[Pigmented dermatofibrosarcoma protuberans (Bednar's tumor)].
Pigmented dermatofibrosarcoma protuberans, first described by Bednar under the term storiform neurofibroma, is an infrequent neoplasm accounting for 1 to 5% of cases of dermatofibrosarcoma protuberans. Bednar's tumor is composed of spindle shaped cells arranged in a distinctive storiform or carthwheel pattern, and melanin-containing dendritic cells scattered within the tumor. The differential diagnosis with (non-pigmented) dermatofibrosarcoma protuberans is based on the presence of this population of pigmented cells. Two cases of pigmented dermatofibrosarcoma protuberans (Bednar's tumor) are reported here in, and a discussion follows on the clinicopathological features of this neoplasm and the different hypotheses on its histogenesis.
Puig
L
L
Servicio de Dermatología, Hospital de San Pablo, Barcelona.
De Moragas
J M
JM
Matías-Guiu
X
X
Moreno
A
A
D000328:Adult; D002648:Child; D005260:Female; D005354:Fibrosarcoma / Q000473:pathology* / Q000648:ultrastructure; D006801:Humans; D008297:Male; D012878:Skin Neoplasms / Q000473:pathology* / Q000648:ultrastructure
Dermatofibrosarcoma protuberans pigmentado (tumor de Bednar).