The occurrence of a fibro-osseous lesion and multiple dental anomalies in a patient with the Greig cephalopolysyndactyly syndrome.
The Greig cephalopolysyndactyly syndrome is an uncommon dysmorphic syndrome characterized by preaxial and postaxial polysyndactyly and minor craniofacial anomalies. It has an autosomal dominant inheritance. A review of the literature has failed to show documentation of any dental or oral abnormalities. Therefore, we report on a patient with Greig syndrome who had a maxillary fibro-osseous lesion and multiple dental and oral abnormalities.
Pliskin
M E
ME
Department of Oral Medicine, University of Pennsylvania School of Dental Medicine, Philadelphia.
Haber
B
B
Kornbrot
A
A
Madani
F
F
Lally
E T
ET
D000015:Abnormalities, Multiple; D000328:Adult; D005147:Facial Bones / Q000002:abnormalities*; D005260:Female; D005350:Fibroma / Q000473:pathology*; D006801:Humans; D008441:Maxillary Neoplasms / Q000473:pathology*; D010016:Osteoma / Q000473:pathology*; D012886:Skull / Q000002:abnormalities*; D013576:Syndactyly; D013577:Syndrome; D014071:Tooth Abnormalities / Q000473:pathology*