title: [Postmortem study of case I of the original family of Roussy and Melle Lévy].
abstract: Post-mortem examination of case I of Roussy and Lévy's original family shows an extensive Schwann cell proliferation with some onion bulb formations. This confirms that this family is suffering from a form of hypertrophic neuropathy. The author reaffirms his concept of Roussy-Lévy syndrome as an autonomous hypertrophic neuropathy. The following criteria seem to justify the autonomy of this syndrome: dominant transmission, very precocious onset, extreme slowness of the evolution, and remarkable benignity of the general prognosis.
mesh_terms: D000368:Aged; D001921:Brain / Q000473:pathology; D002420:Cauda Equina / Q000473:pathology; D005260:Female; D006801:Humans; D006984:Hypertrophy; D010525:Peripheral Nerves / Q000473:pathology*; D010523:Peripheral Nervous System Diseases / Q000235:genetics* / Q000473:pathology; D012583:Schwann Cells / Q000473:pathology*; D013116:Spinal Cord / Q000473:pathology; D013126:Spinal Nerve Roots / Q000473:pathology; D013577:Syndrome
vernacular_title: Etude post mortem du cas I de la famille originale de Roussy et Melle L'evy.