[Internal disease findings in Arndt-Gottron scleromyxedema].
A case of papular mucinosis (scleromyxoedema of Arndt-Gottron) in a 64-year-old man is reported. Although a cutaneous mucinosis, the disease is characterized by a number of systemic disorders which determine the course and prognosis of the disease. A survey of 57 reported cases reveals that, in addition to the obligatory paraproteinaemia, neurological (24% of cases), cardiovascular (10%) and myopathic (9%) symptoms are in the foreground. Systemic lymphoplasmo-reticular involvement occurred in 14%. These findings emphasize the need for interdisciplinary cooperation in the diagnosis and for long-term supervision of patients with this disease.
Lang
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Goos
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D006801:Humans; D006942:Hypergammaglobulinemia / Q000175:diagnosis / Q000473:pathology; D007146:Immunoglobulin lambda-Chains; D008297:Male; D008875:Middle Aged; D009230:Myxedema / Q000175:diagnosis* / Q000473:pathology; D010265:Paraproteinemias / Q000175:diagnosis* / Q000473:pathology; D012598:Sclerosis; D012867:Skin / Q000473:pathology; D013577:Syndrome
D007146:Immunoglobulin lambda-Chains
Interne Krankheitsbefunde bei Skleromyxödem Arndt-Gottron.