[Syndrome of left heart hypoplasia, causing hydrops fetalis and congenital pulmonary lymphangiectasis].
A case of hydrops fetalis and congenital pulmonary lymphangiectasis due to hypoplastic left heart syndrome with intact atrial septum is reported. Authors analyse hydrops and lymphangiectasis physiology in relation to cardiac defect, besides the present day therapeutics possibilities. Patient died four hours after birth.
Herranz Jordán
B
B
Departamento de Pediatría, Hospital Infantil de la Seguridad Social de Badajoz, Facultad de Medicina de la Universidad de Extremadura.
Campo Sampedro
F
F
Cabezas Segurado
F
F
Martínez Tallo
E M
EM
Galán Goméz
E
E
Cardesa García
J J
JJ
D001013:Aorta, Thoracic / Q000473:pathology; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications* / Q000473:pathology; D006801:Humans; D015160:Hydrops Fetalis / Q000209:etiology*; D007223:Infant; D008168:Lung / Q000473:pathology; D008171:Lung Diseases / Q000209:etiology* / Q000473:pathology; D008200:Lymphangiectasis / Q000209:etiology* / Q000473:pathology; D008297:Male; D009206:Myocardium / Q000473:pathology; D011247:Pregnancy; D013577:Syndrome
Síndrome del corazón izquierdo hipoplásico, debutando como hydrops fetalis y linfangiectasia pulmonar congénita.