title: ["Saber-cut" scleroderma and Parry-Romberg facial hemiatrophy. Nosologic problems. Neurologic complications].
abstract: We report two cases of gradual facial hemiatrophy (Parry-Romberg syndrome). The first patient, an adolescent girl under treatment for hypothyroidism, presented with a very severe form combining advanced facial hemiatrophy, epilepsy with hemi-generalized seizures and hemiatrophy of the brain. The second patient was a girl who presented with localized scleroderma resembling a saber injury, homolateral cerebral atrophy and contralateral hemiparesis. Our two cases are evidence in support of a close relationship between saber injury-like scleroderma and the Parry-Romberg syndrome.
authors.forename: C
authors.initials: C
authors.lastname: Klene
authors.forename: P
authors.initials: P
authors.lastname: Massicot
authors.forename: I
authors.initials: I
authors.lastname: Ferrière-Fontan
authors.forename: J
authors.initials: J
authors.lastname: Sarlangue
authors.forename: D
authors.initials: D
authors.lastname: Fontan
authors.forename: J M
authors.initials: JM
authors.lastname: Guillard
mesh_terms: D001284:Atrophy; D001921:Brain / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D004827:Epilepsy / Q000473:pathology; D005150:Facial Hemiatrophy / Q000145:classification / Q000150:complications / Q000473:pathology*; D005260:Female; D006801:Humans; D012595:Scleroderma, Systemic / Q000145:classification / Q000150:complications / Q000473:pathology*
vernacular_title: Sclérodermie "en coup de sabre" et hémi-atrophie faciale de Parry-Romberg. Problème nosologique. Complication neurologique.