Dental management of a child with familial dysautonomia.
Familial dysautonomia is a hereditary sensory neuropathy that involves sensory, motor, and central components of the nervous system. Orofacial features include a tendency toward facial concavity in the child, and convexity in the adult. There is increased salivation, and crowded teeth and malocclusion are characteristic. This patient is not Jewish; this makes his case an extremely rare one.
D002648:Child; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000628:therapy; D004402:Dysautonomia, Familial; D006801:Humans; D008297:Male; D008310:Malocclusion / Q000628:therapy; D014082:Tooth Fractures / Q000628:therapy