Bernard-Soulier syndrome complicating pregnancy: a case report.
The pregnancy of a patient with Bernard-Soulier syndrome is described. Coagulation abnormalities were encountered, as well as isoimmunization from previous transfusions. Immune suppression was achieved with steroids and intravenous gamma globulin, and plasmapheresis was performed to allow platelet transfusion.
Peaceman
A M
AM
Department of Obstetrics, Gynecology, and Reproductive Sciences, University of Texas Medical School, Houston.
Katz
A R
AR
Laville
M
M
D000328:Adult; D001606:Bernard-Soulier Syndrome / Q000235:genetics / Q000628:therapy*; D001791:Blood Platelet Disorders / Q000628:therapy*; D001803:Blood Transfusion; D003241:Consanguinity; D005260:Female; D005808:Genes, Recessive; D006801:Humans; D007116:Immunization, Passive; D008775:Methylprednisolone / Q000627:therapeutic use; D010956:Plasmapheresis; D017713:Platelet Transfusion; D011247:Pregnancy; D011250:Pregnancy Complications, Hematologic / Q000628:therapy*
D008775:Methylprednisolone