title: [Epidemiology and cases of early manifestations of Huntington chorea].
abstract: The authors present some comparative data about the epidemiology of Huntington's chorea and describe a family (father and 5 children) with an unusually early onset (during the first year of life) of the typical combination of choreiform hyperkineses and slowly progressive dementia without any other focal lesions of the nervous system. The course of the disease is very mild and the type of inheritance is dominant.
mesh_terms: D005260:Female; D005799:Genes, Dominant; D006801:Humans; D006816:Huntington Disease / Q000175:diagnosis / Q000453:epidemiology* / Q000235:genetics; D008297:Male; D008875:Middle Aged; D010375:Pedigree; D014610:Uzbekistan
vernacular_title: Ob épidemiologii i sluchaiakh ranneĭ manifestatsii khorei Gentingtona.