title: Primary peripheral neuroepithelioma of the orbit with intracranial extension.
abstract: A 7-year-old girl with clinical signs limited to moderate unilateral proptosis of 2 weeks duration and ipsilateral disc edema was found to have a contiguous orbital and subfrontal intracranial tumor best characterized as a peripheral neuroepithelioma by recent studies. Previously this tumor would have been called an extraosseous Ewing's sarcoma. The tumor had a significant lobular component on either side of the orbital roof. The patient is still alive 24 months posttreatment with multimodal excisional surgery, radiation, and chemotherapy.
authors.affiliation: Department of Ophthalmology, University of Colorado Health Sciences Center, Denver.
authors.forename: W B
authors.initials: WB
authors.lastname: Wilson
authors.forename: J
authors.initials: J
authors.lastname: Roloff
authors.forename: H L
authors.initials: HL
authors.lastname: Wilson
mesh_terms: D002675:Child, Preschool; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000000981:diagnostic imaging / Q000473:pathology* / Q000628:therapy; D009918:Orbital Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000628:therapy; D012512:Sarcoma, Ewing / Q000473:pathology; D014057:Tomography, X-Ray Computed