[A case of von Hippel-Lindau disease with multiple abdominal disorders and renal cell carcinoma].
A 52-year-old male underwent right nephrectomy after a clinical diagnosis of renal cell carcinoma. He suddenly lost consciousness 3 days after the nephrectomy and expired 3 weeks later. An autopsy revealed a hemangio-blastoma in the forehead skin. Multiple cysts, cyst-adenomas and an islet cell tumor were also identified in the pancreas. Considering the presence of blindness and the familiar, prevalence of this disease, his case was diagnosed as a rare manifestation of von Hippel Lindau disease associated with renal cell carcinoma, complicated with abdominal disorders.
Funahashi
H
H
Dept. of Surgery, Nakatsugawa City Hospital.
Tuga
T
T
Oike
E
E
Tuji
S
S
Tubouti
N
N
Nagura
H
H
Nakanishi
H
H
D007516:Adenoma, Islet Cell / Q000473:pathology; D000798:Angiomatosis / Q000175:diagnosis*; D002292:Carcinoma, Renal Cell / Q000473:pathology* / Q000601:surgery; D006394:Hemangiosarcoma / Q000473:pathology; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology* / Q000601:surgery; D008297:Male; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary; D009392:Nephrectomy; D010190:Pancreatic Neoplasms / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000175:diagnosis* / Q000473:pathology