title: [True hermaphroditism with 46, XX karyotype: report of a case].
abstract: A case of true hermaphroditism, in a 4-year-old, legally female, is reported. The external genitalia showed clitorism and labial agglutinate, and her karyotype from peripheral lymphocytoculture was 46,XX. She received gonadectomy at both sides, clitorectomy and plasty of vaginal orifice. Histopathological examination showed that both gonads were ovotestis.
authors.affiliation: Department of Urology, Kinki University School of Medicine.
authors.forename: M
authors.initials: M
authors.lastname: Kodama
authors.forename: Y
authors.initials: Y
authors.lastname: Ishikawa
authors.forename: H
authors.initials: H
authors.lastname: Tujihashi
authors.forename: S
authors.initials: S
authors.lastname: Kunikata
authors.forename: T
authors.initials: T
authors.lastname: Akiyama
authors.forename: A
authors.initials: A
authors.lastname: Okuyama
mesh_terms: D002675:Child, Preschool; D012734:Disorders of Sex Development / Q000235:genetics* / Q000473:pathology / Q000601:surgery; D005260:Female; D006061:Gonadal Dysgenesis, 46,XY / Q000235:genetics; D006801:Humans; D007621:Karyotyping