title: [Pigmented dermatofibrosarcoma protuberans (Bednar's tumor)].
abstract: Pigmented dermatofibrosarcoma protuberans, first described by Bednar under the term storiform neurofibroma, is an infrequent neoplasm accounting for 1 to 5% of cases of dermatofibrosarcoma protuberans. Bednar's tumor is composed of spindle shaped cells arranged in a distinctive storiform or carthwheel pattern, and melanin-containing dendritic cells scattered within the tumor. The differential diagnosis with (non-pigmented) dermatofibrosarcoma protuberans is based on the presence of this population of pigmented cells. Two cases of pigmented dermatofibrosarcoma protuberans (Bednar's tumor) are reported here in, and a discussion follows on the clinicopathological features of this neoplasm and the different hypotheses on its histogenesis.
authors.affiliation: Servicio de Dermatología, Hospital de San Pablo, Barcelona.
authors.forename: L
authors.initials: L
authors.lastname: Puig
authors.forename: J M
authors.initials: JM
authors.lastname: De Moragas
authors.forename: X
authors.initials: X
authors.lastname: Matías-Guiu
authors.forename: A
authors.initials: A
authors.lastname: Moreno
mesh_terms: D000328:Adult; D002648:Child; D005260:Female; D005354:Fibrosarcoma / Q000473:pathology* / Q000648:ultrastructure; D006801:Humans; D008297:Male; D012878:Skin Neoplasms / Q000473:pathology* / Q000648:ultrastructure
vernacular_title: Dermatofibrosarcoma protuberans pigmentado (tumor de Bednar).