title: Renal angiomyolipoma associated with lymph node involvement and renal cell carcinoma in patients with tuberous sclerosis.
abstract: Renal angiomyolipomas are found in more than half of the patients with tuberous sclerosis. We report on 3 patients with tuberous sclerosis and pathologically aggressive renal angiomyolipoma with retroperitoneal lymph node involvement and/or renal cell carcinoma. All patients have had a benign course. The literature is reviewed and supports the benign nature of this seemingly aggressive disorder. An approach to the evaluation and treatment of a child with tuberous sclerosis and renal angiomyolipoma is presented.
authors.affiliation: Department of Surgery, University of Alabama, Birmingham.
authors.forename: R S
authors.initials: RS
authors.lastname: Taylor
authors.forename: D B
authors.initials: DB
authors.lastname: Joseph
authors.forename: E C
authors.initials: EC
authors.lastname: Kohaut
authors.forename: E R
authors.initials: ER
authors.lastname: Wilson
authors.forename: A J
authors.initials: AJ
authors.lastname: Bueschen
mesh_terms: D000293:Adolescent; D000328:Adult; D002292:Carcinoma, Renal Cell / Q000150:complications*; D002648:Child; D005260:Female; D006391:Hemangioma / Q000150:complications*; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008067:Lipoma / Q000150:complications*; D008198:Lymph Nodes / Q000473:pathology; D008207:Lymphatic Metastasis; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D014402:Tuberous Sclerosis / Q000150:complications*