[Mixed connective tissue disease in childhood. Report of a case].
The Authors report a case of MCTD in a 11 years old girl. Initially the disease presented the classical clinical picture of IDM. Successively its evolution was marked by the appearance of the typical clinical features of JRA, SS and of serum antibodies anti-RNP and by absence of antibodies anti-dsDNA and anti-Sm. These data are characteristic of MCTD. The occurrence of this disease in children is extremely rare and the prognosis is related to a possible renal and/or haemopoietic involvement.
Falcini
F
F
Dipartimento di Pediatria, Università degli Studi di Firenze, Italia.
Volpi
M
M
Tafi
L
L
Montanelli
F
F
Taccetti
G
G
Pierattelli
M
M
Pratesi
G
G
D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008947:Mixed Connective Tissue Disease / Q000175:diagnosis / Q000188:drug therapy; D011241:Prednisone / Q000627:therapeutic use; D011379:Prognosis
D011241:Prednisone
La malattia mista del connettivo in età pediatrica. Segnalazione di un caso.