Pulmonary veno-occlusive disease.
A 50-year-old female patient with a long history of Raynaud's phenomenon and rapidly deteriorating right-sided cardiac failure is presented. Pulmonary veno-occlusive disease was diagnosed from typical clinical and hemodynamic findings using a Swan-Ganz balloon catheter. The diagnosis was definitely confirmed at necropsy. There was no clinical, laboratory, or histologic evidence of a connective tissue disease.
D006332:Cardiomegaly / Q000473:pathology; D005260:Female; D006439:Hemodynamics; D006801:Humans; D008875:Middle Aged; D011667:Pulmonary Veins / Q000473:pathology; D011668:Pulmonary Veno-Occlusive Disease / Q000175:diagnosis* / Q000209:etiology; D011928:Raynaud Disease / Q000150:complications