[Resection of a cardiac rhabdomyoma of the right and left ventricular outflow tract].
Rhabdomyomas are benign cardiac tumors often occurring as multiple lesions. We describe an infant with multiple cardiac rhabdomyomas causing severe right-ventricular and left-ventricular outflow tract obstructions. The intracavitary parts of the rhabdomyomas were successfully resected when the patient was 5 weeks old. Echocardiography showed regression in size of the remaining intramural tumors. Since there is only a low growth potential in cardiac rhabdomyomas, surgical management is indicated only in patients with hemodynamic obstruction or significant arrhythmias. Surgery should be primarily directed to relieve hemodynamic obstruction. If complete resection is not possible without damage to vital structures, resection should be restricted to the intracavitary parts of the tumor.
Hofbeck
M
M
Kardiologische Abteilung, Universität Erlangen-Nürnberg.
Deeg
K H
KH
Singer
H
H
vd Emde
J
J
Rein
J
J
D004452:Echocardiography; D006338:Heart Neoplasms / Q000151:congenital* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000151:congenital* / Q000601:surgery; D012207:Rhabdomyoma / Q000151:congenital* / Q000601:surgery; D014694:Ventricular Outflow Obstruction / Q000151:congenital* / Q000601:surgery
Resektion kardialer Rhabdomyome des rechts- und links-ventrikulären Ausflusstraktes.