The surgical management of orbitopalpebral neurofibromatosis.
Orbitopalpebral neurofibromatosis may cause severe soft tissue deformity. Exophthalmos is either due to an intraorbital mass or to the absence of the greater wing of the sphenoid (mesodermal dysplasia). Five patients are presented. Surgical procedures and craniofacial techniques are detailed and discussed.
Morax
S
S
Department of Ophthalmology and Oculo-plastic Surgery, Fondation Ophtalmologique Rothschild, Paris, France.
Herdan
M L
ML
Hurbli
T
T
D000293:Adolescent; D000328:Adult; D002648:Child; D005142:Eyelid Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D005260:Female; D006801:Humans; D008297:Male; D009456:Neurofibromatosis 1 / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D010173:Palpation; D013518:Surgery, Plastic; D014057:Tomography, X-Ray Computed; D014792:Visual Acuity