Ocular hypertelorism, facial basal cell carcinomas, and multiple odontogenic keratocysts of the jaws.
Dentists should be aware of the multiple jaw cysts of NBCS that may develop in patients as young as 7 to 8 years. As the jaw cysts frequently are the initial symptom, dentists have the opportunity to detect the syndrome early, before the patients seek medical treatment. Any young patient with multiple odontogenic keratocysts in the jaws can develop other conditions characteristic of the disease. A careful family history should be taken, and the patient should be monitored closely for subsequent clinical manifestations of the disease.
Friedlander
A H
AH
Brentwood Division, VA Medical Center, West Los Angeles 90073.
Herbosa
E G
EG
Peoples
J R
JR
D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000175:diagnosis*; D001848:Bone Diseases, Developmental / Q000175:diagnosis*; D002280:Basal Cell Carcinoma / Q000175:diagnosis*; D003937:Diagnosis, Differential; D005153:Facial Neoplasms / Q000175:diagnosis*; D006801:Humans; D006972:Hypertelorism / Q000175:diagnosis*; D007570:Jaw Cysts / Q000175:diagnosis*; D008297:Male; D008336:Mandibular Diseases / Q000175:diagnosis