title: [Steinert's disease and conduction disorders. Apropos of a familial study].
abstract: The authors reported a new family case of Steinert with twelve years follow-up. The study of potentials in the bundle of his was performed in all patients, showed an intra- and infra-hisian blocks. This study showed a discrepancy between muscular and myocardial evolutive injury, a very important knowledge for follow-up. Conduction disturbances were found in two cases and pacemaker insertion was performed in one patient. The authors specified the indication of electrophysiological studies during the onset and pacemaker implantation in all patient with a typical or suggestive history of syncope.
authors.affiliation: Service de Cardiologie, Centre Médico-Chirurgical et Obstétrical de la Sécurité Sociale, Strasbourg.
authors.forename: F
authors.initials: F
authors.lastname: Maloisel
authors.forename: F
authors.initials: F
authors.lastname: Wolff
authors.forename: M
authors.initials: M
authors.lastname: Chauvin
authors.forename: C
authors.initials: C
authors.lastname: Zimmerman
authors.forename: C
authors.initials: C
authors.lastname: Brechenmacher
mesh_terms: D000328:Adult; D001145:Arrhythmias, Cardiac / Q000209:etiology*; D004562:Electrocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000150:complications / Q000235:genetics*; D013997:Time Factors
vernacular_title: Maladie de Steinert et troubles de la conduction. A propos d'une étude familiale.