Magnetic resonance imaging in pathologically proven Hallervorden-Spatz disease.
We present an 11-year-old girl in whom high field strength MRI performed 2 1/2 years and 6 months before her death showed prominent hypointensity in the globus pallidus and substantia nigra consistent with iron deposition. This finding suggested Hallervorden-Spatz disease, which was confirmed at autopsy.
Schaffert
D A
DA
Department of Neuropathology, St. Joseph's Hospital and Medical Center, Barrow Neurological Institute, Phoenix, AZ 85013.
Johnsen
S D
SD
Johnson
P C
PC
Drayer
B P
BP
D001480:Basal Ganglia Diseases / Q000473:pathology*; D001921:Brain / Q000473:pathology*; D002648:Child; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D006211:Pantothenate Kinase-Associated Neurodegeneration / Q000473:pathology*