title: Dental management of a patient with glycogen storage disease type I.
abstract: Patients with glycogen storage disease type I (GSD I) have varied medical problems, including a bleeding diathesis characterized by a prolonged bleeding time. A case of a patient with GSD I having a history of medical problems, some of which were related to oral and dental bleeding, was presented. The patient was cariesfree and had generalized moderate to severe periodontal breakdown. A treatment regimen in a hospital setting, using cryoprecipitate and aminocaproic acid, permitted dental care and control of oral bleeding and associated complications.
authors.forename: S A
authors.initials: SA
authors.lastname: Ralls
authors.forename: E C
authors.initials: EC
authors.lastname: Marshall
mesh_terms: D000328:Adult; D003451:Cryoprotective Agents / Q000627:therapeutic use; D003730:Dental Care for Persons with Disabilities; D012534:Dental Scaling; D005884:Gingival Hemorrhage / Q000628:therapy; D005953:Glycogen Storage Disease Type I / Q000150:complications*; D006474:Hemorrhagic Disorders / Q000188:drug therapy / Q000209:etiology / Q000628:therapy; D006801:Humans; D008297:Male; D010510:Periodontal Diseases / Q000209:etiology / Q000601:surgery / Q000628:therapy*; D014092:Tooth Root / Q000601:surgery
chemical_list: D003451:Cryoprotective Agents