-Engelmann Syndrome / Q000150:complications / Q000000981:diagnostic imaging* / Q000628:therapy; D003391:Cranial Nerves; D003937:Diagnosis, Differential; D005158:Facial Paralysis / Q000209:etiology; D005260:Female; D006311:Hearing Disorders / Q000209:etiology; D006801:Humans; D009408:Nerve Compression Syndromes / Q000209:etiology / Q000628:therapy; D010009:Osteochondrodysplasias / Q000000981:diagnostic imaging*; D011859:Radiography
Die Wertigkeit verschiedener radiologischer Untersuchungsverfahren in der Verlaufskontrolle der Camurati-Engelmannschen Krankheit.