[The contribution of computerized tomography to the diagnosis of diffuse pulmonary lymphangiomyomatosis. Apropos of a case].
The authors report a case of lymphangiomatosis (LAM) proven histologically in a 49 year old female. This case benefitted from very detailed CT-scanning (IDM) with characteristic images obtained from the thorax and bilateral renal tumours suggestive of angiomyolipomas. This association seems to be quasi-pathognomic of the disease. The discovery at CT-scanning of cerebral calcification raises a possible connection of LAM with Bourneville's tuberous sclerosis. This CT-scanning study has several points of interest: the early diagnosis of pulmonary lesions which are under evaluated by standard radiography; a complete inventory of the possible localisations of the disease; it enables a possible diagnosis in very frail patients in whom a lung biopsy would be a risk; an ability to assess further progress as there also exists a good correlation between the extent of the disease assessed by TDM and the disturbance in pulmonary function.
Blanchon
F
F
Service de Pneumologie, Centre Hospitalier Général de Meaux.
Grivaux
M
M
Muller
C
C
Chantelot
J M
JM
Beroud
P
P
Attia
M
M
D004359:Drug Therapy, Combination; D004965:Estrogen Antagonists / Q000008:administration & dosage; D005260:Female; D006801:Humans; D008175:Lung Neoplasms / Q000000981:diagnostic imaging* / Q000188:drug therapy / Q000473:pathology; D008203:Lymphangiomyoma / Q000000981:diagnostic imaging* / Q000188:drug therapy / Q000473:pathology; D008232:Lymphoproliferative Disorders / Q000000981:diagnostic imaging*; D008875:Middle Aged; D013629:Tamoxifen / Q000008:administration & dosage; D014057:Tomography, X-Ray Computed
D004965:Estrogen Antagonists; D013629:Tamoxifen
Apport de la tomodensitométrie au diagnostic de lymphangiomyomatose pulmonaire diffuse. A propos d'un cas.