title: Spontaneous carotid cavernous fistula in Ehlers Danlos syndrome.
abstract: A patient is described with Ehlers Danlos syndrome presenting with spontaneous carotid cavernous fistula, in whom there was biochemical evidence for defective type III collagen synthesis. Despite the risks associated with arterial manipulation, the fistula was successfully closed by interventional neuroradiology and the patient has since remained well. This outcome is in contrast with the results in previous reports.
authors.affiliation: Section of Neurology, University of Wales College of Medicine, Cardiff, UK.
authors.forename: R
authors.initials: R
authors.lastname: Fox
authors.forename: F M
authors.initials: FM
authors.lastname: Pope
authors.forename: P
authors.initials: P
authors.lastname: Narcisi
authors.forename: A C
authors.initials: AC
authors.lastname: Nicholls
authors.forename: B E
authors.initials: BE
authors.lastname: Kendall
authors.forename: M D
authors.initials: MD
authors.lastname: Hourihan
authors.forename: D A
authors.initials: DA
authors.lastname: Compston
mesh_terms: D000328:Adult; D001164:Arteriovenous Fistula / Q000000981:diagnostic imaging / Q000628:therapy*; D002340:Carotid Artery Diseases / Q000000981:diagnostic imaging / Q000628:therapy*; D002343:Carotid Artery, Internal / Q000000981:diagnostic imaging; D002404:Catheterization; D002426:Cavernous Sinus / Q000000981:diagnostic imaging; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006801:Humans; D002532:Intracranial Aneurysm / Q000628:therapy*; D008297:Male; D011859:Radiography; D012422:Rupture, Spontaneous