["Saber-cut" scleroderma and Parry-Romberg facial hemiatrophy. Nosologic problems. Neurologic complications].
We report two cases of gradual facial hemiatrophy (Parry-Romberg syndrome). The first patient, an adolescent girl under treatment for hypothyroidism, presented with a very severe form combining advanced facial hemiatrophy, epilepsy with hemi-generalized seizures and hemiatrophy of the brain. The second patient was a girl who presented with localized scleroderma resembling a saber injury, homolateral cerebral atrophy and contralateral hemiparesis. Our two cases are evidence in support of a close relationship between saber injury-like scleroderma and the Parry-Romberg syndrome.
Klene
C
C
Massicot
P
P
Ferrière-Fontan
I
I
Sarlangue
J
J
Fontan
D
D
Guillard
J M
JM
D001284:Atrophy; D001921:Brain / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D004827:Epilepsy / Q000473:pathology; D005150:Facial Hemiatrophy / Q000145:classification / Q000150:complications / Q000473:pathology*; D005260:Female; D006801:Humans; D012595:Scleroderma, Systemic / Q000145:classification / Q000150:complications / Q000473:pathology*
Sclérodermie "en coup de sabre" et hémi-atrophie faciale de Parry-Romberg. Problème nosologique. Complication neurologique.