Radiologic manifestations of the syndrome of neurocrest and colonic tumors.
This report describes the radiologic findings in the recently described syndrome of multiple colonic polyps and malignant tumors of neurocrest origin. One patient had multiple endocrine neoplasia syndrome type 11B with malignant medullary thyroid carcinoma, another had malignant pheochromocytoma, and the third had malignant carcinoid tumor. All patients had multiple colonic tubular or tubulovillous adenomas. In 2 patients, there were 8 sessile or pedunculated polyps distributed throughout the colon. In the patient with multiple endocrine neoplasia syndrome type 11B, the colon was carpeted with small polyps, 2-6 mm in size.
Shapir
J
J
Frank
P
P
D000310:Adrenal Gland Neoplasms / Q000000981:diagnostic imaging*; D000328:Adult; D001466:Barium Sulfate; D002276:Carcinoid Tumor / Q000000981:diagnostic imaging*; D002277:Carcinoma / Q000000981:diagnostic imaging; D003111:Colonic Polyps / Q000000981:diagnostic imaging*; D004733:Enema; D006801:Humans; D008297:Male; D008875:Middle Aged; D009377:Multiple Endocrine Neoplasia / Q000000981:diagnostic imaging*; D009432:Neural Crest; D010673:Pheochromocytoma / Q000000981:diagnostic imaging*; D013577:Syndrome; D013964:Thyroid Neoplasms / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed
D001466:Barium Sulfate