title: Chronic benign familial pemphigus.
abstract: Ten patients with benign familial chronic pemphigus (BFCP) (Hailey-Hailey disease) were evaluated; semiologic and localization differences were described, and special attention was given to solitary or atypical forms. In all the cases, the diagnosis was confirmed by histopathology; some histopathologic differences and the results achieved by direct immunofluorescence of skin are discussed. Most of the patients responded to the treatment with corticosteroids and antibiotics.
authors.affiliation: Department of Dermatology, Italian Hospital, Buenos Aires, Argentina.
authors.forename: R L
authors.initials: RL
authors.lastname: Galimberti
authors.forename: A M
authors.initials: AM
authors.lastname: Kowalczuk
authors.forename: O
authors.initials: O
authors.lastname: Bianchi
authors.forename: M V
authors.initials: MV
authors.lastname: Bonino
authors.forename: A
authors.initials: A
authors.lastname: Garcia Garcia
mesh_terms: D000328:Adult; D001623:Betamethasone / Q000031:analogs & derivatives / Q000627:therapeutic use; D002908:Chronic Disease; D003937:Diagnosis, Differential; D004359:Drug Therapy, Combination; D005260:Female; D005455:Fluorescent Antibody Technique; D005839:Gentamicins / Q000627:therapeutic use; D006801:Humans; D008297:Male; D008875:Middle Aged; D010392:Pemphigus / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics*; D011241:Prednisone / Q000627:therapeutic use; D012621:Seasons; D012867:Skin / Q000473:pathology
chemical_list: D005839:Gentamicins; C011175:betamethasone-17,21-dipropionate; D001623:Betamethasone; D011241:Prednisone