title: Diagnostic and therapeutic problems with an unusual congenital cystic hygroma of the orbit.
abstract: A case of an extensive congenital cystic hygroma in an unusual situation in the orbit is presented. The lesion occurred as an ulcerative, rapidly--growing and repeatedly--bleeding tumour with destruction of the left orbit, parts of the middle face, the nose and the base of skull. Despite X-ray investigation, computed tomography, nuclear magnetic resonance imaging and angiography it was impossible to give a reliable diagnosis. Because of the rapid growth of the tumour and its uncertain nature a radical resection with exenteration of the orbit, resection of the zygoma, the soft tissues of the cheek and parts of the nose and skull base was performed. One year after the resection there was no sign of recurrence.
authors.affiliation: Clinic for Maxillo-Facial Surgery, Medical University, Hannover, West-Germany.
authors.forename: J E
authors.initials: JE
authors.lastname: Hausamen
authors.forename: D
authors.initials: D
authors.lastname: Stolke
authors.forename: E
authors.initials: E
authors.lastname: Trowitzsch
mesh_terms: D005153:Facial Neoplasms / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007223:Infant; D008202:Lymphangioma / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D008297:Male; D009669:Nose Neoplasms / Q000151:congenital; D009918:Orbital Neoplasms / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D012888:Skull Neoplasms / Q000151:congenital