[Basal-cell nevomatosis associated with multifocal fetal rhabdomyoma. A case].
Nevoid basal-cell carcinoma is a hereditary syndrome. Its major features are a multiple basal-cell carcinoma which appears early in childhood, skeletal and genital abnormalities and ectopic calcifications. It may be associated with malignant schwannoma, medulloblastoma and lymphoma. We report one case of nevoid basal-cell carcinoma syndrome associated with foetal rhabdomyoma, thyroid gland polyadenoma and benign schwannoma. The first case of foetal rhabdomyoma associated with this syndrome was described in 1976.
Klijanienko
J
J
Département d'Histopathologie A, Institut Gustave-Roussy, Villejuif.
Caillaud
J M
JM
Micheau
C
C
Flamant
F
F
Schwaab
G
G
Avril
M F
MF
Ponzio-Prion
A
A
D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000473:pathology*; D002280:Basal Cell Carcinoma / Q000473:pathology*; D006801:Humans; D008297:Male; D008441:Maxillary Neoplasms / Q000473:pathology; D009378:Neoplasms, Multiple Primary / Q000473:pathology*; D012207:Rhabdomyoma / Q000473:pathology*; D013964:Thyroid Neoplasms / Q000473:pathology*
Naevomatose basocellulaire associée à un rhabdomyome foetal multifocal. Une observation.