Bilateral opercular polymicrogyria.
Foix-Chavany-Marie syndrome (FCMS), or faciopharyngoglossomasticatory diplegia, is an uncommon syndrome that can result from vascular or developmental lesions of the anterior opercula bilaterally. We report the first pathological documentation of the developmental form of this disorder. Pathological examination revealed bilateral failure of opercular closure, opercular polymicrogyria, periventricular gray-matter heterotopias, and absence of the septum pellucidum.
Becker
P S
PS
Department of Pathology, Johns Hopkins University School of Medicine, Baltimore, MD.
Dixon
A M
AM
Troncoso
J C
JC
D000328:Adult; D001921:Brain / Q000473:pathology; D002544:Cerebral Infarction / Q000150:complications / Q000473:pathology*; D005158:Facial Paralysis / Q000209:etiology / Q000473:pathology*; D005930:Glossopharyngeal Nerve / Q000473:pathology*; D006801:Humans; D008297:Male; D008410:Masticatory Muscles / Q000473:pathology*; D013577:Syndrome