Lymphadenopathy and entero-vesical fistula in Fabry's disease.
A case of a 55-year-old man with known Fabry's disease, complicated by entero-vesical fistula and associated with enlarged mesenteric lymph nodes, is reported. Histopathologic and ultrastructural findings of the involved lymph nodes are described, and pathogenesis of the entero-vesical fistula is briefly discussed. This is the first case, to the authors' knowledge, of urologic complication in Fabry's disease.
D000795:Fabry Disease / Q000150:complications* / Q000473:pathology; D006801:Humans; D007412:Intestinal Fistula / Q000209:etiology / Q000473:pathology*; D007421:Intestine, Small; D008297:Male; D008875:Middle Aged; D001747:Urinary Bladder Fistula / Q000209:etiology / Q000473:pathology*