title: [Cranio-orbital neurofibromatosis. Apropos of a case].
abstract: Principal general manifestations of Recklinghausen's disease are outlined, with emphasis on cephalic lesions, particularly cranio-orbital localizations responsible in a large number of cases for lysis of greater wing of sphenoid. This is associated, amongst other complications, with ophthalmologic sequelae. A clinical case is presented, allowing discussion of the two essential problems raised by cranio-orbital neurofibromatosis: 1) conservation or not of the eye during necessary surgical treatment and 2) the course of the disease which is always progressive.
mesh_terms: D000328:Adult; D005134:Eye Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D013508:Ophthalmologic Surgical Procedures; D009915:Orbit / Q000601:surgery; D009918:Orbital Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery
vernacular_title: Neurofibromatose cranio-orbitaire. A propos d'un cas.