Juvenile pemphigus vulgaris: a 4- to 19-year follow-up of 4 patients.
Juvenile pemphigus (JP) is a rare disease. Of 274 pemphigus patients who were under our care during the last 26 years, 4 (1.4%) were in the JP category. The course and prognosis of the disease in the 4 patients who have been followed for 4-19 years are presented. Two patients are still in complete remission and off treatment for 4 and 6 years. In view of the literature and our experience, it appears that the clinical manifestations and course of JP are variable, similar to adult pemphigus. However, it seems that JP has a favorable prognosis quoad vitam.
David
M
M
Department of Dermatology, Beilinson Medical Center, Petah Tikva, Israel.
Zaidenbaum
M
M
Sandbank
M
M
D000293:Adolescent; D000328:Adult; D000367:Age Factors; D000368:Aged; D000369:Aged, 80 and over; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007557:Israel; D008297:Male; D008875:Middle Aged; D010392:Pemphigus / Q000188:drug therapy / Q000453:epidemiology; D011241:Prednisone / Q000627:therapeutic use; D011379:Prognosis
D011241:Prednisone