[Continuous nocturnal intragastric feeding in glycogenosis type I and III].
Three patients with type I glycogen storage disease (GT I) and four patients with type III glycogen storage disease (GT III) have been treated with nocturnal intragastric feeding and frequent daytime meals for 2 to 8.5 years. In all of them, hypoglycemia was well controlled. Patients with GT. I showed a normal growth rate and an improvement of serum lactate, triglycerides, cholesterol and urate. Patients with GT. III showed no consistent changes in serum triglycerides cholesterol and transaminases and no improvement of myocardiopathy.
D001786:Blood Glucose / Q000378:metabolism; D002648:Child; D002675:Child, Preschool; D004200:Diseases in Twins; D004750:Enteral Nutrition; D005260:Female; D006008:Glycogen Storage Disease / Q000097:blood / Q000503:physiopathology / Q000628:therapy*; D005953:Glycogen Storage Disease Type I / Q000628:therapy; D006010:Glycogen Storage Disease Type III / Q000628:therapy; D006128:Growth; D006801:Humans; D007223:Infant; D007773:Lactates / Q000097:blood; D008055:Lipids / Q000097:blood; D008297:Male
D001786:Blood Glucose; D007773:Lactates; D008055:Lipids
L'alimentation intragastrique nocturne continue dans les glycogénoses de type I et III.