[Cholangiocarcinoma associated with Caroli's disease. Apropos of a case. Review of the literature].
This is a report of a rarely observed occurrence of complication in Caroli's disease, i.e. the emergence of a cholangiocarcinoma in the course of the disease. There are 20 observations reported in the literature, and the hypotheses of pathogenesis set forth are reviewed. The frequency of a malignant transformation during the course of Caroli's disease is compared to the frequencies of other hepatic-biliary congenital cystic tumours. The excision of the cyst resulted in an appreciable period of survival for the patient.
D002759:Adenoma, Bile Duct / Q000209:etiology*; D000328:Adult; D001649:Bile Duct Diseases / Q000151:congenital; D001650:Bile Duct Neoplasms / Q000209:etiology*; D001653:Bile Ducts, Intrahepatic / Q000002:abnormalities*; D004108:Dilatation, Pathologic; D005260:Female; D006801:Humans
Cholangiocarcinome développé sur maladie de Caroli. A propos d'un cas. Revue de la littérature.