[Peripheral nerve tumor with rhabdomyosarcomatous differentiation (malignant "triton" tumor)--report of 3 cases].
In this paper, 3 cases of malignant "triton" tumor are reported. By special stain, immunohistochemistry and electron microscopy, coexistence of rhabdomyoblasts and Schwann's cell elements was demonstrated. Case 1 was associated with von Recklinghausen disease; in case 3, the tumor developed within a nerve; both had background of malignant schwannoma. Case 2 was a girl with congenital giant pigmented nevus. Her tumor was composed predominantly of rhabdomyoblasts element but by immunohistochemistry, it was confirmed that her tumor also occurred within a nerve. The criteria of diagnosis, differential diagnosis and histogenesis are discussed.
Lin
J S
JS
Tianjin Medical College.
Ma
H D
HD
Chen
Z Y
ZY
Zhang
G F
GF
D000293:Adolescent; D000328:Adult; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008875:Middle Aged; D009441:Neurilemma / Q000473:pathology; D009456:Neurofibromatosis 1 / Q000175:diagnosis; D009508:Nevus, Pigmented / Q000175:diagnosis; D010524:Peripheral Nervous System Neoplasms / Q000175:diagnosis*; D012208:Rhabdomyosarcoma / Q000175:diagnosis*