Chronic benign familial pemphigus.
Ten patients with benign familial chronic pemphigus (BFCP) (Hailey-Hailey disease) were evaluated; semiologic and localization differences were described, and special attention was given to solitary or atypical forms. In all the cases, the diagnosis was confirmed by histopathology; some histopathologic differences and the results achieved by direct immunofluorescence of skin are discussed. Most of the patients responded to the treatment with corticosteroids and antibiotics.
Galimberti
R L
RL
Department of Dermatology, Italian Hospital, Buenos Aires, Argentina.
Kowalczuk
A M
AM
Bianchi
O
O
Bonino
M V
MV
Garcia Garcia
A
A
D000328:Adult; D001623:Betamethasone / Q000031:analogs & derivatives / Q000627:therapeutic use; D002908:Chronic Disease; D003937:Diagnosis, Differential; D004359:Drug Therapy, Combination; D005260:Female; D005455:Fluorescent Antibody Technique; D005839:Gentamicins / Q000627:therapeutic use; D006801:Humans; D008297:Male; D008875:Middle Aged; D010392:Pemphigus / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics*; D011241:Prednisone / Q000627:therapeutic use; D012621:Seasons; D012867:Skin / Q000473:pathology
D005839:Gentamicins; C011175:betamethasone-17,21-dipropionate; D001623:Betamethasone; D011241:Prednisone