[An autopsy case of malignant retroperitoneal paraganglioma].
A case of an extra-adrenal malignant paraganglioma of the retroperitoneum is reported. A 33-year-old woman with a complaint of a dull pain in the right thigh was admitted. A CT scan revealed a large retroperitoneal mass situated between the right kidney and the aorta. A biopsied specimen of the right femur uncovered a metastatic focus of a paraganglioma. Subsequent chemotherapy and irradiation ultimately proved ineffective, and the patient died at the age of 37. Autopsy revealed a retroperitoneal mass 11 X 9 X 4 cm, and its metastatic foci in the vertebrae, ribs, sternum, and liver. Six cases of extra-adrenal malignant paragangliomas of the retroperitoneum that have been reported in Japan also are briefly reviewed.
Murao
T
T
Dept. of Pathology, Okayama City Hospital.
Tomiyama
Y
Y
Watanabe
T
T
Tanahashi
T
T
D000328:Adult; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D009362:Neoplasm Metastasis; D010236:Paraganglioma, Extra-Adrenal / Q000473:pathology* / Q000628:therapy; D012186:Retroperitoneal Neoplasms / Q000473:pathology* / Q000628:therapy