Abnormality of citrulline synthesis in liver mitochondria from patients with hyperornithinaemia, hyperammonaemia and homocitrullinuria.
D000592:Amino Acid Metabolism, Inborn Errors / Q000378:metabolism*; D000641:Ammonia / Q000097:blood*; D002956:Citrulline / Q000096:biosynthesis* / Q000652:urine*; D006801:Humans; D007700:Kinetics; D008930:Mitochondria, Liver / Q000378:metabolism*; D009952:Ornithine / Q000097:blood* / Q000378:metabolism
D002956:Citrulline; D000641:Ammonia; D009952:Ornithine