Dysplasia epiphysealis hemimelica at the metacarpophalangeal joint.
Dysplasia epiphysealis hemimelica (DEH) or Trevor's disease is a rare developmental disorder of asymmetric epiphyseal cartilage overgrowth accompanied by an accessory, epiphyseal ossification center. No published reports exist of metacarpal or phalangeal DEH. We report a case of bilateral DEH of the index finger: right-sided distal index metacarpal and left-sided index proximal phalanx. Both were surgically corrected with excision of the accessory ossification center; a transepiphyseal cartilaginous wedge was excised, and the articular surface was maintained. Follow-up shows maintenance of alignment without recurrence at 12 and 18 months after operation.
Maylack
F H
FH
Division of Orthopedic Surgery, Washington University School of Medicine, St. Louis, Mo. 63110.
Manske
P R
PR
Strecker
W B
WB
D005260:Female; D005384:Finger Joint / Q000601:surgery*; D005385:Fingers; D006801:Humans; D007223:Infant; D007592:Joint Diseases / Q000601:surgery*; D008662:Metacarpophalangeal Joint / Q000601:surgery*; D010009:Osteochondrodysplasias / Q000601:surgery*; D010012:Osteogenesis