Von Recklinghausen's neurofibromatosis.
More is being learned each year about the manifestations of neurofibromatosis, but unfortunately no cure has been found. In otolaryngology we see patients with this disease presenting a wide variety of pathology, which can include any of the regions or organs of the head and neck. Table 1 summarizes the otolaryngic manifestation of von Recklinghausen's disease. A well thought out management plan usually requires some sort of surgical management, as well as close coordination with other medical and surgical specialists who are also treating the patient. Due to the multiple organ system involvement in neurofibromatosis, a team approach is the most beneficial for the patient's progress and assistance in leading as functionally and cosmetically normal a life as possible.
D000293:Adolescent; D000328:Adult; D002648:Child; D005260:Female; D006258:Head and Neck Neoplasms; D006801:Humans; D007223:Infant; D008297:Male; D009456:Neurofibromatosis 1