title: [Segmental neurofibromatosis].
abstract: Two additional cases of segmental neurofibromatosis (type V) are reported. This form of neurofibromatosis is manifested by neurofibromas or cafe-au-lait spots in a dermatomal or segmental distribution. Previously reported cases are reviewed. Their clinical manifestations, prognosis and the relationship between the classical neurofibromatosis and segmentary neurofibromatosis are discussed.
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D009456:Neurofibromatosis 1 / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*
vernacular_title: Neurofibromatosis segmentaria.