Dysplastic cardiac development presenting as cardiomyopathy.
Multiple manifestations of disordered or arrested cardiac muscle development are reported in a 14-year-old boy with clinical evidence of heart disease. These include persistent noncommunicating intramyocardial sinusoids, anomalous right ventricular muscle bands, muscular deficiency of ventricular septum, and papillary muscle underdevelopment. To our knowledge, this complex of findings has not been previously described.
Allenby
P A
PA
Department of Pathology, Michael Reese Hospital and Medical Center, Chicago, IL 60616.
Gould
N S
NS
Schwartz
M F
MF
Chiemmongkoltip
P
P
D000293:Adolescent; D001921:Brain / Q000473:pathology; D009202:Cardiomyopathies / Q000151:congenital* / Q000473:pathology; D004699:Endocardium / Q000002:abnormalities / Q000473:pathology; D006330:Heart Defects, Congenital / Q000473:pathology*; D006345:Heart Septal Defects, Ventricular / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology; D006801:Humans; D007668:Kidney / Q000473:pathology; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities / Q000473:pathology; D009206:Myocardium / Q000473:pathology*; D010210:Papillary Muscles / Q000002:abnormalities / Q000473:pathology