Hexosaminidase A activity in skin fibroblasts from various types of GM2 gangliosidosis using a fluorogenic sulphated substrate.
D002384:Catalysis; D002460:Cell Line; D005347:Fibroblasts / Q000201:enzymology; D005678:G(M2) Ganglioside / Q000378:metabolism; D005733:Gangliosidoses / Q000201:enzymology*; D054818:Hexosaminidase A; D006801:Humans; D006923:Hymecromone / Q000031:analogs & derivatives; D012867:Skin / Q000201:enzymology; D001619:beta-N-Acetylhexosaminidases / Q000378:metabolism*
D005678:G(M2) Ganglioside; D006923:Hymecromone; C043647:4-methylumbelliferyl-6-sulfo-2-acetamido-2-deoxy-beta-glucopyranoside; D054818:Hexosaminidase A; D001619:beta-N-Acetylhexosaminidases