Progressive peripheral cone dysfunction.
A 22-year-old man had a three-year history of progressive day blindness, most notably peripherally, and denied difficulty with central vision or color vision. Visual function studies demonstrated a diffuse dysfunction of the photopic system and normal scotopic function. The central cone function, however, was essentially normal. Visual acuity was 20/20 in each eye, results on AO-HRR and Ishihara color plate testing were normal, color naming visual fields demonstrated color discrimination in the central 10 degrees, and foveal adaptation was normal.
Noble
K G
KG
Department of Ophthalmology, New York University Medical Center, NY 10016.
Siegel
I M
IM
Carr
R E
RE
D000328:Adult; D002940:Circadian Rhythm; D003118:Color Perception; D004596:Electroretinography; D006801:Humans; D008297:Male; D010786:Photoreceptor Cells / Q000503:physiopathology*; D012164:Retinal Diseases / Q000150:complications / Q000503:physiopathology; D014786:Vision Disorders / Q000209:etiology; D014792:Visual Acuity; D014794:Visual Fields