Fatal cerebellar herniation secondary to Camurati-Englemann's disease.
Suboccipital craniotomy and cervical laminectomy were performed in a patient with Camurati-Englemann's disease to relieve symptoms of medullary compression. In spite of surgical decompression, the patient expired on the fourth postoperative day from cerebellar herniation.
Simpson
R K
RK
Department of Neurosurgery, Baylor College of Medicine, Houston, Texas 77030.
Fischer
D K
DK
Gall
G K
GK
Rose
J E
JE
D000328:Adult; D001842:Bone and Bones / Q000473:pathology; D003966:Camurati-Engelmann Syndrome / Q000150:complications* / Q000473:pathology; D002526:Cerebellar Diseases / Q000473:pathology*; D002531:Cerebellum / Q000473:pathology; D004677:Encephalocele / Q000473:pathology*; D006801:Humans; D007427:Intracranial Pressure; D008279:Magnetic Resonance Imaging; D008297:Male; D010009:Osteochondrodysplasias / Q000150:complications*; D012886:Skull / Q000473:pathology